Modeling of Friedreich ataxia-related iron overloading cardiomyopathy using patient-specific-induced pluripotent stem cells

Pflugers Archiv European Journal of Physiology

Volumn 466, Issue 9, 2014, Pages 1831-1844

  Lee, Yee Ki ^a   Ho, Philip Wing Lok ^a   Schick, Revital ^b   Lau, Yee Man ^a   Lai, Wing Hon ^a   Zhou, Ting ^c   Li, Yanhua ^c   Ng, Kwong Man ^a   Ho, Shu Leung ^a   Esteban, Miguel Angel ^c   Binah, Ofer ^b   Tse, Hung Fat ^a   Siu, Chung Wah ^a  

^a UNIVERSITY OF HONG KONG   (Hong Kong)

^b TECHNION ISRAEL INSTITUTE OF TECHNOLOGY   (Israel)

^c INSTITUTE OF GEOLOGY AND GEOPHYSICS   (China)

Author keywords

Cardiomyopathy; Friedreich ataxia; Induced pluripotent stem cells

Indexed keywords

FRATAXIN; IRON BINDING PROTEIN;

ADULT; CARDIOMYOPATHIES; COMPLICATION; FEMALE; FRIEDREICH ATAXIA; GENETICS; HEART MUSCLE CELL; HUMAN; IN VITRO STUDY; IRON OVERLOAD; METABOLISM; PATHOLOGY; PLURIPOTENT STEM CELL;

ADULT; CARDIOMYOPATHIES; FEMALE; FRIEDREICH ATAXIA; HUMANS; IN VITRO TECHNIQUES; IRON OVERLOAD; IRON-BINDING PROTEINS; MYOCYTES, CARDIAC; PLURIPOTENT STEM CELLS;

EID: 84905719998     PISSN: 00316768     EISSN: 14322013     Source Type: Journal    
DOI: 10.1007/s00424-013-1414-x     Document Type: Article

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