Leigh Syndrome in Drosophila melanogaster morphological and biochemical characterization of Surf1 post-transcriptional silencing

Journal of Biological Chemistry

Volumn 289, Issue 42, 2014, Pages 29235-29246

  Da Rè, Caterina ^a   Von Stockum, Sophia ^a   Biscontin, Alberto ^a   Millino, Caterina ^a   Cisotto, Paola ^a   Zordan, Mauro A ^a   Zeviani, Massimo ^b   Bernardi, Paolo ^a   De Pittà, Cristiano ^a   Costa, Rodolfo ^a  

^a UNIVERSITY OF PADOVA   (Italy)

^b UNIVERSITY OF CAMBRIDGE   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

BIOCHEMICAL CHARACTERIZATION; DROSOPHILA MELANOGASTER; LEIGH SYNDROME; POST-TRANSCRIPTIONAL;

CYTOCHROME C OXIDASE; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE; DOUBLE STRANDED RNA; DROSOPHILA PROTEIN; MEMBRANE PROTEIN; MIFEPRISTONE; MITOCHONDRIAL PROTEIN; OXYGEN; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATASE; SURF-1 PROTEIN; SURF1 PROTEIN, DROSOPHILA;

ADULT; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; CYTOCHROME C OXIDASE DEFICIENCY; DOWN REGULATION; DROSOPHILA MELANOGASTER; ENZYME ACTIVITY; GENE; GENE DOSAGE; GENE EXPRESSION REGULATION; GENE MUTATION; LARVAL STAGE; LEIGH DISEASE; LETHALITY; MITOCHONDRIAL MEMBRANE POTENTIAL; MITOCHONDRIAL RESPIRATION; MOLECULAR PATHOLOGY; NEUROPATHOLOGY; NONHUMAN; OXYGEN CONSUMPTION; POSTTRANSCRIPTIONAL GENE SILENCING; SURF1 GENE; UPREGULATION; ANIMAL; CELL LINE; CHEMISTRY; ELECTRON TRANSPORT; ENZYMOLOGY; GENE EXPRESSION PROFILING; GENE SILENCING; GENETIC TRANSCRIPTION; GENETICS; HUMAN; METABOLISM; MITOCHONDRION; MUTATION; PHYSIOLOGY; RNA INTERFERENCE; RNA PROCESSING;

ANIMALS; ATP SYNTHETASE COMPLEXES; CELL LINE; DROSOPHILA MELANOGASTER; DROSOPHILA PROTEINS; ELECTRON TRANSPORT; ELECTRON TRANSPORT COMPLEX IV; GENE EXPRESSION PROFILING; GENE SILENCING; HUMANS; LEIGH DISEASE; MEMBRANE POTENTIAL, MITOCHONDRIAL; MEMBRANE PROTEINS; MIFEPRISTONE; MITOCHONDRIA; MITOCHONDRIAL PROTEINS; MUTATION; OXYGEN; RNA INTERFERENCE; RNA PROCESSING, POST-TRANSCRIPTIONAL; RNA, DOUBLE-STRANDED; TRANSCRIPTION, GENETIC;

EID: 84908063359     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M114.602938     Document Type: Article

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