Disease-Associated Mutations of TDP-43 Promote Turnover of the Protein Through the Proteasomal Pathway

Molecular Neurobiology

Volumn 50, Issue 3, 2014, Pages 1049-1058

  Araki, Wataru ^a   Minegishi, Seiji ^a   Motoki, Kazumi ^a,d   Kume, Hideaki ^a   Hohjoh, Hirohiko ^a   Araki, Yumiko M ^a,b   Tamaoka, Akira ^c  

^a NATIONAL INSTITUTE OF NEUROSCIENCE   (Japan)

^b JUNTENDO UNIVERSITY   (Japan)

^c UNIVERSITY OF TSUKUBA   (Japan)

^d NATIONAL INSTITUTE FOR PHYSIOLOGICAL SCIENCES   (Japan)

Author keywords

Amyotrophic lateral sclerosis; Frontotemporal lobar degeneration; Mutation; Proteasome; TDP 43

Indexed keywords

DNA BINDING PROTEIN; PROTEASOME; PROTEIN TDP-43;

AMYOTROPHIC LATERAL SCLEROSIS; BRAIN; CELL INCLUSION; FRONTOTEMPORAL DEMENTIA; GENETICS; HUMAN; METABOLISM; MUTATION; PATHOLOGY; PHOSPHORYLATION; TUMOR CELL LINE;

AMYOTROPHIC LATERAL SCLEROSIS; BRAIN; CELL LINE, TUMOR; DNA-BINDING PROTEINS; FRONTOTEMPORAL LOBAR DEGENERATION; HUMANS; INCLUSION BODIES; MUTATION; PHOSPHORYLATION; PROTEASOME ENDOPEPTIDASE COMPLEX;

EID: 84892906042     PISSN: 08937648     EISSN: 15591182     Source Type: Journal    
DOI: 10.1007/s12035-014-8644-6     Document Type: Article

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