-
1
-
-
0032906408
-
The innate immune system in cystic fibrosis lung disease
-
Bals, R., Weiner, D.J., and Wilson, J.M. 1999. The innate immune system in cystic fibrosis lung disease. J. Clin. Invest. 103:303-307.
-
(1999)
J. Clin. Invest.
, vol.103
, pp. 303-307
-
-
Bals, R.1
Weiner, D.J.2
Wilson, J.M.3
-
2
-
-
0030458141
-
Dendritic cells are recruited into the airway epithelium during the inflammatory response to a broad spectrum of stimuli
-
McWilliam, A.S., et al. 1996. Dendritic cells are recruited into the airway epithelium during the inflammatory response to a broad spectrum of stimuli. J. Exp. Med. 184:2429-2432.
-
(1996)
J. Exp. Med.
, vol.184
, pp. 2429-2432
-
-
McWilliam, A.S.1
-
3
-
-
0026687233
-
Defective regulation of outwardly rectifying cl-channels by protein kinase a corrected by insertion of cftr
-
Egan, M., et al. 1992. Defective regulation of outwardly rectifying Cl-channels by protein kinase A corrected by insertion of CFTR. Nature. 358:581-584.
-
(1992)
Nature
, vol.358
, pp. 581-584
-
-
Egan, M.1
-
4
-
-
0030970422
-
Cystic fibrosis transmembrane conductance regulator inverts protein kinase a-mediated regulation of epithelial sodium channel single channel kinetics
-
Stutts, M.J., Rossier, B.C., and Boucher, R.C. 1997. Cystic fibrosis transmembrane conductance regulator inverts protein kinase A-mediated regulation of epithelial sodium channel single channel kinetics. J. Biol. Chem. 272:14037-14040.
-
(1997)
J. Biol. Chem.
, vol.272
, pp. 14037-14040
-
-
Stutts, M.J.1
Rossier, B.C.2
Boucher, R.C.3
-
5
-
-
0020610435
-
Abnormal ion permeation through cystic fibrosis respiratory epithelium
-
Knowles, M.R., et al. 1983. Abnormal ion permeation through cystic fibrosis respiratory epithelium. Science. 221:1067-1070.
-
(1983)
Science
, vol.221
, pp. 1067-1070
-
-
Knowles, M.R.1
-
7
-
-
0009798178
-
+ and cftr cl-conductances by pka phosphorylation in the native sweat duct
-
+ and CFTR Cl-conductances by PKA phosphorylation in the native sweat duct. Ped. Pulm. 14 (Suppl.):230-231.
-
(1997)
Ped. Pulm.
, vol.14
, Issue.SUPPL.
, pp. 230-231
-
-
Reddy, M.M.1
Quinton, P.M.2
-
8
-
-
0028982894
-
Cftr as a camp-dependent regulator of sodium channels
-
Stutts, M.J., et al. 1995. CFTR as a cAMP-dependent regulator of sodium channels. Science. 269:847-850.
-
(1995)
Science
, vol.269
, pp. 847-850
-
-
Stutts, M.J.1
-
9
-
-
0029870085
-
Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid
-
Smith, J.J., Travis, S.M. Greenberg, E.P., and Welsh, M.J. 1996. Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid. Cell. 85:229-236.
-
(1996)
Cell
, vol.85
, pp. 229-236
-
-
Smith, J.J.1
Travis, S.M.2
Greenberg, E.P.3
Welsh, M.J.4
-
10
-
-
0032160101
-
Loss of cftr chloride channels alters salt absorption by cystic fibrosis airway epithelia in vitro
-
Zabner, J., Smith, J.J., Karp, P.H., Widdicombe, J.H., and Welsh, M.J. 1998. Loss of CFTR chloride channels alters salt absorption by cystic fibrosis airway epithelia in vitro. Mol. Cell. 2:397-403.
