Oxidative stress and successful antioxidant treatment in models of RYR1-related myopathy

Brain

Volumn 135, Issue 4, 2012, Pages 1115-1127

  Dowling, James J ^a   Arbogast, Sandrine ^b,c   Hur, Junguk ^a   Nelson, Darcee D ^a   McEvoy, Anna ^a   Waugh, Trent ^a   Marty, Isabelle ^d   Lunardi, Joel ^d,e   Brooks, Susan V ^a   Kuwada, John Y ^a   Ferreiro, Ana ^b,c,f,g  

^a UNIVERSITY OF MICHIGAN HEALTH SYSTEM   (United States)

^b INSERM   (France)

^c SORBONNE UNIVERSITÉ   (France)

^d GRENOBLE INSTITUT DES NEUROSCIENCES   (France)

^e GRENOBLE UNIVERSITY HOSPITAL   (France)

^f ASSISTANCE PUBLIQUE HÔPITAUX DE PARIS   (France)

^g RAYMOND POINCARÉ HOSPITAL   (France)

Author keywords

antioxidant response; myopathies; neuromuscular disorders; oxidative stress

Indexed keywords

ACETYLCYSTEINE; CATALASE; COPPER ZINC SUPEROXIDE DISMUTASE; CYCLOOXYGENASE 2; CYTOCHROME B; CYTOCHROME B245; EXTRACELLULAR SUPEROXIDE DISMUTASE; MANGANESE SUPEROXIDE DISMUTASE; MONOOXYGENASE DBH LIKE 1; NEUTROPHIL CYTOSOLIC FACTOR 1; NEUTROPHIL CYTOSOLIC FACTOR 2; PROTEIN; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE PHOSPHATE OXIDASE 2; RYANODINE RECEPTOR 1; SELENOPROTEIN; SELENOPROTEIN P; SELENOPROTEIN S; UNCLASSIFIED DRUG; UNSPECIFIC MONOOXYGENASE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL SURVIVAL; CONTROLLED STUDY; DRUG EFFICACY; EMBRYO; EX VIVO STUDY; GENE EXPRESSION; GENETIC ASSOCIATION; HUMAN; HUMAN CELL; IN VIVO STUDY; MICROARRAY ANALYSIS; MITOCHONDRION; MUSCLE FUNCTION; MYOPATHY; MYOTUBE; NONHUMAN; OXIDATIVE STRESS; PATHOPHYSIOLOGY; PRIORITY JOURNAL; RYR1 RELATED MYOPATHY; SIGNAL TRANSDUCTION; ZEBRA FISH;

EID: 84860156013     PISSN: 00068950     EISSN: 14602156     Source Type: Journal    
DOI: 10.1093/brain/aws036     Document Type: Article

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