Changes in vimentin, lamin A/C and mitofilin induce aberrant cell organization in fibroblasts from Fanconi anemia complementation group A (FA-A) patients

Biochimie

Volumn 95, Issue 10, 2013, Pages 1838-1847

  Capanni, Cristina ^b   Bruschi, Maurizio ^a   Columbaro, Marta ^e   Cuccarolo, Paola ^c   Ravera, Silvia ^d   Dufour, Carlo ^a   Candiano, Giovanni ^a   Petretto, Andrea ^a   Degan, Paolo ^c   Cappelli, Enrico ^a  

^a G GASLINI INSTITUTE   (Italy)

^b CNR   (Italy)

^c UNIVERSITY OF GENOA   (Italy)

^d UNIVERSITY OF GENOA   (Italy)

^e RIZZOLI ORTHOPAEDIC INSTITUTE   (Italy)

Author keywords

Cell structure; Fanconi anemia; Oxidative stress

Indexed keywords

FANCONI ANEMIA GROUP A PROTEIN; HYDROGEN PEROXIDE; LAMIN A; LAMIN C; MEMBRANE PROTEIN; MITOFILIN; UNCLASSIFIED DRUG; VIMENTIN;

ARTICLE; CELL NUCLEUS; CELL STRUCTURE; FANCONI ANEMIA; FANCONI ANEMIA GROUP A; HUMAN; HUMAN CELL; IMMUNOFLUORESCENCE; MICROSCOPY; MITOCHONDRION; OXIDATIVE STRESS; TWO DIMENSIONAL GEL ELECTROPHORESIS;

2D-PAGE; ACUTE MYELOID LEUKEMIA; AML; BM; BONE MARROW; CELL STRUCTURE; DOUBLE STRAND BREAKS; DSBS; ENDOPLASMIC RETICULUM; ER; FANCONI ANEMIA; GLUCOSE RESPONSE PROTEIN 94; GRP94; H(2)O(2); HSC; HUMAN STEM CELLS; HYDROGEN PEROXIDE; IFS; INTERMEDIATE FILAMENTS; LAMIN A; LMNA; N-ACETYL CYSTEINE; NAC; OXIDATIVE STRESS; REACTIVE OXYGEN SPECIES; ROS; TWO DIMENSIONAL POLYACRYLAMIDE GEL ELECTROPHORESIS; WB; WESTERN BLOT;

CELL NUCLEUS; CELLS, CULTURED; CYTOSKELETON; FANCONI ANEMIA; FANCONI ANEMIA COMPLEMENTATION GROUP A PROTEIN; FIBROBLASTS; GENE EXPRESSION; HUMANS; HYDROGEN PEROXIDE; LAMIN TYPE A; MICROSCOPY, ELECTRON; MITOCHONDRIA; MITOCHONDRIAL PROTEINS; MUSCLE PROTEINS; MUTATION; OXIDATION-REDUCTION; OXIDATIVE STRESS; VIMENTIN;

EID: 84883237514     PISSN: 03009084     EISSN: 61831638     Source Type: Journal    
DOI: 10.1016/j.biochi.2013.06.024     Document Type: Article

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