Chondrocyte-specific pathology during skeletal growth and therapeutics in a murine model of pseudoachondroplasia

Journal of Bone and Mineral Research

Volumn 29, Issue 5, 2014, Pages 1258-1268

  Posey, Karen L ^a   Coustry, Francoise ^a   Veerisetty, Alka C ^a   Liu, Peiman ^a   Alcorn, Joseph L ^a   Hecht, Jacqueline T ^a,b  

^a UNIVERSITY OF TEXAS MEDICAL SCHOOL   (United States)

^b Shriners Hospital for Children   (United States)

Author keywords

cell death; chondrodystrophy; COMP; genetics; growth plate; mutation

Indexed keywords

BUTYRIC ACID DERIVATIVE; LITHIUM; PHENYLBUTYRIC ACID; UNCLASSIFIED DRUG; VALPROIC ACID; CARTILAGE OLIGOMERIC MATRIX PROTEIN;

ACHONDROPLASIA; ANIMAL CELL; ANIMAL TISSUE; ARTICLE; ARTICULAR CARTILAGE; BONE GROWTH; BONE PLATE; CARTILAGE CELL; CARTILAGE OLIGOMERIC MATRIX PROTEIN GENE; CONTROLLED STUDY; FACE; GENE; GENE EXPRESSION; LIMB; MOUSE; NONHUMAN; PHENOTYPE; PSEUDOACHONDROPLASIA; SKELETON; SKULL; ANIMAL; DISEASE MODEL; GENETICS; HUMAN; INDEL MUTATION; METABOLISM; MUTANT MOUSE STRAIN; PATHOLOGY;

ACHONDROPLASIA; ANIMALS; CARTILAGE OLIGOMERIC MATRIX PROTEIN; CHONDROCYTES; DISEASE MODELS, ANIMAL; HUMANS; INDEL MUTATION; MICE; MICE, MUTANT STRAINS;

EID: 84899080287     PISSN: 08840431     EISSN: 15234681     Source Type: Journal    
DOI: 10.1002/jbmr.2139     Document Type: Article

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