-
1
-
-
0035991525
-
The role of inflammation in the pathophysiology of CF lung disease
-
J.F. Chmiel, M. Berger and M.W. Konstan (2002) The role of inflammation in the pathophysiology of CF lung disease. Clin Rev Allergy Immunol. 23 5-27.
-
(2002)
Clin Rev Allergy Immunol.
, vol.23
, pp. 5-27
-
-
Chmiel, J.F.1
Berger, M.2
Konstan, M.W.3
-
2
-
-
33645130994
-
Cystic fibrosis since 1938
-
P.B. Davis (2006) Cystic fibrosis since 1938. Am J Respir Crit Care Med. 173 475-482.
-
(2006)
Am J Respir Crit Care Med.
, vol.173
, pp. 475-482
-
-
Davis, P.B.1
-
3
-
-
39449133330
-
Airway inflammation in cystic fibrosis
-
A. Elizur, C.L. Cannon and T.W. Ferkol (2008) Airway inflammation in cystic fibrosis. Chest 133 489-495.
-
(2008)
Chest
, vol.133
, pp. 489-495
-
-
Elizur, A.1
Cannon, C.L.2
Ferkol, T.W.3
-
4
-
-
33344468629
-
Cystic fibrosis pulmonary exacerbations
-
T. Ferkol, M. Rosenfeld and C.E. Milla (2006) Cystic fibrosis pulmonary exacerbations. J Pediatr. 148 259-264.
-
(2006)
J Pediatr.
, vol.148
, pp. 259-264
-
-
Ferkol, T.1
Rosenfeld, M.2
Milla, C.E.3
-
5
-
-
36248953255
-
Cystic fibrosis pulmonary guidelines: chronic medications for maintenance of lung health
-
P.A. Flume, B.P. O'Sullivan, K.A. Robinson, et al. (2007) Cystic fibrosis pulmonary guidelines: chronic medications for maintenance of lung health. Am J Respir Crit Care Med. 176 957-969.
-
(2007)
Am J Respir Crit Care Med.
, vol.176
, pp. 957-969
-
-
Flume, P.A.1
O'Sullivan, B.P.2
Robinson, K.A.3
-
6
-
-
0142043977
-
Pathophysiology and management of pulmonary infections in cystic fibrosis
-
R.L. Gibson, J.L. Burns and B.W. Ramsey (2003) Pathophysiology and management of pulmonary infections in cystic fibrosis. Am J Respir Crit Care Med. 168 918-951.
-
(2003)
Am J Respir Crit Care Med.
, vol.168
, pp. 918-951
-
-
Gibson, R.L.1
Burns, J.L.2
Ramsey, B.W.3
-
7
-
-
0036194724
-
Mucus clearance as a primary innate defense mechanism for mammalian airways
-
M.R. Knowles and R.C. Boucher (2002) Mucus clearance as a primary innate defense mechanism for mammalian airways. J Clin Invest. 109 571-577.
-
(2002)
J Clin Invest.
, vol.109
, pp. 571-577
-
-
Knowles, M.R.1
Boucher, R.C.2
-
11
-
-
0037213623
-
Role of airway surface liquid and submucosal glands in cystic fibrosis lung disease
-
A.S. Verkman, Y. Song and J.R. Thiagarajah (2003) Role of airway surface liquid and submucosal glands in cystic fibrosis lung disease. Am J Physiol Cell Physiol. 284 C2-C15.
-
(2003)
Am J Physiol Cell Physiol.
, vol.284
, pp. C2-C15
-
-
Verkman, A.S.1
Song, Y.2
Thiagarajah, J.R.3
-
12
-
-
0036194724
-
Mucus clearance as a primary innate defense mechanism for mammalian airways
-
M.R. Knowles and R.C. Boucher (2002) Mucus clearance as a primary innate defense mechanism for mammalian airways. J Clin Invest. 109 571-577.
-
(2002)
J Clin Invest.
, vol.109
, pp. 571-577
-
-
Knowles, M.R.1
Boucher, R.C.2
-
13
-
-
0032433707
-
Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease
-
H. Matsui, B.R. Grubb, R. Tarran, et al. (1998) Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease. Cell 95 1005-1015.
-
(1998)
Cell
, vol.95
, pp. 1005-1015
-
-
Matsui, H.1
Grubb, B.R.2
Tarran, R.3
-
14
-
-
0032910501
-
The genesis of cystic fibrosis lung disease
-
J.J. Wine (1999) The genesis of cystic fibrosis lung disease. J Clin Invest. 103 309-312.
-
(1999)
J Clin Invest.
, vol.103
, pp. 309-312
-
-
Wine, J.J.1
-
15
-
-
0029870085
-
Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid
-
J.J. Smith, S.M. Travis, E.P. Greenberg, et al. (1996) Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid. Cell 85 229-236.
-
(1996)
Cell
, vol.85
, pp. 229-236
-
-
Smith, J.J.1
Travis, S.M.2
Greenberg, E.P.3
-
16
-
-
0032081281
-
Activation of NF-kappaB by adherent Pseudomonas aeruginosa in normal and cystic fibrosis respiratory epithelial cells
-
E. DiMango, A.J. Ratner, R. Bryan, et al. (1998) Activation of NF-kappaB by adherent Pseudomonas aeruginosa in normal and cystic fibrosis respiratory epithelial cells. J Clin Invest. 101 2598-2605.
-
(1998)
J Clin Invest.
, vol.101
, pp. 2598-2605
-
-
DiMango, E.1
Ratner, A.J.2
Bryan, R.3
-
17
-
-
0030691027
-
Cystic fibrosis transmembrane conductance regulator is an epithelial cell receptor for clearance of Pseudomonas aeruginosa from the lung
-
G.B. Pier, M. Grout and T.S. Zaidi (1997) Cystic fibrosis transmembrane conductance regulator is an epithelial cell receptor for clearance of Pseudomonas aeruginosa from the lung. Proc Natl Acad Sci U S A 94 12088-12093.
-
(1997)
Proc Natl Acad Sci U S A
, vol.94
, pp. 12088-12093
-
-
Pier, G.B.1
Grout, M.2
Zaidi, T.S.3
-
18
-
-
0142043977
-
Pathophysiology and management of pulmonary infections in cystic fibrosis
-
R.L. Gibson, J.L. Burns and B.W. Ramsey (2003) Pathophysiology and management of pulmonary infections in cystic fibrosis. Am J Respir Crit Care Med. 168 918-951.
-
(2003)
Am J Respir Crit Care Med.
, vol.168
, pp. 918-951
-
-
Gibson, R.L.1
Burns, J.L.2
Ramsey, B.W.3
-
19
-
-
0028914085
-
Early pulmonary inflammation in infants with cystic fibrosis
-
T.Z. Khan, J.S. Wagener, T. Bost, et al. (1995) Early pulmonary inflammation in infants with cystic fibrosis. Am J Respir Crit Care Med. 151 1075-1082.
-
(1995)
Am J Respir Crit Care Med.
, vol.151
, pp. 1075-1082
-
-
Khan, T.Z.1
Wagener, J.S.2
Bost, T.3
-
20
-
-
0032770489
-
Quantitation of inflammatory responses to bacteria in young cystic fibrosis and control patients
-
M.S. Muhlebach, P.W. Stewart, M.W. Leigh, et al. (1999) Quantitation of inflammatory responses to bacteria in young cystic fibrosis and control patients. Am J Respir Crit Care Med. 160 186-191.
-
(1999)
Am J Respir Crit Care Med.
, vol.160
, pp. 186-191
-
-
Muhlebach, M.S.1
Stewart, P.W.2
Leigh, M.W.3
-
21
-
-
0029346937
-
The relationship between infection and inflammation in the early stages of lung disease from cystic fibrosis
-
K. Balough, M. McCubbin, M. Weinberger, et al. (1995) The relationship between infection and inflammation in the early stages of lung disease from cystic fibrosis. Pediatr Pulmonol. 20 63-70.
-
(1995)
Pediatr Pulmonol.
, vol.20
, pp. 63-70
-
-
Balough, K.1
McCubbin, M.2
Weinberger, M.3
-
22
-
-
0030768159
-
Lower airway inflammation in infants and young children with cystic fibrosis
-
D.S. Armstrong, K. Grimwood, J.B. Carlin, et al. (1997) Lower airway inflammation in infants and young children with cystic fibrosis. Am J Respir Crit Care Med. 156 1197-1204.
-
(1997)
Am J Respir Crit Care Med.
, vol.156
, pp. 1197-1204
-
-
Armstrong, D.S.1
Grimwood, K.2
Carlin, J.B.3
-
24
-
-
77953635880
-
Association between respiratory tract methicillin-resistant Staphylococcus aureus and survival in cystic fibrosis
-
E.C. Dasenbrook, W. Checkley, C.A. Merlo, et al. (2010) Association between respiratory tract methicillin-resistant Staphylococcus aureus and survival in cystic fibrosis. JAMA. 303 2386-2392.
-
(2010)
JAMA.
, vol.303
, pp. 2386-2392
-
-
Dasenbrook, E.C.1
Checkley, W.2
Merlo, C.A.3
-
25
-
-
0037007684
-
Bronchiectasis
-
A.F. Barker (2002) Bronchiectasis. N Engl J Med. 346 1383-1393.
-
(2002)
N Engl J Med.
