Altered Tnnt3 characterizes selective weakness of fast fibers in mice overexpressing FSHD region gene 1 (FRG1)

American Journal of Physiology - Regulatory Integrative and Comparative Physiology

Volumn 306, Issue 2, 2014, Pages

  Sancisi, Valentina ^a   Germinario, Elena ^b,c   Esposito, Alessandra ^b   Morini, Elisabetta ^a,f   Peron, Samantha ^b   Moggio, Maurizio ^d   Tomelleri, Giuliano ^e   Danieli Betto, Daniela ^b,c   Tupler, Rossella ^a,f  

^a UNIVERSITY OF MODENA AND REGGIO EMILIA   (Italy)

^b UNIVERSITY OF PADOVA   (Italy)

^c Interuniversity Institute of Myology   (Italy)

^d UNIVERSITY OF MILAN   (Italy)

^e UNIVERSITY OF VERONA   (Italy)

^f UNIVERSITY OF MASSACHUSETTS MEDICAL SCHOOL   (United States)

Author keywords

Aberrant splicing; FRG1; Muscle weakness; Muscular dystrophy; Troponin T

Indexed keywords

MESSENGER RNA; MUSCLE PROTEIN; MYOSIN HEAVY CHAIN; PROTEIN FRG1; TROPONIN T; UNCLASSIFIED DRUG;

ALTERNATIVE RNA SPLICING; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; FACIOSCAPULOHUMERAL MUSCULAR DYSTROPHY; FAST MUSCLE; FEMALE; GENE OVEREXPRESSION; HUMAN; HUMAN TISSUE; MOUSE; MUSCLE CONTRACTILITY; MUSCLE STRENGTH; MUSCLE WEAKNESS; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN CROSS LINKING; SOLEUS MUSCLE; STOICHIOMETRY;

ABERRANT SPLICING; FRG1; MUSCLE WEAKNESS; MUSCULAR DYSTROPHY; TROPONIN T;

ALTERNATIVE SPLICING; ANIMALS; BIOLOGICAL MARKERS; GENE EXPRESSION REGULATION; MICE; MICE, TRANSGENIC; MUSCLE FIBERS, FAST-TWITCH; MUSCLE WEAKNESS; PROTEINS; RNA, MESSENGER; TROPONIN T;

EID: 84892576144     PISSN: 03636119     EISSN: 15221490     Source Type: Journal    
DOI: 10.1152/ajpregu.00379.2013     Document Type: Article

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