Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice

Pediatric Research

Volumn 57, Issue 6, 2005, Pages 760-764

  Spiekerkoetter, Ute ^a,b,c   Tokunaga, Chonan ^b   Wendel, Udo ^a   Mayatepek, Ertan ^a   Ijlst, Lodewijk ^c   Vaz, Frederic M ^c   Van Vlies, Naomi ^c   Overmars, Henk ^c   Duran, Marinus ^c   Wijburg, Frits A ^c   Wanders, Ronald J ^c   Strauss, Arnold W ^b  

^a UNIVERSITY HOSPITAL DÜSSELDORF   (Germany)

^b MONROE CARELL JR CHILDREN S HOSPITAL AT VANDERBILT   (United States)

^c UNIVERSITY OF AMSTERDAM   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

ACETONITRILE; ACYLCARNITINE; ACYLCARNITINE BUTYL ESTER; CARNITINE; ESTER; LONG CHAIN FATTY ACID; METHANOL; OXIDOREDUCTASE; UNCLASSIFIED DRUG; VERY LONG CHAIN ACYL COENZYME A DEHYDRODENASE;

AMINO ACID SYNTHESIS; ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; BILE; BLOOD; BODY FLUID; CLINICAL FEATURE; CONTROLLED STUDY; DIET RESTRICTION; ELECTROSPRAY MASS SPECTROMETRY; ENZYME DEFICIENCY; EXERCISE; FATTY ACID OXIDATION; HOMEOSTASIS; KNOCKOUT MOUSE; LIVER; MOUSE; NONHUMAN; PATHOGENESIS; PHENOTYPE; PRIORITY JOURNAL; SKELETAL MUSCLE; STRESS;

ACYL-COA DEHYDROGENASE, LONG-CHAIN; ANIMALS; BILE; CARNITINE; DISEASE MODELS, ANIMAL; HOMEOSTASIS; HUMANS; LIPID METABOLISM, INBORN ERRORS; LIVER; MICE; MICE, KNOCKOUT; MUSCLE, SKELETAL; PHENOTYPE;

EID: 21144445376     PISSN: 00313998     EISSN: None     Source Type: Journal    
DOI: 10.1203/01.PDR.0000157915.26049.47     Document Type: Article

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