메뉴 건너뛰기




Volumn 449, Issue 3, 2009, Pages 164-167

Phosphatidyl ethanolamine with increased polyunsaturated fatty acids in compensation for plasmalogen defect in the Zellweger syndrome brain

Author keywords

Peroxisome; Phosphatidyl ethanolamine; Plasmalogen; Polyunsaturated fatty acid; Zellweger syndrome

Indexed keywords

ARACHIDONIC ACID; DOCOSAPENTAENOIC ACID; PHOSPHATIDYLETHANOLAMINE; PLASMALOGEN; POLYUNSATURATED FATTY ACID;

EID: 57149119658     PISSN: 03043940     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.neulet.2008.11.004     Document Type: Article
Times cited : (19)

References (17)
  • 1
    • 1442333287 scopus 로고    scopus 로고
    • Plasmalogens: targets for oxidants and major lipophilic antioxidants
    • Engelmann B. Plasmalogens: targets for oxidants and major lipophilic antioxidants. Biochem. Soc. Trans. 32 (2004) 147-150
    • (2004) Biochem. Soc. Trans. , vol.32 , pp. 147-150
    • Engelmann, B.1
  • 3
    • 0001687866 scopus 로고    scopus 로고
    • The peroxisome biogenesis disorders
    • Scriver B.V., Beaudet S., Valle D., and Sly O. (Eds), McGraw-Hill, New York
    • Gould S.J., Raymond G.V., and Valle D. The peroxisome biogenesis disorders. In: Scriver B.V., Beaudet S., Valle D., and Sly O. (Eds). The Metabolic and Molecular Basis of Inherited Disease (2001), McGraw-Hill, New York 3181-3217
    • (2001) The Metabolic and Molecular Basis of Inherited Disease , pp. 3181-3217
    • Gould, S.J.1    Raymond, G.V.2    Valle, D.3
  • 4
    • 0025306009 scopus 로고
    • The Zellweger syndrome: deficient conversion of docosahexaenoic acid (22:6(n-3)) to eicosapentaenoic acid (20:5(n-3)) and normal delta4-desaturase activity in cultured skin fibroblasts
    • Grønn M., Christensen E., Hagve T.A., and Bjørn O. The Zellweger syndrome: deficient conversion of docosahexaenoic acid (22:6(n-3)) to eicosapentaenoic acid (20:5(n-3)) and normal delta4-desaturase activity in cultured skin fibroblasts. Biochim. Biophys. Acta 1044 (1990) 249-254
    • (1990) Biochim. Biophys. Acta , vol.1044 , pp. 249-254
    • Grønn, M.1    Christensen, E.2    Hagve, T.A.3    Bjørn, O.4
  • 5
    • 0031041126 scopus 로고    scopus 로고
    • On the molecular etiology of decreased arachidonic (20:4n-6), docosapentaenoic (22:5n-6) and docosahexaenoic (22:6n-3) acids in Zellweger syndrome and other peroxisomal disorders
    • Infante J.P., and Huszagh V.A. On the molecular etiology of decreased arachidonic (20:4n-6), docosapentaenoic (22:5n-6) and docosahexaenoic (22:6n-3) acids in Zellweger syndrome and other peroxisomal disorders. Mol. Cell. Biochem. 168 (1997) 101-115
    • (1997) Mol. Cell. Biochem. , vol.168 , pp. 101-115
    • Infante, J.P.1    Huszagh, V.A.2
  • 6
    • 7044224838 scopus 로고    scopus 로고
    • Membrane fluidity and its roles in the perception of environmental signals
    • Los D.A., and Murata N. Membrane fluidity and its roles in the perception of environmental signals. Biochim. Biophys. Acta 1666 (2004) 142-157
    • (2004) Biochim. Biophys. Acta , vol.1666 , pp. 142-157
    • Los, D.A.1    Murata, N.2
  • 7
    • 0025039469 scopus 로고
    • Severe deficiency of docosahexaenoic acid in peroxisomal disorders: a defect of delta 4 desaturation?
    • Martinez M. Severe deficiency of docosahexaenoic acid in peroxisomal disorders: a defect of delta 4 desaturation?. Neurology 40 (1990) 1292-1298
    • (1990) Neurology , vol.40 , pp. 1292-1298
    • Martinez, M.1
  • 8
    • 0026715768 scopus 로고
    • Abnormal profiles of polyunsaturated fatty acids in the brain, liver, kidney and retina of patients with peroxisomal disorders
    • Martinez M. Abnormal profiles of polyunsaturated fatty acids in the brain, liver, kidney and retina of patients with peroxisomal disorders. Brain Res. 583 (1992) 171-182
    • (1992) Brain Res. , vol.583 , pp. 171-182
