Oxidative stress parameters in urine from patients with disorders of propionate metabolism: A beneficial effect of L-carnitine supplementation

Cellular and Molecular Neurobiology

Volumn 32, Issue 1, 2012, Pages 77-82

  Ribas, Graziela S ^a,b   Biancini, Giovana B ^a,b   Mescka, Caroline ^a,b   Wayhs, Carlos Y ^a,b   Sitta, Angela ^a,b   Wajner, Moacir ^a,b   Vargas, Carmen R ^a,b  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^b HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

Author keywords

L Carnitine; Methylmalonic aciduria; Oxidative stress; Propionic aciduria

Indexed keywords

AMINO ACID; BIOLOGICAL MARKER; CARNITINE; ISOPROSTANE; PROPIONIC ACID; TYROSINE;

ARTICLE; CHILD; CHILD HEALTH; CLINICAL ARTICLE; CLINICAL ASSESSMENT; CLINICAL EVALUATION; CONTROLLED STUDY; DRUG EFFECT; FOLLOW UP; HUMAN; INFANT; LIPID PEROXIDATION; METHYLMALONIC ACIDURIA; OXIDATIVE STRESS; PRESCHOOL CHILD; PRIORITY JOURNAL; PROPIONIC ACIDEMIA; PROTEIN RESTRICTION; SCHOOL CHILD; TREATMENT DURATION; URINALYSIS; URINE LEVEL;

AMINO ACID METABOLISM, INBORN ERRORS; ANTIOXIDANTS; CARNITINE; CHILD; CHILD, PRESCHOOL; DIET, PROTEIN-RESTRICTED; DIETARY SUPPLEMENTS; HUMANS; INFANT; INFANT, NEWBORN; MATCHED-PAIR ANALYSIS; METHYLMALONIC ACID; OXIDATIVE STRESS; PROPIONATES; TREATMENT OUTCOME; TYROSINE;

EID: 84856553552     PISSN: 02724340     EISSN: 15736830     Source Type: Journal    
DOI: 10.1007/s10571-011-9736-8     Document Type: Article

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