Diminished exercise capacity and mitochondrial bc1 complex deficiency in tafazzin-knockdown mice

Frontiers in Physiology

Volumn 4 APR, Issue , 2013, Pages

  Powers, Corey ^a   Huang, Yan ^a   Strauss, Arnold ^a   Khuchua, Zaza ^a  

^a CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

Author keywords

Barth syndrome; Cardiolipins; Complex III; Exercise intolerance; Mouse models; Tafazzin

Indexed keywords

ACYLTRANSFERASE; CARDIOLIPIN; MITOCHONDRIAL ENZYME; TAFAZZIN; UBIQUINOL CYTOCHROME C REDUCTASE; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BARTH SYNDROME; BC1 GENE; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENERGY EXPENDITURE; ENZYME ACTIVITY; ENZYME DEFICIENCY; EXERCISE; FUNCTIONAL DISEASE; FUNCTIONAL STATUS; HEART MITOCHONDRION; HEART MUSCLE CELL; HEART MUSCLE OXYGEN CONSUMPTION; MALE; METABOLIC RATE; MITOCHONDRIAL GENE; MITOCHONDRIAL RESPIRATION; MOUSE; NONHUMAN; PATHOGENESIS; RESPIRATORY CHAIN; REST;

EID: 84883768213     PISSN: None     EISSN: 1664042X     Source Type: Journal    
DOI: 10.3389/fphys.2013.00074     Document Type: Article

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