, vol.346
, pp. 1383-1393
-
-
Barker, A.F.1
-
26
-
-
0034641962
-
Quorum-sensing signals indicate that cystic fibrosis lungs are infected with bacterial biofilms
-
P.K. Singh, A.L. Schaefer, M.R. Parsek, et al. (2000) Quorum-sensing signals indicate that cystic fibrosis lungs are infected with bacterial biofilms. Nature 407 762-764.
-
(2000)
Nature
, vol.407
, pp. 762-764
-
-
Singh, P.K.1
Schaefer, A.L.2
Parsek, M.R.3
-
27
-
-
0037129218
-
Pseudomonas biofilm formation and antibiotic resistance are linked to phenotypic variation
-
E. Drenkard and F.M. Ausubel (2002) Pseudomonas biofilm formation and antibiotic resistance are linked to phenotypic variation. Nature 416 740-743.
-
(2002)
Nature
, vol.416
, pp. 740-743
-
-
Drenkard, E.1
Ausubel, F.M.2
-
28
-
-
23644439540
-
Eradication of early Pseudomonas aeruginosa infection
-
N. Hoiby, B. Frederiksen and T. Pressler (2005) Eradication of early Pseudomonas aeruginosa infection. J Cyst Fibros. 4(suppl 2), 49-54.
-
(2005)
J Cyst Fibros.
, vol.4
, pp. 49-54
-
-
Hoiby, N.1
Frederiksen, B.2
Pressler, T.3
-
29
-
-
67349204479
-
Early anti-pseudomonal acquisition in young patients with cystic fibrosis: rationale and design of the EPIC clinical trial and observational study’
-
M.M. Treggiari, M. Rosenfeld, N. Mayer-Hamblett, et al. (2009) Early anti-pseudomonal acquisition in young patients with cystic fibrosis: rationale and design of the EPIC clinical trial and observational study’. Contemp Clin Trials 30 256-268.
-
(2009)
Contemp Clin Trials
, vol.30
, pp. 256-268
-
-
Treggiari, M.M.1
Rosenfeld, M.2
Mayer-Hamblett, N.3
-
30
-
-
0036683366
-
Detecting Stenotrophomonas maltophilia does not reduce survival of patients with cystic fibrosis
-
C.H. Goss, K. Otto, M.L. Aitken, et al. (2002) Detecting Stenotrophomonas maltophilia does not reduce survival of patients with cystic fibrosis. Am J Respir Crit Care Med. 166 356-361.
-
(2002)
Am J Respir Crit Care Med.
, vol.166
, pp. 356-361
-
-
Goss, C.H.1
Otto, K.2
Aitken, M.L.3
-
31
-
-
0021340634
-
Pseudomonas cepacia infection in cystic fibrosis: an emerging problem
-
A. Isles, I. Maclusky, M. Corey, et al. (1984) Pseudomonas cepacia infection in cystic fibrosis: an emerging problem. J Pediatr. 104 206-210.
-
(1984)
J Pediatr.
, vol.104
, pp. 206-210
-
-
Isles, A.1
Maclusky, I.2
Corey, M.3
-
32
-
-
0035503325
-
Infection with Burkholderia cepacia complex genomovars in patients with cystic fibrosis: virulent transmissible strains of genomovar III can replace Burkholderia multivorans
-
E. Mahenthiralingam, P. Vandamme, M.E. Campbell, et al. (2001) Infection with Burkholderia cepacia complex genomovars in patients with cystic fibrosis: virulent transmissible strains of genomovar III can replace Burkholderia multivorans. Clin Infect Dis. 33 1469-1475.
-
(2001)
Clin Infect Dis.
, vol.33
, pp. 1469-1475
-
-
Mahenthiralingam, E.1
Vandamme, P.2
Campbell, M.E.3
-
33
-
-
32444437595
-
Impact of Burkholderia dolosa on lung function and survival in cystic fibrosis
-
L.A. Kalish, D.A. Waltz, M. Dovey, et al. (2006) Impact of Burkholderia dolosa on lung function and survival in cystic fibrosis. Am J Respir Crit Care Med. 173 421-425.
-
(2006)
Am J Respir Crit Care Med.
, vol.173
, pp. 421-425
-
-
Kalish, L.A.1
Waltz, D.A.2
Dovey, M.3
-
34
-
-
0037445273
-
Nontuberculous mycobacteria. I: multicenter prevalence study in cystic fibrosis
-
K.N. Olivier, D.J. Weber, R.J. Wallace Jr, et al. (2003) Nontuberculous mycobacteria. I: multicenter prevalence study in cystic fibrosis. Am J Respir Crit Care Med. 167 828-834.
-
(2003)
Am J Respir Crit Care Med.
, vol.167
, pp. 828-834
-
-
Olivier, K.N.1
Weber, D.J.2
Wallace, R.J.3
-
35
-
-
0033064891
-
Effects of viral lower respiratory tract infection on lung function in infants with cystic fibrosis
-
P.W. Hiatt, S.C. Grace, C.A. Kozinetz, et al. (1999) Effects of viral lower respiratory tract infection on lung function in infants with cystic fibrosis. Pediatrics 103 619-626.
-
(1999)
Pediatrics
, vol.103
, pp. 619-626
-
-
Hiatt, P.W.1
Grace, S.C.2
Kozinetz, C.A.3
-
36
-
-
0031683179
-
Neutrophils induce damage to respiratory epithelial cells infected with respiratory syncytial virus
-
S.Z. Wang, H. Xu, A. Wraith, et al. (1998) Neutrophils induce damage to respiratory epithelial cells infected with respiratory syncytial virus. Eur Respir J. 12 612-618.
-
(1998)
Eur Respir J.
, vol.12
, pp. 612-618
-
-
Wang, S.Z.1
Xu, H.2
Wraith, A.3
-
37
-
-
33645454457
-
Innate immune responses of human tracheal epithelium to Pseudomonas aeruginosa flagellin, TNF-alpha, and IL-1beta
-
J. Tseng, J. Do, J.H. Widdicombe, et al. (2006) Innate immune responses of human tracheal epithelium to Pseudomonas aeruginosa flagellin, TNF-alpha, and IL-1beta. Am J Physiol Cell Physiol. 290 C678-C690.
-
(2006)
Am J Physiol Cell Physiol.
, vol.290
, pp. C678-C690
-
-
Tseng, J.1
Do, J.2
Widdicombe, J.H.3
-
38
-
-
27444444705
-
Normal and cystic fibrosis airway surface liquid homeostasis. The effects of phasic shear stress and viral infections
-
R. Tarran, B. Button, M. Picher, et al. (2005) Normal and cystic fibrosis airway surface liquid homeostasis. The effects of phasic shear stress and viral infections. J Biol Chem. 280 35751-35759.
-
(2005)
J Biol Chem.
, vol.280
, pp. 35751-35759
-
-
Tarran, R.1
Button, B.2
Picher, M.3
-
39
-
-
0028015883
-
Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation
-
M.W. Konstan, K.A. Hilliard, T.M. Norvell, et al. (1994) Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation. Am J Respir Crit Care Med. 150 448-454.
-
(1994)
Am J Respir Crit Care Med.
, vol.150
, pp. 448-454
-
-
Konstan, M.W.1
Hilliard, K.A.2
Norvell, T.M.3
-
40
-
-
0028240276
-
Protease-antiprotease imbalance in the lungs of children with cystic fibrosis
-
P. Birrer, N.G. McElvaney, A. Rudeberg, et al. (1994) Protease-antiprotease imbalance in the lungs of children with cystic fibrosis. Am J Respir Crit Care Med. 150 207-213.
-
(1994)
Am J Respir Crit Care Med.
, vol.150
, pp. 207-213
-
-
Birrer, P.1
McElvaney, N.G.2
Rudeberg, A.3
-
41
-
-
39449133330
-
Airway inflammation in cystic fibrosis
-
A. Elizur, C.L. Cannon and T.W. Ferkol (2008) Airway inflammation in cystic fibrosis. Chest 133 489-495.
-
(2008)
Chest
, vol.133
, pp. 489-495
-
-
Elizur, A.1
Cannon, C.L.2
Ferkol, T.W.3
-
43
-
-
0035991525
-
The role of inflammation in the pathophysiology of CF lung disease
-
J.F. Chmiel, M. Berger and M.W. Konstan (2002) The role of inflammation in the pathophysiology of CF lung disease. Clin Rev Allergy Immunol. 23 5-27.
-
(2002)
Clin Rev Allergy Immunol.
, vol.23
, pp. 5-27
-
-
Chmiel, J.F.1
Berger, M.2
Konstan, M.W.3
-
44
-
-
0022979529
-
Complement activation in cystic fibrosis respiratory fluids: in vivo and in vitro generation of C5a and chemotactic activity
-
R.B. Fick Jr, R.A. Robbins, S.U. Squier, et al. (1986) Complement activation in cystic fibrosis respiratory fluids: in vivo and in vitro generation of C5a and chemotactic activity. Pediatr Res. 20 1258-1268.
-
(1986)
Pediatr Res.
, vol.20
, pp. 1258-1268
-
-
Fick, R.B.1
Robbins, R.A.2
Squier, S.U.3
-
45
-
-
21244455537
-
Role of IL-17A, IL-17F, and the IL-17 receptor in regulating growth-related oncogene-alpha and granulocyte colony-stimulating factor in bronchial epithelium: implications for airway inflammation in cystic fibrosis
-
F. McAllister, A. Henry, J.L. Kreindler, et al. (2005) Role of IL-17A, IL-17F, and the IL-17 receptor in regulating growth-related oncogene-alpha and granulocyte colony-stimulating factor in bronchial epithelium: implications for airway inflammation in cystic fibrosis. J Immunol. 175 404-412.
