Viral-mediated expression of desmin mutants to create mouse models of myofibrillar myopathy

Skeletal Muscle

Volumn 3, Issue 1, 2013, Pages

  Joanne, Pierre ^a   Chourbagi, Oussama ^a   Hourdé, Christophe ^b   Ferry, Arnaud ^a,b   Butler Browne, Gillian ^b   Vicart, Patrick ^a   Dumonceaux, Julie ^b   Agbulut, Onnik ^a  

^a UNIVERSITÉ PARIS DESCARTES   (France)

^b SORBONNE UNIVERSITÉ   (France)

Author keywords

AAV vectors; Desmin; Desminopathy; Intermediate filament; Myofibrillar myopathy; Phenotypic heterogeneity

Indexed keywords

EID: 84874964600     PISSN: None     EISSN: 20445040     Source Type: Journal    
DOI: 10.1186/2044-5040-3-4     Document Type: Article

References (43)

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