Pulmonary Abnormalities in Animal Models Due to Niemann-Pick Type C1 (NPC1) or C2 (NPC2) Disease

PLoS ONE

Volumn 8, Issue 7, 2013, Pages

  Roszell, Blair R ^a   Tao, Jian Qin ^a   Yu, Kevin J ^a   Gao, Ling ^a   Huang, Shaohui ^a   Ning, Yue ^a   Feinstein, Sheldon I ^a   Vite, Charles H ^b   Bates, Sandra R ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

MEMBRANE PROTEIN; NIEMANN PICK TYPE C1 PROTEIN; NIEMANN PICK TYPE C2 PROTEIN; SURFACTANT PROTEIN A; UNCLASSIFIED DRUG;

ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DISEASE ASSOCIATION; ELECTRON MICROSCOPY; GENE FREQUENCY; GENE MUTATION; IMMUNOCYTOCHEMISTRY; LAMELLAR BODY; LUNG ALVEOLUS MACROPHAGE; LUNG DISEASE; MORPHOLOGY; NIEMANN PICK DISEASE; NONHUMAN; PHENOTYPE; PROTEIN DEGRADATION; PROTEIN DOMAIN; PROTEIN TRANSPORT; SIGNAL TRANSDUCTION;

ANIMALS; ANIMALS, GENETICALLY MODIFIED; BRONCHOALVEOLAR LAVAGE FLUID; CATS; CHOLESTEROL; DISEASE MODELS, ANIMAL; FEMALE; LIPID METABOLISM; LUNG; MACROPHAGES, ALVEOLAR; MALE; MICE; NIEMANN-PICK DISEASE, TYPE C; PHOSPHOLIPIDS; PROTEIN ISOFORMS; PROTEINS; PULMONARY SURFACTANTS; VESICULAR TRANSPORT PROTEINS;

ANIMALIA; MUS;

EID: 84879758282     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0067084     Document Type: Article

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