    • Martinez, M.1
  • 9
    • 0032932397 scopus 로고    scopus 로고
    • Plasma very long chain fatty acids in 3,000 peroxisome disease patients and 29,000 controls
    • Moser A.B., Kreiter N., Bezman L., Lu S., Raymond G.V., Naidu S., and Moser H.M. Plasma very long chain fatty acids in 3,000 peroxisome disease patients and 29,000 controls. Ann. Neurol. 45 (1999) 100-110
    • (1999) Ann. Neurol. , vol.45 , pp. 100-110
    • Moser, A.B.1    Kreiter, N.2    Bezman, L.3    Lu, S.4    Raymond, G.V.5    Naidu, S.6    Moser, H.M.7
  • 10
    • 0035102918 scopus 로고    scopus 로고
    • Plasmalogens: biosynthesis and functions
    • Nagan N., and Zoeller R.A. Plasmalogens: biosynthesis and functions. Prog. Lipid Res. 40 (2001) 199-229
    • (2001) Prog. Lipid Res. , vol.40 , pp. 199-229
    • Nagan, N.1    Zoeller, R.A.2
  • 11
    • 1542273632 scopus 로고    scopus 로고
    • Alterations of FFA metabolism and membrane fluidity in peroxisome-defective mutant ZP102 cells
    • Nagura M., Saito M., Iwamori M., Sakakihara Y., and Igarashi T. Alterations of FFA metabolism and membrane fluidity in peroxisome-defective mutant ZP102 cells. Lipids 39 (2004) 43-50
    • (2004) Lipids , vol.39 , pp. 43-50
    • Nagura, M.1    Saito, M.2    Iwamori, M.3    Sakakihara, Y.4    Igarashi, T.5
  • 12
    • 0024550933 scopus 로고
    • Structural and chemical alterations in the cerebral maldevelopment of fetal cerebro-hepato-renal (Zellweger) syndrome
    • Powers J.M., Tummons R.C., Caviness Jr. V.S., Moser A.B., and Moser H.W. Structural and chemical alterations in the cerebral maldevelopment of fetal cerebro-hepato-renal (Zellweger) syndrome. J. Neuropath. Exp. Neurol. 48 (1989) 270-289
    • (1989) J. Neuropath. Exp. Neurol. , vol.48 , pp. 270-289
    • Powers, J.M.1    Tummons, R.C.2    Caviness Jr., V.S.3    Moser, A.B.4    Moser, H.W.5
  • 13
    • 0033583582 scopus 로고    scopus 로고
    • Accumulation of glycolipids in mutant Chinese hamster ovary cells (Z65) with defective peroxisomal assembly and comparison of the metabolic rate of glycosphingolipids between Z65 cells and wild-type CHO-K1 cells
    • Saito M., Iwamori M., Lin B., Oka A., Fujiki Y., Shimozawa N., Kamoshita S., Yanagisawa M., and Sakakihara Y. Accumulation of glycolipids in mutant Chinese hamster ovary cells (Z65) with defective peroxisomal assembly and comparison of the metabolic rate of glycosphingolipids between Z65 cells and wild-type CHO-K1 cells. Biochim. Biophys. Acta 1438 (1999) 55-62
    • (1999) Biochim. Biophys. Acta , vol.1438 , pp. 55-62
    • Saito, M.1    Iwamori, M.2    Lin, B.3    Oka, A.4    Fujiki, Y.5    Shimozawa, N.6    Kamoshita, S.7    Yanagisawa, M.8    Sakakihara, Y.9
  • 14
    • 34249651910 scopus 로고    scopus 로고
    • Alterations in the molecular species of plasmalogen phospholipids and glycolipids due to peroxisomal dysfunction in Chinese hamster ovary-mutant Z65 cells by FABMS method
    • Saito M., Horikawa M., Iwamori Y., Sakakihara Y., Mizuguchi M., Igarashi T., Fujiki Y., and Iwamori M. Alterations in the molecular species of plasmalogen phospholipids and glycolipids due to peroxisomal dysfunction in Chinese hamster ovary-mutant Z65 cells by FABMS method. J. Chromatogr. B 852 (2007) 367-373
    • (2007) J. Chromatogr. B , vol.852 , pp. 367-373
    • Saito, M.1    Horikawa, M.2    Iwamori, Y.3    Sakakihara, Y.4    Mizuguchi, M.5    Igarashi, T.6    Fujiki, Y.7    Iwamori, M.8
  • 16
    • 0014329483 scopus 로고
    • Distribution and fatty acid composition of phosphoglycerides in normal human brain
    • Svennerholm L. Distribution and fatty acid composition of phosphoglycerides in normal human brain. J. Lipid Res. 9 (1968) 570-579
    • (1968) J. Lipid Res. , vol.9 , pp. 570-579
    • Svennerholm, L.1


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.