The nebulin SH3 domain is dispensable for normal skeletal muscle structure but is required for effective active load bearing in mouse

Journal of Cell Science

Volumn 126, Issue 23, 2013, Pages 5477-5489

  Yamamoto, Daniel L ^a   Vitiello, Carmen ^b   Zhang, Jianlin ^c   Gokhin, David S ^d   Castaldi, Alessandra ^e,f   Coulis, Gerald ^b   Piaser, Fabio ^e,f   Filomena, Maria Carmela ^f,g   Eggenhuizen, Peter J ^a   Kunderfranco, Paolo ^e,f   Camerini, Serena ^h   Takano, Kazunori ⁱ   Endo, Takeshi ⁱ   Crescenzi, Marco ^h   Luther, Pradeep K L ^j   Lieber, Richard L ^d   Chen, Ju ^c   Bang, Marie Louise ^e,f  

^a INSTITUTE OF BIOMEDICAL TECHNOLOGIES   (Italy)

^b IRCCS MULTIMEDICA   (Italy)

^c UNIVERSITY OF CALIFORNIA   (United States)

^d UNIVERSITY OF CALIFORNIA SAN DIEGO   (United States)

^e Milan Unit   (Italy)

^f HUMANITAS CLINICAL AND RESEARCH CENTER   (Italy)

^g UNIVERSITY OF MILAN   (Italy)

^h ISTITUTO SUPERIORE DI SANITÀ   (Italy)

ⁱ CHIBA UNIVERSITY   (Japan)

^j NATIONAL HEART AND LUNG INSTITUTE   (United Kingdom)

more..

Author keywords

Nebulin; Nemaline myopathy; Sarcomere; Skeletal muscle; Z line

Indexed keywords

MUSCLE PROTEIN; MYOPALLADIN; NEBULIN; NEURAL WISKOTT ALDRICH SYNDROME PROTEIN; PALLADIN; PROTEIN SH3; UNCLASSIFIED DRUG; ZYXIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; ECCENTRIC MUSCLE CONTRACTION; FUNCTIONAL PROTEOMICS; GENE DELETION; GENE EXPRESSION; GENE LOCATION; MOUSE; MUSCLE CELL; MUSCLE INJURY; MUSCLE STRENGTH; MUSCLE TETANIC CONTRACTION; NONHUMAN; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN PROTEIN INTERACTION; SKELETAL MUSCLE; STOP CODON; WEIGHT BEARING;

NEBULIN; NEMALINE MYOPATHY; SARCOMERE; SKELETAL MUSCLE; Z-LINE;

ANIMALS; CYTOSKELETAL PROTEINS; ELASTIC MODULUS; EXCITATION CONTRACTION COUPLING; FEMALE; GENE EXPRESSION; HUMANS; ISOMETRIC CONTRACTION; MALE; MICE; MUSCLE PROTEINS; MUSCLE, SKELETAL; MYOPATHIES, NEMALINE; PHOSPHOPROTEINS; PROTEIN BINDING; PROTEIN STRUCTURE, TERTIARY; TENSILE STRENGTH; WEIGHT-BEARING; WISKOTT-ALDRICH SYNDROME PROTEIN, NEURONAL; ZYXIN;

EID: 84890244333     PISSN: 00219533     EISSN: 14779137     Source Type: Journal    
DOI: 10.1242/jcs.137026     Document Type: Article

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