Identification of the peroxisomal β-oxidation enzymes involved in the biosynthesis of docosahexaenoic acid

Journal of Lipid Research

Volumn 42, Issue 12, 2001, Pages 1987-1995

  Ferdinandusse, Sacha ^a   Denis, Simone ^a   Mooijer, Petra A W ^a   Zhang, Zhongyi ^b   Reddy, Janardan K ^b   Spector, Arthur A ^c   Wanders, Ronald J A ^a,d  

^a UNIVERSITY OF AMSTERDAM   (Netherlands)

^b NORTHWESTERN UNIVERSITY   (United States)

^c UNIVERSITY OF IOWA   (United States)

^d ACADEMIC MEDICAL CENTER   (Netherlands)

Author keywords

3 ketoacyl CoA thiolase; D bifunctional protein; Linolenic acid; Peroxisomal and mitochondrial fatty acid oxidation disorders; Polyunsaturated fatty acids; Sterol carrier protein X; Straight chain acyl CoA oxidase; Tetracosahexaenoic acid

Indexed keywords

ACETYL COENZYME A ACYLTRANSFERASE; ACYL COENZYME A OXIDASE; CARNITINE PALMITOYLTRANSFERASE; DOCOSAHEXAENOIC ACID; ICOSAPENTAENOIC ACID; LINOLENIC ACID; POLYUNSATURATED FATTY ACID; STEROL CARRIER PROTEIN;

ADRENOLEUKODYSTROPHY; ANIMAL CELL; ARTICLE; CHONDRODYSPLASIA PUNCTATA; CONTROLLED STUDY; DISORDERS OF PEROXISOMAL FUNCTIONS; ENZYME ANALYSIS; ENZYME DEFICIENCY; FATTY ACID OXIDATION; FATTY ACID SYNTHESIS; FIBROBLAST; HUMAN; HUMAN CELL; KNOCKOUT MOUSE; MITOCHONDRION; MOUSE; NONHUMAN; PEROXISOME; PRIORITY JOURNAL; PROTEIN DEFICIENCY; ZELLWEGER SYNDROME;

ACETYL-COA C-ACETYLTRANSFERASE; ACETYL-COA C-ACYLTRANSFERASE; ACYL-COA OXIDASE; ANIMALS; CARNITINE ACYLTRANSFERASES; CARRIER PROTEINS; CELL LINE; CHROMATOGRAPHY, HIGH PRESSURE LIQUID; DOCOSAHEXAENOIC ACIDS; FIBROBLASTS; HUMANS; LIPID METABOLISM, INBORN ERRORS; MICE; MICE, KNOCKOUT; MITOCHONDRIA; OXIDATION-REDUCTION; OXIDOREDUCTASES; PEROXISOMES; RADIOISOTOPES; ZELLWEGER SYNDROME;

EID: 0035658316     PISSN: 00222275     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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