Polyglutamine disease toxicity is regulated by nemo-like kinase in spinocerebellar ataxia type 1

Journal of Neuroscience

Volumn 33, Issue 22, 2013, Pages 9328-9336

  Ju, Hyoungseok ^a   Kokubu, Hiroshi ^a   Todd, Tiffany W ^a   Kahle, Juliette J ^b   Kim, Soeun ^a   Richman, Ronald ^b,c   Chirala, Karthik ^b   Orr, Harry T ^d   Zoghbi, Huda Y ^b,c   Lim, Janghoo ^a  

^a YALE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b BAYLOR COLLEGE OF MEDICINE   (United States)

^c TEXAS CHILDREN S HOSPITAL   (United States)

^d UNIVERSITY OF MINNESOTA MEDICAL SCHOOL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ATAXIN 1; I KAPPA B KINASE GAMMA; MITOGEN ACTIVATED PROTEIN KINASE; NEMO LIKE KINASE; POLYGLUTAMINE; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BEHAVIOR; CONFOCAL MICROSCOPY; CONTROLLED STUDY; DEGENERATIVE DISEASE; DROSOPHILA; GEL FILTRATION CHROMATOGRAPHY; GENE INTERACTION; HUMAN; HUMAN CELL; IMMUNOFLUORESCENCE TEST; IMMUNOPRECIPITATION; MOUSE; NEUROPATHOLOGY; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN INTERACTION; PROTEIN PHOSPHORYLATION; SPINOCEREBELLAR DEGENERATION; TRANSGENIC ORGANISM; WESTERN BLOTTING;

ANIMALS; ANIMALS, GENETICALLY MODIFIED; BEHAVIOR, ANIMAL; BLOTTING, WESTERN; BRAIN; CEREBELLUM; CHROMATOGRAPHY, GEL; DROSOPHILA MELANOGASTER; FEMALE; GENE EXPRESSION; HEK293 CELLS; HEREDODEGENERATIVE DISORDERS, NERVOUS SYSTEM; HUMANS; IMMUNOPRECIPITATION; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MITOGEN-ACTIVATED PROTEIN KINASES; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; PEPTIDES; PHOSPHORYLATION; SPINOCEREBELLAR ATAXIAS;

EID: 84878296871     PISSN: 02706474     EISSN: 15292401     Source Type: Journal    
DOI: 10.1523/JNEUROSCI.3465-12.2013     Document Type: Article

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