Very-long-chain polyunsaturated fatty acids accumulate in phosphatidylcholine of fibroblasts from patients with Zellweger syndrome and acyl-CoA oxidase1 deficiency

Biochimica et Biophysica Acta - Molecular and Cell Biology of Lipids

Volumn 1841, Issue 4, 2014, Pages 610-619

  Abe, Yuichi ^a   Honsho, Masanori ^a   Nakanishi, Hiroki ^b   Taguchi, Ryo ^c   Fujiki, Yukio ^a  

^a KYUSHU UNIVERSITY   (Japan)

^b AKITA UNIVERSITY   (Japan)

^c CHUBU UNIVERSITY   (Japan)

Author keywords

Lipidomics; Peroxisomal oxidation; Peroxisome; Very long chain fatty acid; X ALD; Zellweger syndrome

Indexed keywords

ACYL COENZYME A OXIDASE 1; D BIFUNCTIONAL PROTEIN; DOCOSAHEXAENOIC ACID; MESSENGER RNA; MONOUNSATURATED FATTY ACID; PHOSPHATIDYLCHOLINE; PHOSPHATIDYLETHANOLAMINE; POLYUNSATURATED FATTY ACID; PROTEIN; UNCLASSIFIED DRUG; VERY LONG CHAIN POLYUNSATURATED FATTY ACID; VERY LONG CHAIN SATURATED FATTY ACID; ACYL COENZYME A; UNSATURATED FATTY ACID;

ACYL COENZYME A OXIDASE 1 DEFICIENCY; ADRENOLEUKODYSTROPHY; ARTICLE; CHONDRODYSPLASIA PUNCTATA; CONTROLLED STUDY; DISORDERS OF PEROXISOMAL FUNCTIONS; FIBROBLAST; HUMAN; HUMAN TISSUE; LIPID COMPOSITION; LIPID OXIDATION; LIPIDOMICS; PRIORITY JOURNAL; REAL TIME POLYMERASE CHAIN REACTION; RNA INTERFERENCE; TANDEM MASS SPECTROMETRY; ZELLWEGER SYNDROME; ANIMAL; CELL CULTURE; DEFICIENCY; GENETICS; HAMSTER; METABOLISM; OXIDATION REDUCTION REACTION; PATHOLOGY; PEROXISOME;

ACYL COENZYME A; ADRENOLEUKODYSTROPHY; ANIMALS; CELLS, CULTURED; CRICETINAE; FATTY ACIDS, UNSATURATED; FIBROBLASTS; HUMANS; OXIDATION-REDUCTION; PEROXISOMAL DISORDERS; PEROXISOMES; PHOSPHATIDYLCHOLINES; ZELLWEGER SYNDROME;

EID: 84896899993     PISSN: 13881981     EISSN: 18792618     Source Type: Journal    
DOI: 10.1016/j.bbalip.2014.01.001     Document Type: Article

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