Desmin mutations in the terminal consensus motif prevent synemin-desmin heteropolymer filament assembly

Experimental Cell Research

Volumn 317, Issue 6, 2011, Pages 886-897

  Chourbagi, Oussama ^a   Bruston, Francine ^a   Carinci, Marianna ^a   Xue, Zhigang ^b   Vicart, Patrick ^a   Paulin, Denise ^b   Agbulut, Onnik ^a  

^a UNIVERSITÉ PARIS DESCARTES   (France)

^b SORBONNE UNIVERSITÉ   (France)

Author keywords

Desminopathy; Desmuslin; Intermediate filaments; Salt bridges

Indexed keywords

DESMIN; DIMER; INTERMEDIATE FILAMENT PROTEIN; MUTANT PROTEIN; PROTEIN SYNEMIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ARTICLE; COMPUTER MODEL; EX VIVO STUDY; HUMAN; HUMAN CELL; MOUSE; MUTATION; NONHUMAN; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; PROTEIN MOTIF; PROTEIN STRUCTURE;

EID: 79952186178     PISSN: 00144827     EISSN: 10902422     Source Type: Journal    
DOI: 10.1016/j.yexcr.2011.01.013     Document Type: Article

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