Oxidative stress in desminopathies and myotilinopathies: A link between oxidative damage and abnormal protein aggregation

Brain Pathology

Volumn 17, Issue 4, 2007, Pages 377-388

  Janué, Anna ^a   Olivé, Montse ^a   Ferrer, Isidre ^a  

^a HOSPITAL UNIVERSITARI DE BELLVITGE   (Spain)

Author keywords

[No Author keywords available]

Indexed keywords

3 NITROTYROSINE; 4 HYDROXYNONENAL; ADVANCED GLYCATION END PRODUCT; ENDOTHELIAL NITRIC OXIDE SYNTHASE; INDUCIBLE NITRIC OXIDE SYNTHASE; ISOENZYME; ISOPROTEIN; MALONALDEHYDE; N CARBOXYETHYLLYSINE; N CARBOXYMETHYLLYSINE; NEURONAL NITRIC OXIDE SYNTHASE; PROTEIN P62; REACTIVE OXYGEN METABOLITE; SUPEROXIDE DISMUTASE; UBIQUITIN; UNCLASSIFIED DRUG;

ARTICLE; CONFOCAL MICROSCOPY; CONTROLLED STUDY; DESMINOPATHY; DISEASE ASSOCIATION; GEL ELECTROPHORESIS; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOFLUORESCENCE TEST; IMMUNOHISTOCHEMISTRY; MUSCLE BIOPSY; MUSCLE CELL; MYOPATHY; MYOTILINOPATHY; NITRATION; OXIDATIVE STRESS; PATHOPHYSIOLOGY; PROTEIN AGGREGATION; PROTEIN DEGRADATION; PROTEIN FOLDING; WESTERN BLOTTING;

ADULT; AGED; AGED, 80 AND OVER; BIOLOGICAL MARKERS; CYTOSKELETAL PROTEINS; DESMIN; FEMALE; GLYCOSYLATION END PRODUCTS, ADVANCED; HUMANS; LIPID PEROXIDATION; MALE; MIDDLE AGED; MUSCLE PROTEINS; MUSCULAR DISEASES; MYOFIBRILS; NITRIC OXIDE SYNTHASE; NITRO COMPOUNDS; OXIDATIVE STRESS; PROTEASOME ENDOPEPTIDASE COMPLEX; SUPEROXIDE DISMUTASE;

EID: 35148847303     PISSN: 10156305     EISSN: None     Source Type: Journal    
DOI: 10.1111/j.1750-3639.2007.00087.x     Document Type: Article

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