-
(2005)
J Immunol.
, vol.175
, pp. 404-412
-
-
McAllister, F.1
Henry, A.2
Kreindler, J.L.3
-
46
-
-
0033831270
-
Exaggerated activation of nuclear factor-kappaB and altered IkappaB-beta processing in cystic fibrosis bronchial epithelial cells
-
A. Venkatakrishnan, A.A. Stecenko, G. King, et al. (2000) Exaggerated activation of nuclear factor-kappaB and altered IkappaB-beta processing in cystic fibrosis bronchial epithelial cells. Am J Respir Cell Mol Biol. 23 396-403.
-
(2000)
Am J Respir Cell Mol Biol.
, vol.23
, pp. 396-403
-
-
Venkatakrishnan, A.1
Stecenko, A.A.2
King, G.3
-
47
-
-
0034805902
-
Dysregulated NF-kappaB activation in cystic fibrosis: evidence for a primary inflammatory disorder
-
T.S. Blackwell, A.A. Stecenko and J.W. Christman (2001) Dysregulated NF-kappaB activation in cystic fibrosis: evidence for a primary inflammatory disorder. Am J Physiol Lung Cell Mol Physiol. 281 L69-L70.
-
(2001)
Am J Physiol Lung Cell Mol Physiol.
, vol.281
, pp. L69-L70
-
-
Blackwell, T.S.1
Stecenko, A.A.2
Christman, J.W.3
-
48
-
-
0035191223
-
Relationship between IkappaBalpha deficiency, NFkappaB activity and interleukin-8 production in CF human airway epithelial cells
-
O. Tabary, S. Escotte, J.P. Couetil, et al. (2001) Relationship between IkappaBalpha deficiency, NFkappaB activity and interleukin-8 production in CF human airway epithelial cells. Pflugers Arch. 443(suppl), S40-S44.
-
(2001)
Pflugers Arch.
, vol.443
, pp. S40-S44
-
-
Tabary, O.1
Escotte, S.2
Couetil, J.P.3
-
49
-
-
4143105723
-
Isoprenoid-mediated control of SMAD3 expression in a cultured model of cystic fibrosis epithelial cells
-
J.Y. Lee, H.L. Elmer, K.R. Ross, et al. (2004) Isoprenoid-mediated control of SMAD3 expression in a cultured model of cystic fibrosis epithelial cells. Am J Respir Cell Mol Biol. 31 234-240.
-
(2004)
Am J Respir Cell Mol Biol.
, vol.31
, pp. 234-240
-
-
Lee, J.Y.1
Elmer, H.L.2
Ross, K.R.3
-
50
-
-
0034997191
-
Proinflammatory cytokine responses to P. aeruginosa infection in human airway epithelial cell lines
-
D. Kube, U. Sontich, D. Fletcher, et al. (2001) Proinflammatory cytokine responses to P. aeruginosa infection in human airway epithelial cell lines. Am J Physiol Lung Cell Mol Physiol. 280 L493-L502.
-
(2001)
Am J Physiol Lung Cell Mol Physiol.
, vol.280
, pp. L493-L502
-
-
Kube, D.1
Sontich, U.2
Fletcher, D.3
-
51
-
-
0032817772
-
Altered respiratory epithelial cell cytokine production in cystic fibrosis
-
T.L. Bonfield, M.W. Konstan and M. Berger (1999) Altered respiratory epithelial cell cytokine production in cystic fibrosis. J Allergy Clin Immunol. 104 72-78.
-
(1999)
J Allergy Clin Immunol.
, vol.104
, pp. 72-78
-
-
Bonfield, T.L.1
Konstan, M.W.2
Berger, M.3
-
52
-
-
0036840478
-
Inflammatory response in airway epithelial cells isolated from patients with cystic fibrosis
-
N. Aldallal, E.E. McNaughton, L.J. Manzel, et al. (2002) Inflammatory response in airway epithelial cells isolated from patients with cystic fibrosis. Am J Respir Crit Care Med. 166 1248-1256.
-
(2002)
Am J Respir Crit Care Med.
, vol.166
, pp. 1248-1256
-
-
Aldallal, N.1
McNaughton, E.E.2
Manzel, L.J.3
-
54
-
-
84882926882
-
The effect of polarized release of CXC-chemokines from wild-type and cystic fibrosis murine airway epithelial cells
-
e-pub Jul 16
-
M.M. Farberman, A. Ibricevic, T.D. Joseph, et al. (2010) The effect of polarized release of CXC-chemokines from wild-type and cystic fibrosis murine airway epithelial cells. Am J Respir Cell Mol Biol e-pub Jul 16
-
(2010)
Am J Respir Cell Mol Biol
-
-
Farberman, M.M.1
Ibricevic, A.2
Joseph, T.D.3
-
55
-
-
0031836105
-
Mice lacking neutrophil elastase reveal impaired host defense against gram negative bacterial sepsis
-
A. Belaaouaj, R. McCarthy, M. Baumann, et al. (1998) Mice lacking neutrophil elastase reveal impaired host defense against gram negative bacterial sepsis. Nat Med. 4 615-618.
-
(1998)
Nat Med.
, vol.4
, pp. 615-618
-
-
Belaaouaj, A.1
McCarthy, R.2
Baumann, M.3
-
56
-
-
0027131471
-
Alpha 1-Proteinase inhibitor, elastase activity, and lung disease severity in cystic fibrosis
-
C.M. O'Connor, K. Gaffney, J. Keane, et al. (1993) Alpha 1-Proteinase inhibitor, elastase activity, and lung disease severity in cystic fibrosis. Am Rev Respir Dis. 148 1665-1670.
-
(1993)
Am Rev Respir Dis.
, vol.148
, pp. 1665-1670
-
-
O'Connor, C.M.1
Gaffney, K.2
Keane, J.3
-
57
-
-
0026681802
-
Neutrophil elastase in respiratory epithelial lining fluid of individuals with cystic fibrosis induces interleukin-8 gene expression in a human bronchial epithelial cell line
-
H. Nakamura, K. Yoshimura, N.G. McElvaney, et al. (1992) Neutrophil elastase in respiratory epithelial lining fluid of individuals with cystic fibrosis induces interleukin-8 gene expression in a human bronchial epithelial cell line. J Clin Invest. 89 1478-1484.
-
(1992)
J Clin Invest.
, vol.89
, pp. 1478-1484
-
-
Nakamura, H.1
Yoshimura, K.2
McElvaney, N.G.3
-
58
-
-
0025374923
-
Neutrophil elastase cleaves C3bi on opsonized pseudomonas as well as CR1 on neutrophils to create a functionally important opsonin receptor mismatch
-
M.F. Tosi, H. Zakem and M. Berger (1990) Neutrophil elastase cleaves C3bi on opsonized pseudomonas as well as CR1 on neutrophils to create a functionally important opsonin receptor mismatch. J Clin Invest. 86 300-308.
-
(1990)
J Clin Invest.
, vol.86
, pp. 300-308
-
-
Tosi, M.F.1
Zakem, H.2
Berger, M.3
-
59
-
-
0021239746
-
Proteins of the cystic fibrosis respiratory tract. Fragmented immunoglobulin G opsonic antibody causing defective opsonophagocytosis
-
R.B. Fick Jr, G.P. Naegel, S.U. Squier, et al. (1984) Proteins of the cystic fibrosis respiratory tract. Fragmented immunoglobulin G opsonic antibody causing defective opsonophagocytosis. J Clin Invest. 74 236-248.
-
(1984)
J Clin Invest.
, vol.74
, pp. 236-248
-
-
Fick, R.B.1
Naegel, G.P.2
Squier, S.U.3
-
60
-
-
85054761802
-
Aspiration, bronchial obstruction, bronchiectasis, and related disorders
-
New York City, NY: Springer Science
-
T. Tomashefski and D. Dail (2008) Aspiration, bronchial obstruction, bronchiectasis, and related disorders. Nonneoplastic Lung Disease. Vol 1 New York City, NY: Springer Science
-
(2008)
Nonneoplastic Lung Disease.
, vol.1
-
-
Tomashefski, T.1
Dail, D.2
-
62
-
-
33344468629
-
Cystic fibrosis pulmonary exacerbations
-
T. Ferkol, M. Rosenfeld and C.E. Milla (2006) Cystic fibrosis pulmonary exacerbations. J Pediatr. 148 259-264.
-
(2006)
J Pediatr.
, vol.148
, pp. 259-264
-
-
Ferkol, T.1
Rosenfeld, M.2
Milla, C.E.3
-
63
-
-
0023476010
-
What is a “pulmonary exacerbation” in cystic fibrosis?
-
R.E. Wood and M.W. Leigh (1987) What is a “pulmonary exacerbation” in cystic fibrosis? J Pediatr. 111 841-842.
-
(1987)
J Pediatr.
, vol.111
, pp. 841-842
-
-
Wood, R.E.1
Leigh, M.W.2
-
65
-
-
0036157691
-
Nasal polyps in cystic fibrosis: Clinical endoscopic study with nasal lavage fluid analysis
-
G. Henriksson, K.M. Westrin, F. Karpati, et al. (2002) Nasal polyps in cystic fibrosis: Clinical endoscopic study with nasal lavage fluid analysis. Chest 121 40-47.