-
(1998)
Mol. Cell
, vol.2
, pp. 397-403
-
-
Zabner, J.1
Smith, J.J.2
Karp, P.H.3
Widdicombe, J.H.4
Welsh, M.J.5
-
11
-
-
0022970788
-
Missing cl conductance in cystic fibrosis
-
Quinton, P.M. 1986. Missing Cl conductance in cystic fibrosis. Am. J. Physiol. 251:C649-C6S2.
-
(1986)
Am. J. Physiol.
, vol.251
-
-
Quinton, P.M.1
-
12
-
-
0020700816
-
Chloride impermeability in cystic fibrosis
-
Quinton, P.M. 1983. Chloride impermeability in cystic fibrosis. Nature. 301:421-422.
-
(1983)
Nature
, vol.301
, pp. 421-422
-
-
Quinton, P.M.1
-
13
-
-
0030949875
-
Human beta-defensin-1 is a salt-sensitive antibiotic in lung that is inactivated in cystic fibrosis
-
Goldman, M.J., Anderson, G.M., Stolzenberg, E.D., Kari, U.P., Zasloff, M., and Wilson, J.M. 1997. Human beta-defensin-1 is a salt-sensitive antibiotic in lung that is inactivated in cystic fibrosis. Cell. 88:553-560.
-
(1997)
Cell
, vol.88
, pp. 553-560
-
-
Goldman, M.J.1
Anderson, G.M.2
Stolzenberg, E.D.3
Kari, U.P.4
Zasloff, M.5
Wilson, J.M.6
-
14
-
-
0032433707
-
Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease
-
Matsui, H., et al. 1998. Evidence for periciliary liquid layer depletion, not abnormal Ion composition, in the pathogenesis of cystic fibrosis airways disease. Cell. 95:1005-1015.
-
(1998)
Cell
, vol.95
, pp. 1005-1015
-
-
Matsui, H.1
-
15
-
-
0026907529
-
Mislocalization of delta f508 cftr in cystic fibrosis sweat gland
-
Kartner, N., Augustinas, O., Jensen, T.J., Naismith, A.L., and Riordan, J.R. 1992. Mislocalization of delta F508 CFTR in cystic fibrosis sweat gland. Nat. Genet. 1:321-327.
-
(1992)
Nat. Genet.
, vol.1
, pp. 321-327
-
-
Kartner, N.1
Augustinas, O.2
Jensen, T.J.3
Naismith, A.L.4
Riordan, J.R.5
-
16
-
-
0031786931
-
Role of aquaporin water channels in kidney and lung
-
Verkman, A.S. 1998. Role of aquaporin water channels in kidney and lung. Am. J. Med. Sci. 316:310-320.
-
(1998)
Am. J. Med. Sci.
, vol.316
, pp. 310-320
-
-
Verkman, A.S.1
-
17
-
-
0030984472
-
Plasma membrane water permeability of cultured cells and epithelia measured by light microscopy with spatial filtering
-
Farinas, J., Kneen, M., Moore, M., and Verkman, A.S. 1997. Plasma membrane water permeability of cultured cells and epithelia measured by light microscopy with spatial filtering. J. Gen. Physiol. 110:283-296.
-
(1997)
J. Gen. Physiol.
, vol.110
, pp. 283-296
-
-
Farinas, J.1
Kneen, M.2
Moore, M.3
Verkman, A.S.4
-
18
-
-
0025995482
-
Simple technique for culture of highly differentiated cells from dog tracheal epithelium
-
Kondo, M., Finkbeiner, W.E., and Widdicombe, J.H. 1991. Simple technique for culture of highly differentiated cells from dog tracheal epithelium. Am. J. Physiol. 261:L106-L117.
-
(1991)
Am. J. Physiol.
, vol.261
-
-
Kondo, M.1
Finkbeiner, W.E.2
Widdicombe, J.H.3
-
19
-
-
0032414862
-
Camp-dependent absorption of chloride across airway epithelium
-
Uyekubo, S.N., et al. 1998. cAMP-dependent absorption of chloride across airway epithelium. Am. J. Physiol. 275:L1219-L1227.
-
(1998)
Am. J. Physiol.
