Experimental evidence for protein oxidative damage and altered antioxidant defense in patients with medium-chain acyl-CoA dehydrogenase deficiency

Journal of Inherited Metabolic Disease

Volumn 37, Issue 5, 2014, Pages 783-789

  Derks, Terry G J ^a,b,c   Touw, Catharina M L ^a,b   Ribas, Graziela S ^c,d   Biancini, Giovana B ^c,d   Vanzin, Camila S ^c,d   Negretto, Giovanna ^c,d   Mescka, Caroline P ^c,d   Reijngoud, Dirk Jan ^a,b   Smit, G Peter A ^a   Wajner, Moacir ^c,d   Vargas, Carmen R ^c,d  

^a UNIVERSITY MEDICAL CENTER GRONINGEN   (Netherlands)

^b UNIVERSITY OF GRONINGEN   (Netherlands)

^c FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^d HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

Author keywords

[No Author keywords available]

Indexed keywords

ACYL COENZYME A DEHYDROGENASE; ANTIOXIDANT; CARNITINE; PROTEIN; RIBOFLAVIN; VITAMIN;

ADOLESCENT; ADULT; CHILD; CROSS-SECTIONAL STUDY; DEFICIENCY; DISORDERS OF LIPID AND LIPOPROTEIN METABOLISM; ERYTHROCYTE; FEMALE; GENETICS; HUMAN; INFANT; LIPID METABOLISM; MALE; METABOLISM; NEWBORN; OXIDATIVE STRESS; PRESCHOOL CHILD; YOUNG ADULT;

ACYL-COA DEHYDROGENASE; ADOLESCENT; ADULT; ANTIOXIDANTS; CARNITINE; CHILD; CHILD, PRESCHOOL; CROSS-SECTIONAL STUDIES; ERYTHROCYTES; FEMALE; HUMANS; INFANT; INFANT, NEWBORN; LIPID METABOLISM; LIPID METABOLISM, INBORN ERRORS; MALE; OXIDATIVE STRESS; PROTEINS; RIBOFLAVIN; VITAMINS; YOUNG ADULT;

EID: 84895775773     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-014-9700-0     Document Type: Article

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