-
(2002)
Chest
, vol.121
, pp. 40-47
-
-
Henriksson, G.1
Westrin, K.M.2
Karpati, F.3
-
66
-
-
18744399263
-
Sequential genotyping of Pseudomonas aeruginosa from upper and lower airways of cystic fibrosis patients
-
A. Jung, I. Kleinau, G. Schonian, et al. (2002) Sequential genotyping of Pseudomonas aeruginosa from upper and lower airways of cystic fibrosis patients. Eur Respir J. 20 1457-1463.
-
(2002)
Eur Respir J.
, vol.20
, pp. 1457-1463
-
-
Jung, A.1
Kleinau, I.2
Schonian, G.3
-
67
-
-
0020385130
-
Treatment and prognosis of nasal polyps in cystic fibrosis
-
R.C. Stern, T.F. Boat, R.E. Wood, et al. (1982) Treatment and prognosis of nasal polyps in cystic fibrosis. Am J Dis Child. 136 1067-1070.
-
(1982)
Am J Dis Child.
, vol.136
, pp. 1067-1070
-
-
Stern, R.C.1
Boat, T.F.2
Wood, R.E.3
-
68
-
-
85047686252
-
Cystic fibrosis pulmonary guidelines: pulmonary complications: hemoptysis and pneumothorax
-
e-pub Mar 18
-
P.A. Flume, P.J. Mogayzel Jr, K.A. Robinson, et al. (2010) Cystic fibrosis pulmonary guidelines: pulmonary complications: hemoptysis and pneumothorax. Am J Respir Crit Care Med. e-pub Mar 18
-
(2010)
Am J Respir Crit Care Med.
-
-
Flume, P.A.1
Mogayzel, P.J.2
Robinson, K.A.3
-
69
-
-
0027564769
-
Cystic Fibrosis Foundation consensus conference report on pulmonary complications of cystic fibrosis
-
D.V. Schidlow, L.M. Taussig and M.R. Knowles (1993) Cystic Fibrosis Foundation consensus conference report on pulmonary complications of cystic fibrosis. Pediatr Pulmonol. 15 187-198.
-
(1993)
Pediatr Pulmonol.
, vol.15
, pp. 187-198
-
-
Schidlow, D.V.1
Taussig, L.M.2
Knowles, M.R.3
-
70
-
-
0031808223
-
Bronchial artery embolization for the treatment of hemoptysis in patients with cystic fibrosis
-
G.M. Brinson, P.G. Noone, M.A. Mauro, et al. (1998) Bronchial artery embolization for the treatment of hemoptysis in patients with cystic fibrosis. Am J Respir Crit Care Med. 157 1951-1958.
-
(1998)
Am J Respir Crit Care Med.
, vol.157
, pp. 1951-1958
-
-
Brinson, G.M.1
Noone, P.G.2
Mauro, M.A.3
-
71
-
-
0023819109
-
Bronchodilator responsiveness in infants and young children with cystic fibrosis
-
P. Hiatt, H. Eigen, P. Yu, et al. (1988) Bronchodilator responsiveness in infants and young children with cystic fibrosis. Am Rev Respir Dis. 137 119-122.
-
(1988)
Am Rev Respir Dis.
, vol.137
, pp. 119-122
-
-
Hiatt, P.1
Eigen, H.2
Yu, P.3
-
72
-
-
0034103455
-
Bronchodilators in cystic fibrosis
-
P.L. Brand (2000) Bronchodilators in cystic fibrosis. J R Soc Med. 93(suppl), 37-39.
-
(2000)
J R Soc Med.
, vol.93
, pp. 37-39
-
-
Brand, P.L.1
-
73
-
-
0018093989
-
Cystic fibrosis, atopy, and airways lability
-
M. Silverman, F.D. Hobbs, I.R. Gordon, et al. (1978) Cystic fibrosis, atopy, and airways lability. Arch Dis Child 53 873-877.
-
(1978)
Arch Dis Child
, vol.53
, pp. 873-877
-
-
Silverman, M.1
Hobbs, F.D.2
Gordon, I.R.3
-
74
-
-
0017883026
-
Bronchial reactivity in cystic fibrosis
-
C.M. Mellis and H. Levison (1978) Bronchial reactivity in cystic fibrosis. Pediatrics 61 446-450.
-
(1978)
Pediatrics
, vol.61
, pp. 446-450
-
-
Mellis, C.M.1
Levison, H.2
-
75
-
-
0141956255
-
Allergic bronchopulmonary aspergillosis in cystic fibrosis–state of the art: Cystic Fibrosis Foundation Consensus Conference
-
D.A. Stevens, R.B. Moss, V.P. Kurup, et al. (2003) Allergic bronchopulmonary aspergillosis in cystic fibrosis–state of the art: Cystic Fibrosis Foundation Consensus Conference. Clin Infect Dis. 37(suppl), S225-S264.
-
(2003)
Clin Infect Dis.
, vol.37
, pp. S225-S264
-
-
Stevens, D.A.1
Moss, R.B.2
Kurup, V.P.3
-
76
-
-
29544437697
-
Voriconazole therapy in children with cystic fibrosis
-
T. Hilliard, S. Edwards, R. Buchdahl, et al. (2005) Voriconazole therapy in children with cystic fibrosis. J Cyst Fibros. 4 215-220.
-
(2005)
J Cyst Fibros.
, vol.4
, pp. 215-220
-
-
Hilliard, T.1
Edwards, S.2
Buchdahl, R.3
-
77
-
-
0036311232
-
Relationship between nutritional status and lung function in cystic fibrosis: cross sectional and longitudinal analyses from the German CF quality assurance (CFQA) project
-
G. Steinkamp and B. Wiedemann (2002) Relationship between nutritional status and lung function in cystic fibrosis: cross sectional and longitudinal analyses from the German CF quality assurance (CFQA) project. Thorax 57 596-601.
-
(2002)
Thorax
, vol.57
, pp. 596-601
-
-
Steinkamp, G.1
Wiedemann, B.2
-
78
-
-
0033825741
-
Trends in pulmonary function in patients with cystic fibrosis correlate with the degree of glucose intolerance at baseline
-
C.E. Milla, W.J. Warwick and A. Moran (2000) Trends in pulmonary function in patients with cystic fibrosis correlate with the degree of glucose intolerance at baseline. Am J Respir Crit Care Med. 162 891-895.
-
(2000)
Am J Respir Crit Care Med.
, vol.162
, pp. 891-895
-
-
Milla, C.E.1
Warwick, W.J.2
Moran, A.3
-
79
-
-
0036320272
-
Pseudomonas aeruginosa and other predictors of mortality and morbidity in young children with cystic fibrosis
-
J. Emerson, M. Rosenfeld, S. McNamara, et al. (2002) Pseudomonas aeruginosa and other predictors of mortality and morbidity in young children with cystic fibrosis. Pediatr Pulmonol. 34 91-100.
-
(2002)
Pediatr Pulmonol.
, vol.34
, pp. 91-100
-
-
Emerson, J.1
Rosenfeld, M.2
McNamara, S.3
-
80
-
-
0035002870
-
Clinical outcome after early Pseudomonas aeruginosa infection in cystic fibrosis
-
G.M. Nixon, D.S. Armstrong, R. Carzino, et al. (2001) Clinical outcome after early Pseudomonas aeruginosa infection in cystic fibrosis. J Pediatr. 138 699-704.
-
(2001)
J Pediatr.
, vol.138
, pp. 699-704
-
-
Nixon, G.M.1
Armstrong, D.S.2
Carzino, R.3
-
81
-
-
0021871444
-
Pseudomonas cepacia colonization among patients with cystic fibrosis. A new opportunist
-
M.J. Thomassen, C.A. Demko, J.D. Klinger, et al. (1985) Pseudomonas cepacia colonization among patients with cystic fibrosis. A new opportunist. Am Rev Respir Dis. 131 791-796.
-
(1985)
Am Rev Respir Dis.
, vol.131
, pp. 791-796
-
-
Thomassen, M.J.1
Demko, C.A.2
Klinger, J.D.3
-
82
-
-
0029016495
-
Gender differences in cystic fibrosis: Pseudomonas aeruginosa infection
-
C.A. Demko, P.J. Byard and P.B. Davis (1995) Gender differences in cystic fibrosis: Pseudomonas aeruginosa infection. J Clin Epidemiol. 48 1041-1049.
-
(1995)
J Clin Epidemiol.
, vol.48
, pp. 1041-1049
-
-
Demko, C.A.1
Byard, P.J.2
Davis, P.B.3
-
83
-
-
0033866283
-
Time to think again: cystic fibrosis is not an “all or none” disease
-
A. Bush and C. Wallis (2000) Time to think again: cystic fibrosis is not an “all or none” disease. Pediatr Pulmonol. 30 139-144.
-
(2000)
Pediatr Pulmonol.
, vol.30
, pp. 139-144
-
-
Bush, A.1
Wallis, C.2
-
84
-
-
77949502126
-
Impact of socioeconomic status, race, and ethnicity on quality of life in patients with cystic fibrosis in the United States
-
A.L. Quittner, M.S. Schechter, L. Rasouliyan, et al. (2010) Impact of socioeconomic status, race, and ethnicity on quality of life in patients with cystic fibrosis in the United States. Chest 137 642-650.
