Dimerization, oligomerization, and aggregation of human amyotrophic lateral sclerosis copper/zinc superoxide dismutase 1 protein mutant forms in live cells

Journal of Biological Chemistry

Volumn 289, Issue 21, 2014, Pages 15094-15103

  Kim, Jiho ^a   Lee, Honggun ^a   Lee, Joo Hyun ^a   Kwon, Do Yoon ^a   Genovesio, Auguste ^a   Fenistein, Denis ^a   Ogier, Arnaud ^a   Brondani, Vincent ^a   Grailhe, Regis ^a  

^a Neurodegeneration and Applied Microscopy   (South Korea)

Author keywords

[No Author keywords available]

Indexed keywords

AGGREGATES; DIMERIZATION; ENERGY TRANSFER; FLUORESCENCE; FLUORESCENCE SPECTROSCOPY; NEURONS; OLIGOMERIZATION; OLIGOMERS; OXYGEN;

AMYOTROPHIC LATERAL SCLEROSIS; COPPER/ZINC SUPEROXIDE DISMUTASE; FLUORESCENCE CORRELATION SPECTROSCOPY; FLUORESCENCE RESONANCE ENERGY TRANSFER; FLUORESCENCE TECHNIQUE; GENETIC MUTATIONS; MICROSCOPIC TECHNIQUES; PROTEIN AGGREGATION;

PROTEINS;

COPPER ZINC SUPEROXIDE DISMUTASE;

AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; CONTROLLED STUDY; DIMERIZATION; DISEASE ASSOCIATION; FLUORESCENCE COMPLEMENTATION; FLUORESCENCE CORRELATION SPECTROSCOPY; FLUORESCENCE RESONANCE ENERGY TRANSFER; HUMAN; HUMAN CELL; IMAGE BASED QUANTIFICATION; MEDICAL PROCEDURES; MUTATION; OLIGOMERIZATION; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN CONFORMATION; PROTEIN EXPRESSION; UBIQUITINATION;

FLUORESCENCE CORRELATION SPECTROSCOPY; FLUORESCENCE RESONANCE ENERGY TRANSFER (FRET); MUTANT; PROTEIN AGGREGATION; PROTEIN MISFOLDING; SUPEROXIDE DISMUTASE (SOD);

AMYOTROPHIC LATERAL SCLEROSIS; FLUORESCENCE RESONANCE ENERGY TRANSFER; HEK293 CELLS; HUMANS; LIVER; LUMINESCENT PROTEINS; MICROSCOPY, CONFOCAL; MODELS, MOLECULAR; MUTANT PROTEINS; MUTATION; PROTEIN MULTIMERIZATION; PROTEIN STRUCTURE, QUATERNARY; SPECTROMETRY, FLUORESCENCE; SUPEROXIDE DISMUTASE;

EID: 84901405867     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M113.542613     Document Type: Article

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