Analysis of Leigh syndrome mutations in the yeast SURF1 homolog reveals a new member of the cytochrome oxidase assembly factor family

Molecular and Cellular Biology

Volumn 30, Issue 18, 2010, Pages 4480-4491

  Bestwick, Megan ^a   Jeong, Mi Young ^a   Khalimonchuk, Oleh ^a   Kim, Hyung ^a   Winge, Dennis R ^a  

^a UNIVERSITY OF UTAH HEALTH SCIENCES CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CYCLOOXYGENASE 1; CYTOCHROME C OXIDASE; CYTOCHROME C1; CYTOCHROME OXIDASE ASSEMBLY 4; FUNGAL PROTEIN; MITOCHONDRIAL PROTEIN; PROTEIN SHY1; UNCLASSIFIED DRUG; COA2 PROTEIN, S CEREVISIAE; MEMBRANE PROTEIN; PROTEIN SUBUNIT; SACCHAROMYCES CEREVISIAE PROTEIN; SHY1 PROTEIN, S CEREVISIAE; SURF-1 PROTEIN;

ARTICLE; CONTROLLED STUDY; ENZYME ACTIVITY; FUNGAL GENE; GENE REPRESSION; LEIGH DISEASE; MISSENSE MUTATION; NONHUMAN; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN DEFICIENCY; PROTEIN FUNCTION; PROTEIN LOCALIZATION; PROTEIN MOTIF; SURF1 GENE; YEAST; AMINO ACID SEQUENCE; ANIMAL; CELL RESPIRATION; GENETICS; HUMAN; METABOLISM; MOLECULAR GENETICS; PHYSIOLOGY; PROTEIN SUBUNIT; PROTEIN SYNTHESIS; SACCHAROMYCES CEREVISIAE; SEQUENCE ALIGNMENT;

AMINO ACID SEQUENCE; ANIMALS; CELL RESPIRATION; ELECTRON TRANSPORT COMPLEX IV; HUMANS; LEIGH DISEASE; MEMBRANE PROTEINS; MITOCHONDRIAL PROTEINS; MOLECULAR SEQUENCE DATA; MUTATION, MISSENSE; PROTEIN BIOSYNTHESIS; PROTEIN SUBUNITS; SACCHAROMYCES CEREVISIAE; SACCHAROMYCES CEREVISIAE PROTEINS; SEQUENCE ALIGNMENT;

EID: 77956700021     PISSN: 02707306     EISSN: 10985549     Source Type: Journal    
DOI: 10.1128/MCB.00228-10     Document Type: Article

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