-
(2010)
Chest
, vol.137
, pp. 642-650
-
-
Quittner, A.L.1
Schechter, M.S.2
Rasouliyan, L.3
-
85
-
-
0347812925
-
Non-genetic influences on cystic fibrosis lung disease: the role of sociodemographic characteristics, environmental exposures, and healthcare interventions
-
M.S. Schechter (2003) Non-genetic influences on cystic fibrosis lung disease: the role of sociodemographic characteristics, environmental exposures, and healthcare interventions. Semin Respir Crit Care Med. 24 639-652.
-
(2003)
Semin Respir Crit Care Med.
, vol.24
, pp. 639-652
-
-
Schechter, M.S.1
-
86
-
-
0037795302
-
Growth and nutritional indexes in early life predict pulmonary function in cystic fibrosis
-
M.W. Konstan, S.M. Butler, M.E. Wohl, et al. (2003) Growth and nutritional indexes in early life predict pulmonary function in cystic fibrosis. J Pediatr. 142 624-630.
-
(2003)
J Pediatr.
, vol.142
, pp. 624-630
-
-
Konstan, M.W.1
Butler, S.M.2
Wohl, M.E.3
-
87
-
-
0031810780
-
Cystic fibrosis: when should high-resolution computed tomography of the chest be obtained?
-
A.S. Brody (1998) Cystic fibrosis: when should high-resolution computed tomography of the chest be obtained? Pediatrics 101 1071.
-
(1998)
Pediatrics
, vol.101
, pp. 1071
-
-
Brody, A.S.1
-
88
-
-
30444446184
-
Computed tomography in the evaluation of cystic fibrosis lung disease
-
A.S. Brody, H.A. Tiddens, R.G. Castile, et al. (2005) Computed tomography in the evaluation of cystic fibrosis lung disease. Am J Respir Crit Care Med. 172 1246-1252.
-
(2005)
Am J Respir Crit Care Med.
, vol.172
, pp. 1246-1252
-
-
Brody, A.S.1
Tiddens, H.A.2
Castile, R.G.3
-
89
-
-
34247589696
-
Computed tomography reflects lower airway inflammation and tracks changes in early cystic fibrosis
-
S.D. Davis, L.A. Fordham, A.S. Brody, et al. (2007) Computed tomography reflects lower airway inflammation and tracks changes in early cystic fibrosis. Am J Respir Crit Care Med. 175 943-950.
-
(2007)
Am J Respir Crit Care Med.
, vol.175
, pp. 943-950
-
-
Davis, S.D.1
Fordham, L.A.2
Brody, A.S.3
-
90
-
-
43649084697
-
Estimation of the radiation dose from CT in cystic fibrosis
-
P.A. de Jong, H.A. Tiddens, M.H. Lequin, et al. (2008) Estimation of the radiation dose from CT in cystic fibrosis. Chest 133 1289-1291.
-
(2008)
Chest
, vol.133
, pp. 1289-1291
-
-
de Jong, P.A.1
Tiddens, H.A.2
Lequin, M.H.3
-
91
-
-
0026520359
-
Prediction of mortality in patients with cystic fibrosis
-
E. Kerem, J. Reisman, M. Corey, et al. (1992) Prediction of mortality in patients with cystic fibrosis. N Engl J Med. 326 1187-1191.
-
(1992)
N Engl J Med.
, vol.326
, pp. 1187-1191
-
-
Kerem, E.1
Reisman, J.2
Corey, M.3
-
92
-
-
0031471090
-
Longitudinal analysis of pulmonary function decline in patients with cystic fibrosis
-
M. Corey, L. Edwards, H. Levison, et al. (1997) Longitudinal analysis of pulmonary function decline in patients with cystic fibrosis. J Pediatr. 131 809-814.
-
(1997)
J Pediatr.
, vol.131
, pp. 809-814
-
-
Corey, M.1
Edwards, L.2
Levison, H.3
-
93
-
-
0031021662
-
Identifying treatments that halt progression of pulmonary disease in cystic fibrosis
-
P.B. Davis, P.J. Byard and M.W. Konstan (1997) Identifying treatments that halt progression of pulmonary disease in cystic fibrosis. Pediatr Res. 41 161-165.
-
(1997)
Pediatr Res.
, vol.41
, pp. 161-165
-
-
Davis, P.B.1
Byard, P.J.2
Konstan, M.W.3
-
94
-
-
0032718969
-
Diagnostic accuracy of oropharyngeal cultures in infants and young children with cystic fibrosis
-
M. Rosenfeld, J. Emerson, F. Accurso, et al. (1999) Diagnostic accuracy of oropharyngeal cultures in infants and young children with cystic fibrosis. Pediatr Pulmonol. 28 321-328.
-
(1999)
Pediatr Pulmonol.
, vol.28
, pp. 321-328
-
-
Rosenfeld, M.1
Emerson, J.2
Accurso, F.3
-
95
-
-
0036907325
-
Induced sputum inflammatory measures correlate with lung function in children with cystic fibrosis
-
S.D. Sagel, M.K. Sontag, J.S. Wagener, et al. (2002) Induced sputum inflammatory measures correlate with lung function in children with cystic fibrosis. J Pediatr. 141 811-817.
-
(2002)
J Pediatr.
, vol.141
, pp. 811-817
-
-
Sagel, S.D.1
Sontag, M.K.2
Wagener, J.S.3
-
97
-
-
33645130994
-
Cystic fibrosis since 1938
-
P.B. Davis (2006) Cystic fibrosis since 1938. Am J Respir Crit Care Med. 173 475-482.
-
(2006)
Am J Respir Crit Care Med.
, vol.173
, pp. 475-482
-
-
Davis, P.B.1
-
98
-
-
63249110872
-
Update in cystic fibrosis 2008
-
F. Ratjen (2009) Update in cystic fibrosis 2008. Am J Respir Crit Care Med. 179 445-448.
-
(2009)
Am J Respir Crit Care Med.
, vol.179
, pp. 445-448
-
-
Ratjen, F.1
-
99
-
-
66849099545
-
Airway-clearance therapy guidelines and implementation
-
M.K. Lester and P.A. Flume (2009) Airway-clearance therapy guidelines and implementation. Respir Care 54 733-750.
-
(2009)
Respir Care
, vol.54
, pp. 733-750
-
-
Lester, M.K.1
Flume, P.A.2
-
100
-
-
73349092769
-
Airway clearance therapy in cystic fibrosis patients
-
G. Pisi and A. Chetta (2009) Airway clearance therapy in cystic fibrosis patients. Acta Biomed. 80 102-106.
-
(2009)
Acta Biomed.
, vol.80
, pp. 102-106
-
-
Pisi, G.1
Chetta, A.2
-
101
-
-
66849124547
-
Cystic fibrosis pulmonary guidelines: airway clearance therapies
-
P. Flume, K. Robinson, B. O'Sullivan, et al. (2009) Cystic fibrosis pulmonary guidelines: airway clearance therapies. Respir Care 54 522-537.
-
(2009)
Respir Care
, vol.54
, pp. 522-537
-
-
Flume, P.1
Robinson, K.2
O'Sullivan, B.3
-
102
-
-
44149097787
-
Recent advances in cystic fibrosis
-
F. Ratjen (2008) Recent advances in cystic fibrosis. Paediatr Respir Rev. 9 144-148.
-
(2008)
Paediatr Respir Rev.
, vol.9
, pp. 144-148
-
-
Ratjen, F.1
-
103
-
-
70349096824
-
Emerging treatments in cystic fibrosis
-
A.M. Jones and J.M. Helm (2009) Emerging treatments in cystic fibrosis. Drugs 69 1903-1910.
-
(2009)
Drugs
, vol.69
, pp. 1903-1910
-
-
Jones, A.M.1
Helm, J.M.2
-
104
-
-
77953361961
-
Beyond postural drainage and percussion: Airway clearance in people with cystic fibrosis
-
J.A. Pryor, E. Tannenbaum, S.F. Scott, et al. (2010) Beyond postural drainage and percussion: Airway clearance in people with cystic fibrosis. J Cyst Fibros. 9 187-192.
-
(2010)
J Cyst Fibros.
, vol.9
, pp. 187-192
-
-
Pryor, J.A.1
Tannenbaum, E.2
Scott, S.F.3
-
105
-
-
2542444725
-
Physiotherapy in infants and young children with cystic fibrosis: current practice and future developments
-
L. Lannefors, B.M. Button and M. McIlwaine (2004) Physiotherapy in infants and young children with cystic fibrosis: current practice and future developments. J R Soc Med. 97(suppl 44), 8-25.
-
(2004)
J R Soc Med.
, vol.97
, pp. 8-25
-
-
Lannefors, L.1
Button, B.M.2
McIlwaine, M.3
-
106
-
-
34047136511
-
Chest physical therapy, breathing techniques and exercise in children with CF
-
M. McIlwaine (2007) Chest physical therapy, breathing techniques and exercise in children with CF. Paediatr Respir Rev. 8 8-16.
-
(2007)
Paediatr Respir Rev.
, vol.8
, pp. 8-16
-
-
McIlwaine, M.1
-
107
-
-
34047113309
-
Airway clearance devices in cystic fibrosis
-
J.H. Marks (2007) Airway clearance devices in cystic fibrosis. Paediatr Respir Rev. 8 17-23.
-
(2007)
Paediatr Respir Rev.
, vol.8
, pp. 17-23
-
-
Marks, J.H.1
-
108
-
-
33144467144
-
Nonpharmacologic airway clearance therapies
-
F.D. McCool and M.J. Rosen (2006) Nonpharmacologic airway clearance therapies. Chest 129(suppl), 250S-259S.
