Inhibition of angiogenesis by β-galactosylceramidase deficiency in globoid cell leukodystrophy

Brain

Volumn 136, Issue 9, 2013, Pages 2859-2875

  Belleri, Mirella ^a   Ronca, Roberto ^a   Coltrini, Daniela ^a   Nico, Beatrice ^b   Ribatti, Domenico ^b,c   Poliani, Pietro L ^a   Giacomini, Arianna ^a   Alessi, Patrizia ^a   Marchesini, Sergio ^a   Santos, Marta B ^d   Bongarzone, Ernesto R ^d   Presta, Marco ^a  

^a UNIVERSITY OF BRESCIA   (Italy)

^b UNIVERSITY OF BARI   (Italy)

^c NATIONAL CANCER INSTITUTE GIOVANNI PAOLO II   (Italy)

^d UNIVERSITY OF ILLINOIS AT CHICAGO   (United States)

Author keywords

angiogenesis; Krabbe disease; neurodegeneration; psychosine; twitcher mice

Indexed keywords

ANGIOGENESIS INHIBITOR; ANGIOPOIETIN 2; CD31 ANTIGEN; COMPLEMENTARY DNA; FIBROBLAST GROWTH FACTOR 2; GALACTOSYLCERAMIDASE; LENTIVIRUS VECTOR; PSYCHOSINE; SHORT HAIRPIN RNA; SMALL INTERFERING RNA; VASCULAR ENDOTHELIAL CADHERIN; VASCULOTROPIN A; VASCULOTROPIN RECEPTOR 2;

ACTIN FILAMENT; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ANTIANGIOGENIC ACTIVITY; ARTICLE; BLOOD VESSEL PERMEABILITY; BLOOD VESSEL REACTIVITY; BRAIN BIOPSY; CELL PROLIFERATION; CHICK EMBRYO; CHORIOALLANTOIS; CONTROLLED STUDY; DOWN REGULATION; EMBRYO; ENDOTHELIUM CELL; ENZYME ASSAY; GENE MUTATION; GENE SILENCING; GENETIC TRANSDUCTION; GLOBOID CELL LEUKODYSTROPHY; HETEROZYGOTE; HISTOPATHOLOGY; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; IN VITRO STUDY; MICROVASCULAR ENDOTHELIAL CELL; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; RNA INTERFERENCE; UMBILICAL VEIN ENDOTHELIAL CELL; VASCULAR RING; WILD TYPE;

EID: 84883333573     PISSN: 00068950     EISSN: 14602156     Source Type: Journal    
DOI: 10.1093/brain/awt215     Document Type: Article

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