Cystic fibrosis: An inherited disease affecting mucin-producing organs

International Journal of Biochemistry and Cell Biology

Volumn 52, Issue , 2014, Pages 136-145

  Ehre, Camille ^a   Ridley, Caroline ^b   Thornton, David J ^b  

^a UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF MANCHESTER   (United Kingdom)

Author keywords

CF; CFTR; Mucin; Mucus; Pathogenesis

Indexed keywords

ACETYLCYSTEINE; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; EPITHELIAL SODIUM CHANNEL; IVACAFTOR; LUMACAFTOR; MARCKS PROTEIN; MESSENGER RNA; MUCIN; MUCIN 19; MUCIN 2; MUCIN 5AC; MUCIN 5B; MUCIN 6; MUCOLYTIC AGENT; OSMOTIC AGENT; UNCLASSIFIED DRUG;

AIRWAY OBSTRUCTION; ALTERNATIVE MEDICINE; BIOPHYSICS; COVALENT BOND; CYSTIC FIBROSIS; EXOCYTOSIS; FORCED EXPIRATORY VOLUME; GENE EXPRESSION; GENE THERAPY; GLYCOSYLATION; HIGH THROUGHPUT SCREENING; HUMAN; LUNG FIBROSIS; LUNG FUNCTION; MUCOCILIARY CLEARANCE; MUCUS; NONHUMAN; PHENOTYPE; PROTEIN CROSS LINKING; PROTEIN FUNCTION; PROTEIN SYNTHESIS; REVIEW; SPUTUM; VARIABLE NUMBER OF TANDEM REPEAT; ANIMAL; BIOSYNTHESIS; GENETICS; METABOLISM; PATHOLOGY;

ANIMALIA;

ANIMALS; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; HUMANS; MUCINS;

EID: 84901617618     PISSN: 13572725     EISSN: 18785875     Source Type: Journal    
DOI: 10.1016/j.biocel.2014.03.011     Document Type: Review

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