-
(2006)
Chest
, vol.129
, pp. 250S-259S
-
-
McCool, F.D.1
Rosen, M.J.2
-
109
-
-
84965187625
-
Chest physiotherapy compared to no chest physiotherapy for cystic fibrosis
-
CD001401
-
C. van der Schans, A. Prasad and E. Main (2000) Chest physiotherapy compared to no chest physiotherapy for cystic fibrosis. Cochrane Database Syst Rev. 2 CD001401
-
(2000)
Cochrane Database Syst Rev.
, vol.2
-
-
van der Schans, C.1
Prasad, A.2
Main, E.3
-
110
-
-
73349096288
-
Exercise programs for children with cystic fibrosis: A systematic review of randomized controlled trials
-
N. van Doorn (2010) Exercise programs for children with cystic fibrosis: A systematic review of randomized controlled trials. Disabil Rehabil. 32 41-49.
-
(2010)
Disabil Rehabil.
, vol.32
, pp. 41-49
-
-
van Doorn, N.1
-
111
-
-
77953328174
-
Emerging therapies in cystic fibrosis
-
P. Anderson (2010) Emerging therapies in cystic fibrosis. Ther Adv Respir Dis. 4 177-185.
-
(2010)
Ther Adv Respir Dis.
, vol.4
, pp. 177-185
-
-
Anderson, P.1
-
112
-
-
73449113631
-
Measuring and improving respiratory outcomes in cystic fibrosis lung disease: Opportunities and challenges to therapy
-
E.T. Zemanick, J.K. Harris, S. Conway, et al. (2009) Measuring and improving respiratory outcomes in cystic fibrosis lung disease: Opportunities and challenges to therapy. J Cyst Fibros. 9 1-16.
-
(2009)
J Cyst Fibros.
, vol.9
, pp. 1-16
-
-
Zemanick, E.T.1
Harris, J.K.2
Conway, S.3
-
113
-
-
44649166466
-
Inhaled mannitol improves lung function in cystic fibrosis
-
A. Jaques, E. Daviskas, J.A. Turton, et al. (2008) Inhaled mannitol improves lung function in cystic fibrosis. Chest 133 1388-1396.
-
(2008)
Chest
, vol.133
, pp. 1388-1396
-
-
Jaques, A.1
Daviskas, E.2
Turton, J.A.3
-
114
-
-
30944466084
-
A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis
-
M.R. Elkins, M. Robinson, B.R. Rose, et al. (2006) A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis. N Engl J Med. 354 229-240.
-
(2006)
N Engl J Med.
, vol.354
, pp. 229-240
-
-
Elkins, M.R.1
Robinson, M.2
Rose, B.R.3
-
115
-
-
57349158832
-
Safety and tolerability of inhaled hypertonic saline in young children with cystic fibrosis
-
E.P. Dellon, S.H. Donaldson, R. Johnson, et al. (2008) Safety and tolerability of inhaled hypertonic saline in young children with cystic fibrosis. Pediatr Pulmonol. 43 1100-1106.
-
(2008)
Pediatr Pulmonol.
, vol.43
, pp. 1100-1106
-
-
Dellon, E.P.1
Donaldson, S.H.2
Johnson, R.3
-
117
-
-
66849097677
-
Mucus, phlegm and sputum in cystic fibrosis
-
B.K. Rubin (2009) Mucus, phlegm and sputum in cystic fibrosis. Respir Care 54 726-732.
-
(2009)
Respir Care
, vol.54
, pp. 726-732
-
-
Rubin, B.K.1
-
119
-
-
0032987387
-
Systematic review of N-acetylcysteine in cystic fibrosis
-
Y. Duijvestijn and P. Brand (1999) Systematic review of N-acetylcysteine in cystic fibrosis. Acta Pædiatr. 88 38-41.
-
(1999)
Acta Pædiatr.
, vol.88
, pp. 38-41
-
-
Duijvestijn, Y.1
Brand, P.2
-
120
-
-
0027477437
-
Antibiotic therapy for chronic infection of pseudomonas in the lung
-
N. Hoiby (1993) Antibiotic therapy for chronic infection of pseudomonas in the lung. Annu Rev Med. 44 1-10.
-
(1993)
Annu Rev Med.
, vol.44
, pp. 1-10
-
-
Hoiby, N.1
-
121
-
-
0037445216
-
Significant microbiological effect of inhaled tobramycin in young children with cystic fibrosis
-
R.L. Gibson, J. Emerson, S. McNamara, et al. (2003) Significant microbiological effect of inhaled tobramycin in young children with cystic fibrosis. Am J Respir Crit Care Med. 167 841-849.
-
(2003)
Am J Respir Crit Care Med.
, vol.167
, pp. 841-849
-
-
Gibson, R.L.1
Emerson, J.2
McNamara, S.3
-
122
-
-
0030995361
-
Antibiotic treatment of initial colonization with Pseudomonas aeruginosa postpones chronic infection and prevents deterioration of pulmonary function in cystic fibrosis
-
B. Frederiksen, C. Koch and N. Høiby (1997) Antibiotic treatment of initial colonization with Pseudomonas aeruginosa postpones chronic infection and prevents deterioration of pulmonary function in cystic fibrosis. Pediatr Pulmonol. 23 330-335.
-
(1997)
Pediatr Pulmonol.
, vol.23
, pp. 330-335
-
-
Frederiksen, B.1
Koch, C.2
Høiby, N.3
-
123
-
-
0025868478
-
Prevention of chronic Pseudomonas aeruginosa colonisation in cystic fibrosis by early treatment
-
N.H. Valerius, C. Koch and N. Hoiby (1991) Prevention of chronic Pseudomonas aeruginosa colonisation in cystic fibrosis by early treatment. Lancet. 338 725-726.
-
(1991)
Lancet.
, vol.338
, pp. 725-726
-
-
Valerius, N.H.1
Koch, C.2
Hoiby, N.3
-
124
-
-
77950914953
-
Treatment of early Pseudomonas aeruginosa infection in patients with cystic fibrosis: the ELITE trial
-
F. Ratjen, A. Munck, P. Kho, et al. (2010) Treatment of early Pseudomonas aeruginosa infection in patients with cystic fibrosis: the ELITE trial. Thorax 65 286-291.
-
(2010)
Thorax
, vol.65
, pp. 286-291
-
-
Ratjen, F.1
Munck, A.2
Kho, P.3
-
125
-
-
23444457294
-
Combination antibiotic susceptibility testing to treat exacerbations of cystic fibrosis associated with multiresistant bacteria: a randomised, double-blind, controlled clinical trial
-
S.D. Aaron, K.L. Vandemheen, W. Ferris, et al. (2005) Combination antibiotic susceptibility testing to treat exacerbations of cystic fibrosis associated with multiresistant bacteria: a randomised, double-blind, controlled clinical trial. Lancet. 366 463-471.
-
(2005)
Lancet.
, vol.366
, pp. 463-471
-
-
Aaron, S.D.1
Vandemheen, K.L.2
Ferris, W.3
-
126
-
-
0023555047
-
Drug disposition in cystic fibrosis: progress in understanding pathophysiology and pharmacokinetics
-
J. Prandota (1987) Drug disposition in cystic fibrosis: progress in understanding pathophysiology and pharmacokinetics. Pediatr Infect Dis J. 6 1111-1126.
-
(1987)
Pediatr Infect Dis J.
, vol.6
, pp. 1111-1126
-
-
Prandota, J.1
-
127
-
-
0036733378
-
Pseudomonas aeruginosa: resistance and therapy
-
B.A. Cunha (2002) Pseudomonas aeruginosa: resistance and therapy. Semin Respir Infect. 17 231-239.
-
(2002)
Semin Respir Infect.
, vol.17
, pp. 231-239
-
-
Cunha, B.A.1
-
128
-
-
79952263651
-
Duration of intravenous antibiotic therapy in people with cystic fibrosis
-
CD006682
-
B. Fernandes, A. Plummer and M. Wildman (2008) Duration of intravenous antibiotic therapy in people with cystic fibrosis. Cochrane Database Syst Rev. 2 CD006682
-
(2008)
Cochrane Database Syst Rev.
, vol.2
-
-
Fernandes, B.1
Plummer, A.2
Wildman, M.3
-
129
-
-
0033531143
-
Intermittent administration of inhaled tobramycin in patients with cystic fibrosis. Cystic Fibrosis Inhaled Tobramycin Study Group
-
B.W. Ramsey, M.S. Pepe, J.M. Quan, et al. (1999) Intermittent administration of inhaled tobramycin in patients with cystic fibrosis. Cystic Fibrosis Inhaled Tobramycin Study Group. N Engl J Med. 340 23-30.
-
(1999)
N Engl J Med.
, vol.340
, pp. 23-30
-
-
Ramsey, B.W.1
Pepe, M.S.2
Quan, J.M.3
-
130
-
-
65949124667
-
Efficacy and safety of inhaled aztreonam lysine for airway pseudomonas in cystic fibrosis
-
G.Z. Retsch-Bogart, A.L. Quittner, R.L. Gibson, et al. (2009) Efficacy and safety of inhaled aztreonam lysine for airway pseudomonas in cystic fibrosis. Chest. 135 1223-1232.
-
(2009)
Chest.
