Enhanced expression of a-series gangliosides in fibroblasts of patients with peroxisome biogenesis disorders

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1535, Issue 3, 2001, Pages 285-293

  Tatsumi, K ^a   Saito, M ^a   Lin, B ^a   Iwamori, M ^b   Ichiseki, H ^a   Shimozawa, N ^c   Kamoshita, S ^d   Igarashi, T ^a   Sakakihara, Y ^a  

^a UNIVERSITY OF TOKYO   (Japan)

^b KINKI UNIVERSITY   (Japan)

^c GIFU UNIVERSITY   (Japan)

^d NATIONAL CENTER FOR GLOBAL HEALTH AND MEDICINE   (Japan)

Author keywords

Fibroblast; Ganglioside; Infantile Refsum disease; Zellweger syndrome

Indexed keywords

GANGLIOSIDE GD 1A; GANGLIOSIDE GM1; GANGLIOSIDE GM2; GANGLIOSIDE GM3; GLYCOSPHINGOLIPID;

APOPTOSIS; ARTICLE; CASE REPORT; CELL DIFFERENTIATION; CELL PROLIFERATION; CONTROLLED STUDY; FEMALE; FIBROBLAST; HUMAN; HUMAN CELL; IMMUNOHISTOCHEMISTRY; INFANT; LIPID METABOLISM; NERVE CELL; PATHOGENESIS; PRESCHOOL CHILD; PRIORITY JOURNAL; REFSUM DISEASE; ZELLWEGER SYNDROME;

FIBROBLASTS; G(M3) GANGLIOSIDE; GANGLIOSIDES; HUMANS; IMMUNOHISTOCHEMISTRY; INFANT; PEROXISOMAL DISORDERS; REFSUM DISEASE; ZELLWEGER SYNDROME;

EID: 0035953036     PISSN: 09254439     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0925-4439(01)00027-8     Document Type: Article

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