Thematic review series: Recent advances in the treatment of lysosomal storage diseases: Lysosomal exocytosis and lipid storage disorders

Journal of Lipid Research

Volumn 55, Issue 6, 2014, Pages 995-1009

  Samie, Mohammad Ali ^a   Xu, Haoxing ^a  

^a UNIVERSITY OF MICHIGAN   (United States)

Author keywords

Calcium; Lysosomal storage disease; Transcription factor EB; Transient receptor potential mucolipin 1

Indexed keywords

ADENOSINE TRIPHOSPHATASE; ADENOSINE TRIPHOSPHATE; BETA N ACETYLHEXOSAMINIDASE; CALCIUM CHANNEL; CALCIUM ION; CHOLESTEROL; CYTOSKELETON PROTEIN; LYSOSOME ASSOCIATED MEMBRANE PROTEIN 1; MOLECULAR MOTOR; NEURAMINIDASE 1; PHOSPHATIDYLINOSITIDE; RAB7 PROTEIN; SIALIDASE; SNARE PROTEIN; SPHINGOMYELIN; SYNAPTOSOMAL ASSOCIATED PROTEIN 23; SYNAPTOTAGMIN; SYNAPTOTAGMIN VII; TFEB TRANSCRIPTION FACTOR; TRANSCRIPTION FACTOR; TRANSIENT RECEPTOR POTENTIAL MUCOLIPIN 1 CALCIUM CHANNEL; UNCLASSIFIED DRUG; VACUOLAR ADENOSINE TRIPHOSPHATASE; HYDROLASE;

AUTOPHAGOSOME; CALCIUM TRANSPORT; CELL MIGRATION; CELL STIMULATION; CELLULAR, SUBCELLULAR AND MOLECULAR BIOLOGICAL PHENOMENA AND FUNCTIONS; COMPLEX FORMATION; DISEASE ASSOCIATION; DISEASE CLASSIFICATION; ENERGY METABOLISM; ENZYMATIC DEGRADATION; ENZYME ACTIVITY; ENZYME RELEASE; EXOCYTOSIS; FLUORESCENCE MICROSCOPY; HUMAN; LIPIDOSIS; LYSOSOMAL EXOCYTOSIS; LYSOSOMAL NUTRIENT SENSING SYSTEM; LYSOSOME; MEMBRANE BIOLOGY; MEMBRANE REPAIR; MOLECULAR DYNAMICS; MOLECULAR INTERACTION; MOLECULAR PATHOLOGY; MULTIVESICULAR BODY; NERVE FIBER GROWTH; NONHUMAN; PHAGOCYTOSIS; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FUNCTION; REGULATORY MECHANISM; REVIEW; TOTAL INTERNAL REFLECTION FLUORESCENCE MICROSCOPY; ANIMAL; DISORDERS OF LIPID AND LIPOPROTEIN METABOLISM; GENETICS; LIPID METABOLISM; METABOLISM; PATHOLOGY;

ANIMALS; EXOCYTOSIS; HUMANS; HYDROLASES; LIPID METABOLISM; LIPID METABOLISM, INBORN ERRORS; LYSOSOMES;

EID: 84901670787     PISSN: 00222275     EISSN: 15397262     Source Type: Journal    
DOI: 10.1194/jlr.R046896     Document Type: Review

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