, vol.135
, pp. 1223-1232
-
-
Retsch-Bogart, G.Z.1
Quittner, A.L.2
Gibson, R.L.3
-
131
-
-
0023265976
-
Colistin inhalation therapy in cystic fibrosis patients with chronic Pseudomonas aeruginosa lung infection
-
T. Jensen, S.S. Pedersen, S. Garne, et al. (1987) Colistin inhalation therapy in cystic fibrosis patients with chronic Pseudomonas aeruginosa lung infection. J Antimicrob Chemother. 19 831-838.
-
(1987)
J Antimicrob Chemother.
, vol.19
, pp. 831-838
-
-
Jensen, T.1
Pedersen, S.S.2
Garne, S.3
-
132
-
-
70350456264
-
Atypical mycobacterial and fungal infections in cystic fibrosis
-
L.A. Whittaker and C. Teneback (2009) Atypical mycobacterial and fungal infections in cystic fibrosis. Semin Respir Crit Care Med. 30 539-546.
-
(2009)
Semin Respir Crit Care Med.
, vol.30
, pp. 539-546
-
-
Whittaker, L.A.1
Teneback, C.2
-
133
-
-
0037445208
-
Nontuberculous mycobacteria. II: nested-cohort study of impact on cystic fibrosis lung disease
-
K.N. Olivier, D.J. Weber, J.H. Lee, et al. (2003) Nontuberculous mycobacteria. II: nested-cohort study of impact on cystic fibrosis lung disease. Am J Respir Crit Care Med. 167 835-840.
-
(2003)
Am J Respir Crit Care Med.
, vol.167
, pp. 835-840
-
-
Olivier, K.N.1
Weber, D.J.2
Lee, J.H.3
-
134
-
-
0018864505
-
Hypogammaglobulinemia in patients with cystic fibrosis
-
W.J. Matthews Jr, M. Williams, B. Oliphint, et al. (1980) Hypogammaglobulinemia in patients with cystic fibrosis. N Engl J Med. 302 245-249.
-
(1980)
N Engl J Med.
, vol.302
, pp. 245-249
-
-
Matthews, W.J.1
Williams, M.2
Oliphint, B.3
-
135
-
-
0021970474
-
Alternate-day prednisone reduces morbidity and improves pulmonary function in cystic fibrosis
-
H. Auerbach, M. Williams, J. Kirkpatrick, et al. (1985) Alternate-day prednisone reduces morbidity and improves pulmonary function in cystic fibrosis. Lancet. 2 686-688.
-
(1985)
Lancet.
, vol.2
, pp. 686-688
-
-
Auerbach, H.1
Williams, M.2
Kirkpatrick, J.3
-
136
-
-
0028969594
-
A multicenter study of alternate-day prednisone therapy in patients with cystic fibrosis. Cystic Fibrosis Foundation Prednisone Trial Group
-
H. Eigen, B.J. Rosenstein, S. FitzSimmons, et al. (1995) A multicenter study of alternate-day prednisone therapy in patients with cystic fibrosis. Cystic Fibrosis Foundation Prednisone Trial Group. J Pediatr. 126 515-523.
-
(1995)
J Pediatr.
, vol.126
, pp. 515-523
-
-
Eigen, H.1
Rosenstein, B.J.2
FitzSimmons, S.3
-
138
-
-
0028914667
-
Effect of high-dose ibuprofen in patients with cystic fibrosis
-
M.W. Konstan, P.J. Byard, C.L. Hoppel, et al. (1995) Effect of high-dose ibuprofen in patients with cystic fibrosis. N Engl J Med. 332 848-854.
-
(1995)
N Engl J Med.
, vol.332
, pp. 848-854
-
-
Konstan, M.W.1
Byard, P.J.2
Hoppel, C.L.3
-
139
-
-
0141816759
-
Azithromycin in patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa: a randomized controlled trial
-
L. Saiman, B.C. Marshall, N. Mayer-Hamblett, et al. (2003) Azithromycin in patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa: a randomized controlled trial. JAMA. 290 1749-1756.
-
(2003)
JAMA.
, vol.290
, pp. 1749-1756
-
-
Saiman, L.1
Marshall, B.C.2
Mayer-Hamblett, N.3
-
140
-
-
77951887288
-
Effect of azithromycin on pulmonary function in patients with cystic fibrosis uninfected with Pseudomonas aeruginosa: a randomized controlled trial
-
L. Saiman, M. Anstead, N. Mayer-Hamblett, et al. (2010) Effect of azithromycin on pulmonary function in patients with cystic fibrosis uninfected with Pseudomonas aeruginosa: a randomized controlled trial. JAMA. 303 1707-1715.
-
(2010)
JAMA.
, vol.303
, pp. 1707-1715
-
-
Saiman, L.1
Anstead, M.2
Mayer-Hamblett, N.3
-
141
-
-
33645229803
-
High-dose oral N-acetylcysteine, a glutathione prodrug, modulates inflammation in cystic fibrosis
-
R. Tirouvanziam, C.K. Conrad, T. Bottiglieri, et al. (2006) High-dose oral N-acetylcysteine, a glutathione prodrug, modulates inflammation in cystic fibrosis. Proc Natl Acad Sci U S A. 103 4628-4633.
-
(2006)
Proc Natl Acad Sci U S A.
, vol.103
, pp. 4628-4633
-
-
Tirouvanziam, R.1
Conrad, C.K.2
Bottiglieri, T.3
-
142
-
-
0025966879
-
1-antitrypsin treatment of cystic fibrosis
-
N.G. McElvaney, R.C. Hubbard, P. Birrer, et al. (1991) Aerosol α1-antitrypsin treatment of cystic fibrosis. Lancet. 337 392-394.
-
(1991)
Lancet.
, vol.337
, pp. 392-394
-
-
McElvaney, N.G.1
Hubbard, R.C.2
Birrer, P.3
-
143
-
-
29144484773
-
Leukotriene receptor antagonists in children with cystic fibrosis lung disease : anti-inflammatory and clinical effects
-
S. Schmitt-Grohé and S. Zielen (2005) Leukotriene receptor antagonists in children with cystic fibrosis lung disease : anti-inflammatory and clinical effects. Paediatr Drugs. 7 353-363.
-
(2005)
Paediatr Drugs.
, vol.7
, pp. 353-363
-
-
Schmitt-Grohé, S.1
Zielen, S.2
-
144
-
-
20144387174
-
Randomized, double-blind, placebo-controlled, dose-escalating study of aerosolized interferon gamma-1b in patients with mild to moderate cystic fibrosis lung disease
-
R.B. Moss, N. Mayer-Hamblett, J. Wagener, et al. (2005) Randomized, double-blind, placebo-controlled, dose-escalating study of aerosolized interferon gamma-1b in patients with mild to moderate cystic fibrosis lung disease. Pediatr Pulmonol. 39 209-218.
-
(2005)
Pediatr Pulmonol.
, vol.39
, pp. 209-218
-
-
Moss, R.B.1
Mayer-Hamblett, N.2
Wagener, J.3
-
145
-
-
84921431378
-
Vaccines for preventing influenza in people with cystic fibrosis
-
CD001753
-
P. Dharmaraj and R.L. Smyth (2009) Vaccines for preventing influenza in people with cystic fibrosis. Cochrane Database Syst Rev. 4 CD001753
-
(2009)
Cochrane Database Syst Rev.
, vol.4
-
-
Dharmaraj, P.1
Smyth, R.L.2
-
146
-
-
77950824214
-
Influenza-associated cystic fibrosis pulmonary exacerbations
-
J.R. Ortiz, K.M. Neuzil, J.C. Victor, et al. (2010) Influenza-associated cystic fibrosis pulmonary exacerbations. Chest. 137 852-860.
-
(2010)
Chest.
, vol.137
, pp. 852-860
-
-
Ortiz, J.R.1
Neuzil, K.M.2
Victor, J.C.3
-
147
-
-
84887225754
-
Palivizumab for prophylaxis against respiratory syncytial virus infection in children with cystic fibrosis
-
CD007743
-
K.A. Robinson, O.A. Odelola, I. Saldanha, et al. (2010) Palivizumab for prophylaxis against respiratory syncytial virus infection in children with cystic fibrosis. Cochrane Database Syst Rev. 2 CD007743
-
(2010)
Cochrane Database Syst Rev.
, vol.2
-
-
Robinson, K.A.1
Odelola, O.A.2
Saldanha, I.3
-
148
-
-
17744372496
-
Early diagnosis of cystic fibrosis through neonatal screening prevents severe malnutrition and improves long-term growth
-
P.M. Farrell, M.R. Kosorok, M.J. Rock, et al. (2001) Early diagnosis of cystic fibrosis through neonatal screening prevents severe malnutrition and improves long-term growth. Pediatrics. 107 1-13.
-
(2001)
Pediatrics.
, vol.107
, pp. 1-13
-
-
Farrell, P.M.1
Kosorok, M.R.2
Rock, M.J.3
-
150
-
-
33846910543
-
Cystic fibrosis diagnosed after 2 months of age leads to worse outcomes and requires more therapy
-
E.J. Sims, A. Clark, J. McCormick, et al. (2007) Cystic fibrosis diagnosed after 2 months of age leads to worse outcomes and requires more therapy. Pediatrics. 119 19-28.
-
(2007)
Pediatrics.
, vol.119
, pp. 19-28
-
-
Sims, E.J.1
Clark, A.2
McCormick, J.3
-
151
-
-
0036220978
-
Antibiotic prophylaxis in infants and young children with cystic fibrosis: A randomized controlled trial
-
H.R. Stutman, J.M. Lieberman, E. Nussbaum, et al. (2002) Antibiotic prophylaxis in infants and young children with cystic fibrosis: A randomized controlled trial. J Pediatr. 140 299-305.
