Biomechanical characterization of a desminopathy in primary human myoblasts

Biochemical and Biophysical Research Communications

Volumn 419, Issue 4, 2012, Pages 703-707

  Bonakdar, Navid ^a   Luczak, Justyna ^a   Lautscham, Lena ^a   Czonstke, Maja ^a   Koch, Thorsten M ^a   Mainka, Astrid ^a   Jungbauer, Tajana ^b   Goldmann, Wolfgang H ^a   Schröder, Rolf ^b   Fabry, Ben ^a  

^a UNIVERSITY OF ERLANGEN NUREMBERG   (Germany)

^b UNIVERSITY HOSPITAL ERLANGEN   (Germany)

Author keywords

Cell stretcher; Desmin; Desminopathy; Intermediate filaments; Magnetic tweezer; Myofibrillar myopathy

Indexed keywords

DESMIN;

ARTICLE; CELL DEATH; CONTROLLED STUDY; DESMINOPATHY; GENE MUTATION; HETEROZYGOSITY; HUMAN; HUMAN CELL; IN VITRO STUDY; MECHANICAL STRESS; MUSCLE INJURY; MYOBLAST; MYOPATHY; PRIORITY JOURNAL; PROTEIN EXPRESSION; SARCOPLASM; SKELETAL MUSCLE; WILD TYPE;

ARGININE; CELL ADHESION; CELLS, CULTURED; CYTOSKELETON; DESMIN; HUMANS; MUSCULAR DISEASES; MUTATION, MISSENSE; MYOBLASTS; PROLINE; STRESS, MECHANICAL;

EID: 84858750382     PISSN: 0006291X     EISSN: 10902104     Source Type: Journal    
DOI: 10.1016/j.bbrc.2012.02.083     Document Type: Article

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