Induced pluripotent stem cells from friedreich ataxia patients fail to upregulate frataxin during in vitro differentiation to peripheral sensory neurons

Stem Cells and Development

Volumn 22, Issue 24, 2013, Pages 3271-3282

  Eigentler, Andreas ^a   Boesch, Sylvia ^a   Schneider, Rainer ^b   Dechant, Georg ^a   Nat, Roxana ^a  

^a INNSBRUCK MEDICAL UNIVERSITY   (Austria)

^b UNIVERSITY OF INNSBRUCK   (Austria)

Author keywords

[No Author keywords available]

Indexed keywords

FRATAXIN;

ADULT; ARTICLE; CASE REPORT; CHILD; CONTROLLED STUDY; EMBRYO; FEMALE; FRIEDREICH ATAXIA; HUMAN; HUMAN CELL; IN VITRO STUDY; MALE; NERVE CELL DIFFERENTIATION; NERVE DEGENERATION; NEURAL CREST CELL; ONTOGENY; PLURIPOTENT STEM CELL; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN EXPRESSION; SENSORY NERVE CELL; TRINUCLEOTIDE REPEAT; UPREGULATION;

CELL DIFFERENTIATION; FRIEDREICH ATAXIA; GENE EXPRESSION REGULATION; HUMANS; INDUCED PLURIPOTENT STEM CELLS; IRON-BINDING PROTEINS; SENSORY RECEPTOR CELLS;

EID: 84889657597     PISSN: 15473287     EISSN: 15578534     Source Type: Journal    
DOI: 10.1089/scd.2013.0126     Document Type: Article

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