-
(2002)
J Pediatr.
, vol.140
, pp. 299-305
-
-
Stutman, H.R.1
Lieberman, J.M.2
Nussbaum, E.3
-
152
-
-
84921429624
-
Prophylactic antibiotics for cystic fibrosis
-
CD001912
-
A. Smyth and S. Walters (2003) Prophylactic antibiotics for cystic fibrosis. Cochrane Database Syst Rev. 3 CD001912
-
(2003)
Cochrane Database Syst Rev.
, vol.3
-
-
Smyth, A.1
Walters, S.2
-
153
-
-
84891705714
-
Vaccines for preventing infection with Pseudomonas aeruginosa in cystic fibrosis
-
CD001399
-
H.K. Johansen and P.C. Gotzsche (2008) Vaccines for preventing infection with Pseudomonas aeruginosa in cystic fibrosis. Cochrane Database Syst Rev. 4 CD001399
-
(2008)
Cochrane Database Syst Rev.
, vol.4
-
-
Johansen, H.K.1
Gotzsche, P.C.2
-
154
-
-
68949167590
-
Palivizumab, pneumococcal and influenza vaccination in cystic fibrosis
-
M. Jain and A.H. Thomson (2009) Palivizumab, pneumococcal and influenza vaccination in cystic fibrosis. J R Soc Med. 102(suppl), 23-28.
-
(2009)
J R Soc Med.
, vol.102
, pp. 23-28
-
-
Jain, M.1
Thomson, A.H.2
-
155
-
-
77955413607
-
Early eradication of Pseudomonas aeruginosa in patients with cystic fibrosis
-
B. Stuart, J.H. Lin and P.J. Mogayzel Jr (2010) Early eradication of Pseudomonas aeruginosa in patients with cystic fibrosis. Paediatr Respir Rev. 11 177-184.
-
(2010)
Paediatr Respir Rev.
, vol.11
, pp. 177-184
-
-
Stuart, B.1
Lin, J.H.2
Mogayzel, P.J.3
-
156
-
-
70349240683
-
Registry of the International Society for Heart and Lung Transplantation: Twelfth Official Pediatric Lung and Heart/Lung Transplantation Report 2009
-
P. Aurora, L.B. Edwards, J.D. Christie, et al. (2009) Registry of the International Society for Heart and Lung Transplantation: Twelfth Official Pediatric Lung and Heart/Lung Transplantation Report 2009. J Heart Lung Transplant. 28 1023-1030.
-
(2009)
J Heart Lung Transplant.
, vol.28
, pp. 1023-1030
-
-
Aurora, P.1
Edwards, L.B.2
Christie, J.D.3
-
157
-
-
0035865730
-
Predictive 5-year survivorship model of cystic fibrosis
-
T.G. Liou, F.R. Adler, S.C. Fitzsimmons, et al. (2001) Predictive 5-year survivorship model of cystic fibrosis. Am J Epidemiol. 153 345-352.
-
(2001)
Am J Epidemiol.
, vol.153
, pp. 345-352
-
-
Liou, T.G.1
Adler, F.R.2
Fitzsimmons, S.C.3
-
158
-
-
33645685224
-
Development of the new lung allocation system in the United States
-
T.M. Egan, S. Murray, R.T. Bustami, et al. (2006) Development of the new lung allocation system in the United States. Am J Transplant. 6 1212-1227.
-
(2006)
Am J Transplant.
, vol.6
, pp. 1212-1227
-
-
Egan, T.M.1
Murray, S.2
Bustami, R.T.3
-
159
-
-
33846372637
-
Pre-transplant mechanical ventilation increases short-term morbidity and mortality in pediatric patients with cystic fibrosis
-
A. Elizur, S.C. Sweet, C.B. Huddleston, et al. (2007) Pre-transplant mechanical ventilation increases short-term morbidity and mortality in pediatric patients with cystic fibrosis. J Heart Lung Transplant. 26 127-131.
-
(2007)
J Heart Lung Transplant.
, vol.26
, pp. 127-131
-
-
Elizur, A.1
Sweet, S.C.2
Huddleston, C.B.3
-
160
-
-
34250617423
-
Lower incidence of bronchiolitis obliterans in pediatric liver-lung transplant recipients with cystic fibrosis
-
A. Faro, R. Shepherd, C.B. Huddleston, et al. (2007) Lower incidence of bronchiolitis obliterans in pediatric liver-lung transplant recipients with cystic fibrosis. Transplantation. 83 1435-1439.
-
(2007)
Transplantation.
, vol.83
, pp. 1435-1439
-
-
Faro, A.1
Shepherd, R.2
Huddleston, C.B.3
-
161
-
-
40749097542
-
Pediatric transplantation in the United States, 1997-2006
-
J.C. Magee, S.M. Krishnan, M.R. Benfield, et al. (2008) Pediatric transplantation in the United States, 1997-2006. Am J Transplant. 8 935-945.
-
(2008)
Am J Transplant.
, vol.8
, pp. 935-945
-
-
Magee, J.C.1
Krishnan, S.M.2
Benfield, M.R.3
-
163
-
-
36348965454
-
Lung transplantation and survival in children with cystic fibrosis
-
T.G. Liou, F.R. Adler, D.R. Cox, et al. (2007) Lung transplantation and survival in children with cystic fibrosis. N Engl J Med. 357 2143-2152.
-
(2007)
N Engl J Med.
, vol.357
, pp. 2143-2152
-
-
Liou, T.G.1
Adler, F.R.2
Cox, D.R.3
-
164
-
-
40149089861
-
Lung transplantation and survival in children with cystic fibrosis: solid statistics—flawed interpretation
-
S.C. Sweet, P. Aurora, C. Benden, et al. (2008) Lung transplantation and survival in children with cystic fibrosis: solid statistics—flawed interpretation. Pediatr Transplant. 12 129-136.
-
(2008)
Pediatr Transplant.
, vol.12
, pp. 129-136
-
-
Sweet, S.C.1
Aurora, P.2
Benden, C.3
-
165
-
-
0033530379
-
Lung transplantation and life extension in children with cystic fibrosis
-
P. Aurora, B. Whitehead, A. Wade, et al. (1999) Lung transplantation and life extension in children with cystic fibrosis. Lancet. 354 1591-1593.
-
(1999)
Lancet.
, vol.354
, pp. 1591-1593
-
-
Aurora, P.1
Whitehead, B.2
Wade, A.3
-
166
-
-
15544388657
-
Quality of life after lung transplantation: a cross-sectional study
-
B. Smeritschnig, P. Jaksch, A. Kocher, et al. (2005) Quality of life after lung transplantation: a cross-sectional study. J Heart Lung Transplant. 24 474-480.
-
(2005)
J Heart Lung Transplant.
, vol.24
, pp. 474-480
-
-
Smeritschnig, B.1
Jaksch, P.2
Kocher, A.3
-
167
-
-
50149098401
-
Effectiveness of PTC124 treatment of cystic fibrosis caused by nonsense mutations: a prospective phase II trial
-
E. Kerem, S. Hirawat, S. Armoni, et al. (2008) Effectiveness of PTC124 treatment of cystic fibrosis caused by nonsense mutations: a prospective phase II trial. Lancet. 372 719-727.
-
(2008)
Lancet.
, vol.372
, pp. 719-727
-
-
Kerem, E.1
Hirawat, S.2
Armoni, S.3
-
168
-
-
33744831154
-
Rescue of DeltaF508-CFTR trafficking and gating in human cystic fibrosis airway primary cultures by small molecules
-
F. Van Goor, K.S. Straley, D. Cao, et al. (2006) Rescue of DeltaF508-CFTR trafficking and gating in human cystic fibrosis airway primary cultures by small molecules. Am J Physiol Lung Cell Mol Physiol. 290 L1117-L1130.
-
(2006)
Am J Physiol Lung Cell Mol Physiol.
, vol.290
, pp. L1117-L1130
-
-
Van Goor, F.1
Straley, K.S.2
Cao, D.3
-
169
-
-
73249114731
-
Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770
-
F. Van Goor, S. Hadida, P.D. Grootenhuis, et al. (2009) Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770. Proc Natl Acad Sci U S A. 106 18825-18830.
-
(2009)
Proc Natl Acad Sci U S A.
, vol.106
, pp. 18825-18830
-
-
Van Goor, F.1
Hadida, S.2
Grootenhuis, P.D.3
-
170
-
-
34547949974
-
Phase 2 Randomized safety and efficacy trial of nebulized denufosol tetrasodium in cystic fibrosis
-
R.R. Deterding, L.M. LaVange, J.M. Engels, et al. (2007) Phase 2 Randomized safety and efficacy trial of nebulized denufosol tetrasodium in cystic fibrosis. Am J Respir Crit Care Med. 176 362-369.
-
(2007)
Am J Respir Crit Care Med.
, vol.176
, pp. 362-369
-
-
Deterding, R.R.1
LaVange, L.M.2
Engels, J.M.3
-
171
-
-
34248597371
-
Inhalation of Moli 1901 in patients with cystic fibrosis
-
H. Grasemann, F. Stehling, H. Brunar, et al. (2007) Inhalation of Moli 1901 in patients with cystic fibrosis. Chest 131 1461-1466.
-
(2007)
Chest
, vol.131
, pp. 1461-1466
-
-
Grasemann, H.1
Stehling, F.2
Brunar, H.3
|