Pulmonary function and pathology in hydroxypropyl-beta-cyclodextin-treated and untreated Npc1-/- mice

Molecular Genetics and Metabolism

Volumn 103, Issue 2, 2011, Pages 142-147

  Muralidhar, Akshay ^a   Borbon, Ivan A ^a   Esharif, Dyadin M ^a   Ke, Wangjing ^a   Manacheril, Rinu ^a   Daines, Michael ^a,b   Erickson, Robert P ^a,c  

^a UNIVERSITY OF ARIZONA COLLEGE OF MEDICINE   (United States)

^b UNIVERSITY OF ARIZONA   (United States)

^c University of Arizona   (United States)

Author keywords

Foamy macrophages; Hydroxypropyl beta cyclodextrins; Intracellular cholesterol transport; Niemann Pick C1; Small animal ventilator

Indexed keywords

2 HYDROXYPROPYL BETA CYCLODEXTRIN; CHOLESTEROL; COLLAGEN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; DRUG EFFECT; DRUG EFFICACY; HISTOPATHOLOGY; INSPIRATORY CAPACITY; LUNG ALVEOLUS MACROPHAGE; LUNG COMPLIANCE; LUNG WEIGHT; MOUSE; NIEMANN PICK DISEASE; NONHUMAN; PRIORITY JOURNAL; TREATMENT OUTCOME;

ANIMALS; BETA-CYCLODEXTRINS; CHOLESTEROL; DISEASE MODELS, ANIMAL; LUNG; MICE; MICE, INBRED BALB C; MICE, KNOCKOUT; NIEMANN-PICK DISEASE, TYPE C; RESPIRATORY FUNCTION TESTS;

ANIMALIA; MUS;

EID: 79956278406     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2011.03.001     Document Type: Article

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