N-Acetyl-L-Cysteine Prevents Stress-Induced Desmin Aggregation in Cellular Models of Desminopathy

PLoS ONE

Volumn 8, Issue 10, 2013, Pages

  Segard, Bertrand David ^a   Delort, Florence ^a   Bailleux, Virginie ^b   Simon, Stéphanie ^a,c   Leccia, Emilie ^b,d   Gausseres, Blandine ^a   Briki, Fatma ^b   Vicart, Patrick ^a   Batonnet Pichon, Sabrina ^a  

^a UNIVERSITÉ PARIS DESCARTES   (France)

^b UNIVERSITÉ PARIS SACLAY   (France)

^c HENRI MONDOR HOSPITAL   (France)

^d PSL RESEARCH UNIVERSITY   (France)

Author keywords

[No Author keywords available]

Indexed keywords

ACETYLCYSTEINE; COMPLEMENTARY DNA; DESMIN; DEXAMETHASONE; FISETIN;

ANIMAL CELL; ANTIOXIDANT ACTIVITY; ARTICLE; CELL PROTECTION; CONTROLLED STUDY; DESMIN GENE; DESMINOPATHY; GENE; GENE MUTATION; MECHANICAL STRESS; MOLECULAR CLONING; MOLECULAR MODEL; MOUSE; MYOPATHY; NONHUMAN; OXIDATION REDUCTION STATE; OXIDATIVE STRESS; PROTEIN AGGREGATION; PROTEIN DOMAIN; TEMPERATURE STRESS; WILD TYPE;

ACETYLCYSTEINE; ANIMALS; CARDIOMYOPATHIES; CELL LINE; CODON; CYTOSKELETON; DESMIN; DISEASE MODELS, ANIMAL; ENDOPLASMIC RETICULUM STRESS; GENE EXPRESSION; HEAT-SHOCK PROTEINS; HUMANS; MICE; MUSCULAR DYSTROPHIES; MUTATION; PROTEIN BINDING; STRESS, PHYSIOLOGICAL;

EID: 84885060583     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0076361     Document Type: Article

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