, vol.275
-
-
Uyekubo, S.N.1
-
20
-
-
0027141851
-
Elemental composition of human airway surface fluid in healthy and diseased airways
-
Joris, L., Dab, I., and Quinton, P.M. 1993. Elemental composition of human airway surface fluid in healthy and diseased airways. Am. Rev. Respir. Dis. 148:1633-1637.
-
(1993)
Am. Rev. Respir. Dis.
, vol.148
, pp. 1633-1637
-
-
Joris, L.1
Dab, I.2
Quinton, P.M.3
-
21
-
-
0028097887
-
Viscosity versus composition in airway pathology
-
Quinton, P.M. 1994. Viscosity versus composition in airway pathology. Am. J. Respir. Crit. Care Med. 149:6-7.
-
(1994)
Am. J. Respir. Crit. Care Med.
, vol.149
, pp. 6-7
-
-
Quinton, P.M.1
-
22
-
-
0026951303
-
Submucosal glands are the predominant site of cftr expression in the human bronchus
-
Engelhardt, J.F., et al. 1992. Submucosal glands are the predominant site of CFTR expression in the human bronchus. Nat. Genet. 2:240-248.
-
(1992)
Nat. Genet.
, vol.2
, pp. 240-248
-
-
Engelhardt, J.F.1
-
23
-
-
0028210022
-
Expression of the cystic fibrosis gene in adult human lung
-
Engelhardt, J.F., Zepeda, M., Cohn, J.A., Yankaskas, J.R., and Wilson, J.M. 1994. Expression of the cystic fibrosis gene in adult human lung. J. Clin. Invest. 93:737-749.
-
(1994)
J. Clin. Invest.
, vol.93
, pp. 737-749
-
-
Engelhardt, J.F.1
Zepeda, M.2
Cohn, J.A.3
Yankaskas, J.R.4
Wilson, J.M.5
-
24
-
-
0031913234
-
Inhibition of airway liquid secretion and its effect on the physical properties of airway mucus
-
Trout, L., King, M., Feng, W., Inglis, S.K., and Ballard, ST. 1998. Inhibition of airway liquid secretion and its effect on the physical properties of airway mucus. Am. J. Physiol. 274:L258-L263.
-
(1998)
Am. J. Physiol.
, vol.274
-
-
Trout, L.1
King, M.2
Feng, W.3
Inglis, S.K.4
Ballard, S.T.5
-
25
-
-
0028307695
-
Calu-3: A human airway epithelial cell line that shows camp-dependent cl-secretion
-
Shen, B.Q., Finkbeiner, W.E., Wine, J.J., Mrsny, R.J., and Widdicombe, J.H. 1994. Calu-3: a human airway epithelial cell line that shows cAMP-dependent Cl-secretion. Am. J. Physiol. 266:L493-L501.
-
(1994)
Am. J. Physiol.
, vol.266
-
-
Shen, B.Q.1
Finkbeiner, W.E.2
Wine, J.J.3
Mrsny, R.J.4
Widdicombe, J.H.5
-
26
-
-
0031943230
-
Evidence that calu-3 human airway cells secrete bicarbonate
-
Lee, M.C., Penland, C.M., Widdicombe, J.H., and Wine, J.J. 1998. Evidence that Calu-3 human airway cells secrete bicarbonate. Am. J. Physiol. 274:L450-L453.
-
(1998)
Am. J. Physiol.
, vol.274
-
-
Lee, M.C.1
Penland, C.M.2
Widdicombe, J.H.3
Wine, J.J.4
-
27
-
-
0031416788
-
Calcium-stimulated cl-secretion in calu-3 human airway cells requires cftr
-
Moon, S., Singh, M, Krouse, M.E., and Wine, J.J. 1997. Calcium-stimulated Cl-secretion in Calu-3 human airway cells requires CFTR Am. J. Physiol. 273:L1208-L1219.
-
(1997)
Am. J. Physiol.
, vol.273
-
-
Moon, S.1
Singh, M.2
Krouse, M.E.3
Wine, J.J.4
|