Compromised paraspeckle formation as a pathogenic factor in FUSopathies

Human Molecular Genetics

Volumn 23, Issue 9, 2014, Pages 2298-2312

  Shelkovnikova, Tatyana A ^a   Robinson, Hannah K ^a   Troakes, Claire ^c   Ninkina, Natalia ^a,b   Buchman, Vladimir L ^a,b  

^a CARDIFF UNIVERSITY   (United Kingdom)

^b INSTITUTE OF PHYSIOLOGICALLY ACTIVE COMPOUNDS   (Russian Federation)

^c KING'S COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

FUSED IN SARCOMA PROTEIN; PRION PROTEIN; LONG UNTRANSLATED RNA; NEAT1 LONG NON-CODING RNA, HUMAN; RNA BINDING PROTEIN;

AMINO TERMINAL SEQUENCE; AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; CELL CULTURE; CELL INCLUSION; CELL NUCLEUS INCLUSION BODY; CELL STRUCTURE; CELLULAR STRESS RESPONSE; DEGENERATIVE DISEASE; GAIN OF FUNCTION MUTATION; HOMEOSTASIS; HUMAN; MOTONEURON; NONHUMAN; PATHOGENESIS; PRION; PRIORITY JOURNAL; PROTEIN INTERACTION; PROTEIN LOCALIZATION; PROTEIN METHYLATION; ANIMAL; CELL LINE; IN VITRO STUDY; METABOLISM; MOUSE; TRANSGENIC MOUSE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CELL LINE; CELLS, CULTURED; HUMANS; IN VITRO TECHNIQUES; INTRANUCLEAR INCLUSION BODIES; MICE; MICE, TRANSGENIC; RNA, LONG NONCODING; RNA-BINDING PROTEIN FUS;

EID: 84897500412     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddt622     Document Type: Article

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