Pathology and pathogenesis of sensory neuropathy in Friedreich's ataxia

Acta Neuropathologica

Volumn 120, Issue 1, 2010, Pages 97-108

  Morral, Jennifer A ^a   Davis, Ashley N ^a   Qian, Jiang ^b   Gelman, Benjamin B ^c   Koeppen, Arnulf H ^a,b  

^a STRATTON VA MEDICAL CENTER   (United States)

^b ALBANY MEDICAL COLLEGE   (United States)

^c UNIVERSITY OF TEXAS MEDICAL BRANCH   (United States)

Author keywords

Axons; Friedreich's ataxia; Laminin; Myelin sheath; Neural crest; S100 protein; Schwann cells; Sural nerve

Indexed keywords

BETA TUBULIN; FERRITIN; FERROPORTIN; LAMININ; MYELIN BASIC PROTEIN; PERIPHERAL MYELIN PROTEIN 22; PROTEIN S 100; CATION TRANSPORT PROTEIN; METAL TRANSPORTING PROTEIN 1;

ADULT; AGED; ARTICLE; AUTOPSY; CELL INTERACTION; CELL MIGRATION; CELLULAR DISTRIBUTION; CLINICAL ARTICLE; CONTROLLED STUDY; CYTOPLASM; DORSAL ROOT; ELECTRON MICROSCOPY; FEMALE; FRIEDREICH ATAXIA; HISTOPATHOLOGY; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOCYTOCHEMISTRY; IMMUNOREACTIVITY; MALE; MYELINATED NERVE; NERVE FIBER; NERVE FIBER DEGENERATION; NERVE SHEATH; NEURAL CREST; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN LOCALIZATION; SCHWANN CELL; SENSORY NERVE; SENSORY NEUROPATHY; SURAL NERVE; ADOLESCENT; CASE CONTROL STUDY; CHILD; METABOLISM; MIDDLE AGED; NEUROPATHY; PATHOLOGY; PRESCHOOL CHILD; ULTRASTRUCTURE; YOUNG ADULT;

ADOLESCENT; ADULT; AGED; AXONS; CASE-CONTROL STUDIES; CATION TRANSPORT PROTEINS; CHILD; CHILD, PRESCHOOL; FEMALE; FERRITINS; FRIEDREICH ATAXIA; HEREDITARY SENSORY AND AUTONOMIC NEUROPATHIES; HUMANS; MALE; MIDDLE AGED; NERVE FIBERS, MYELINATED; SCHWANN CELLS; SURAL NERVE; YOUNG ADULT;

EID: 77953871516     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-010-0675-0     Document Type: Article

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