Characterization of dystrophin deficient rats: A new model for duchenne muscular dystrophy

PLoS ONE

Volumn 9, Issue 10, 2014, Pages

  Larcher, Thibaut ^a   Lafoux, Aude ^b   Tesson, Laurent ^b   Remy, Sé Verine ^b   Thepenier, Virginie ^b   François, Virginie ^b   Guiner, Caroline Le ^b,c   Goubin, Helicia ^a   Dutilleul, Maé Va ^a   Guigand, Lydie ^a   Toumaniantz, Gilles ^b   De Cian, Anne ^b   Boix, Charlotte ^b   Renaud, Jean Baptiste ^b   Cherel, Yan ^a   Giovannangeli, Carine ^b   Concordet, Jean Paul ^b   Anegon, Ignacio ^b   Huchet, Corinne ^b  

^a INRA UMR 703   (France)

^b INSERM   (France)

^c GÉNÉTHON   (France)

Author keywords

[No Author keywords available]

Indexed keywords

CREATINE KINASE; DYSTROPHIN; MESSENGER RNA;

ADIPOSE TISSUE; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; CREATINE KINASE BLOOD LEVEL; DIAPHRAGM MUSCLE; DISEASE SEVERITY; DMD GENE; DUCHENNE MUSCULAR DYSTROPHY; DYSTROPHIN DEFICIENT RAT; EXON; FEMALE; GENE; GENE DELETION; GENE TARGETING; IMMUNOHISTOCHEMISTRY; LEG MUSCLE; MALE; MOTOR ACTIVITY; MUSCLE NECROSIS; MUSCLE REGENERATION; MUSCLE STRENGTH; MYOFIBROSIS; NONHUMAN; RAT; RAT STRAIN; WESTERN BLOTTING; ANIMAL; ANIMAL MUSCULAR DYSTROPHY; BLOOD; DEFICIENCY; DISEASE MODEL; FIBROSIS; GENE EXPRESSION; GENETICS; HEART MUSCLE; HEART VENTRICLE REMODELING; METABOLISM; MUSCLE WEAKNESS; MUTATION; NUCLEOTIDE SEQUENCE; PATHOLOGY; PATHOPHYSIOLOGY; SKELETAL MUSCLE;

RATTUS;

ANIMALS; BASE SEQUENCE; CREATINE KINASE; DISEASE MODELS, ANIMAL; DYSTROPHIN; EXONS; FEMALE; FIBROSIS; GENE DELETION; GENE EXPRESSION; GENE TARGETING; MALE; MUSCLE WEAKNESS; MUSCLE, SKELETAL; MUSCULAR DYSTROPHY, ANIMAL; MUSCULAR DYSTROPHY, DUCHENNE; MUTATION; MYOCARDIUM; RATS; RNA, MESSENGER; VENTRICULAR REMODELING;

EID: 84907942795     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0110371     Document Type: Article

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