Recruitment into stress granules prevents irreversible aggregation of FUS protein mislocalized to the cytoplasm

Cell Cycle

Volumn 12, Issue 19, 2013, Pages 3383-3391

  Shelkovnikova, Tatyana A ^a,b   Robinson, Hannah K ^a   Connor Robson, Natalie ^a   Buchman, Vladimir L ^a,b  

^a CARDIFF UNIVERSITY   (United Kingdom)

^b INSTITUTE OF PHYSIOLOGICALLY ACTIVE COMPOUNDS   (Russian Federation)

Author keywords

Amyotrophic lateral sclerosis; Cytoplasmic RNP complexes; FUSopathy; Pro tein aggre gation; Proteinopathy; RNA binding proteins

Indexed keywords

FUSED IN SARCOMA PROTEIN; TAR DNA BINDING PROTEIN;

AGGRESOME; AMINO ACID SUBSTITUTION; ANIMAL CELL; ARTICLE; CARBOXY TERMINAL SEQUENCE; CELLULAR DISTRIBUTION; CYTOPLASM; HUMAN; HUMAN CELL; NONHUMAN; NUCLEAR LOCALIZATION SIGNAL; PROTEIN AGGREGATION; PROTEIN LOCALIZATION; RNA BINDING; STRESS;

AMYOTROPHIC LATERAL SCLEROSIS; CYTOPLASMIC RNP COMPLEXES; FUSOPATHY; PROTEIN AGGREGATION; PROTEINOPATHY; RNA-BINDING PROTEINS;

CELL LINE, TUMOR; CYTOPLASM; CYTOPLASMIC GRANULES; HUMANS; MUTATION; PROTEIN BINDING; PROTEIN STRUCTURE, TERTIARY; RECOMBINANT FUSION PROTEINS; RNA; RNA-BINDING PROTEIN FUS;

EID: 84886681536     PISSN: 15384101     EISSN: 15514005     Source Type: Journal    
DOI: 10.4161/cc.26241     Document Type: Article

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