FHL1 reduces dystrophy in transgenic mice overexpressing FSHD muscular dystrophy region gene 1 (FRG1)

PLoS ONE

Volumn 10, Issue 2, 2015, Pages

  Feeney, Sandra J ^a   McGrath, Meagan J ^a   Sriratana, Absorn ^a   Gehrig, Stefan M ^b   Lynch, Gordon S ^b   Arcy, Colleen E D' ^a   Price, John T ^a,c   McLean, Catriona A ^a,d   Tupler, Rossella ^e,f   Mitchell, Christina A ^a  

^a MONASH UNIVERSITY   (Australia)

^b UNIVERSITY OF MELBOURNE   (Australia)

^c VICTORIA UNIVERSITY   (Australia)

^d ALFRED HOSPITAL   (Australia)

^e UNIVERSITY OF MASSACHUSETTS MEDICAL SCHOOL   (United States)

^f UNIVERSITY OF MODENA AND REGGIO EMILIA   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; C2C12 CELL LINE; CELL ACTIVATION; CELL COUNT; CELL DIFFERENTIATION; CONTROLLED STUDY; FACIOSCAPULOHUMERAL MUSCULAR DYSTROPHY; FHL1 GENE; FRG1 GENE; GENE EXPRESSION; GENE OVEREXPRESSION; IN VITRO STUDY; KYPHOSIS; MALE; MOUSE; MUSCLE CELL; MUSCLE FUNCTION; MUSCLE MASS; MYOBLAST; MYOFIBROSIS; NONHUMAN; QUADRICEPS FEMORIS MUSCLE; SATELLITE CELL; TRANSGENE; TRANSGENIC MOUSE; TRICEPS BRACHII MUSCLE; ANIMAL; CELL LINE; CYTOLOGY; FEMALE; FIBROSIS; GENETICS; HUMAN; METABOLISM; MUSCLE DEVELOPMENT; PATHOLOGY; PATHOPHYSIOLOGY; SKELETAL MUSCLE;

MUS; MUS MUSCULUS;

FHL1 PROTEIN, HUMAN; FRG1 PROTEIN, HUMAN; LIM PROTEIN; MUSCLE PROTEIN; NUCLEAR PROTEIN; SIGNAL PEPTIDE;

ANIMALS; CELL LINE; FEMALE; FIBROSIS; GENE EXPRESSION; HUMANS; INTRACELLULAR SIGNALING PEPTIDES AND PROTEINS; LIM DOMAIN PROTEINS; MALE; MICE; MICE, TRANSGENIC; MUSCLE DEVELOPMENT; MUSCLE PROTEINS; MUSCLE, SKELETAL; MUSCULAR DYSTROPHY, FACIOSCAPULOHUMERAL; MYOBLASTS; NUCLEAR PROTEINS;

EID: 84923239746     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0117665     Document Type: Article

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