Granulomatous disease in CVID: Retrospective analysis of clinical characteristics and treatment efficacy in a cohort of 59 patients

Journal of Clinical Immunology

Volumn 33, Issue 1, 2013, Pages 84-95

  Boursiquot, Jean Nicolas ^a   Gérard, Laurence ^b   Malphettes, Marion ^b   Fieschi, Claire ^b   Galicier, Lionel ^b   Boutboul, David ^b   Borie, Raphael ^c   Viallard, Jean François ^d   Soulas Sprauel, Pauline ^e   Berezne, Alice ^f   Jaccard, Arnaud ^g   Hachulla, Eric ^h   Haroche, Julien ^f   Schleinitz, Nicolas ⁱ   Têtu, Laurent ^j   Oksenhendler, Eric ^b  

^a LAVAL UNIVERSITY   (Canada)

^b SAINT LOUIS HOSPITAL   (France)

^c HÔPITAL TENON   (France)

^d HAUT LÉVÊQUE HOSPITAL   (France)

^e INSERM   (France)

^f ASSISTANCE PUBLIQUE HÔPITAUX DE PARIS   (France)

^g DUPUYTREN UNIVERSITY HOSPITAL   (France)

^h LILLE UNIVERSITY HOSPITAL   (France)

ⁱ HÔPITAL DE LA CONCEPTION   (France)

^j CHU RANGUEIL   (France)

more..

Author keywords

Antibody deficiency; CVID; Granulomatous disease; Primary immune deficiency; Treatment

Indexed keywords

ALPHA2B INTERFERON; AZATHIOPRINE; CORTICOSTEROID; CYCLOPHOSPHAMIDE; CYCLOSPORIN; HYDROXYCHLOROQUINE; IMMUNOGLOBULIN A; IMMUNOGLOBULIN G; IMMUNOGLOBULIN M; IMMUNOSUPPRESSIVE AGENT; INFLIXIMAB; METHOTREXATE; MYCOPHENOLIC ACID 2 MORPHOLINOETHYL ESTER; PREDNISONE; RAPAMYCIN; RITUXIMAB; THALIDOMIDE;

ADULT; ARTICLE; COHORT ANALYSIS; COMMON VARIABLE IMMUNODEFICIENCY; DRUG EFFICACY; FEMALE; GRANULOMATOSIS; HUMAN; IMMUNOGLOBULIN BLOOD LEVEL; IMMUNOGLOBULIN DEFICIENCY; LIVER GRANULOMA; LUNG GRANULOMA; MAJOR CLINICAL STUDY; MALE; PRIORITY JOURNAL; PROSPECTIVE STUDY; REGULATORY T LYMPHOCYTE; RETROSPECTIVE STUDY; SKIN GRANULOMA; SPLENOMEGALY; TREATMENT RESPONSE; YOUNG ADULT; AGAMMAGLOBULINEMIA; ANTIBODY SPECIFICITY; CASE REPORT; CHILD; CHRONIC GRANULOMATOUS DISEASE; IMMUNOLOGY; IMMUNOPHENOTYPING; INFANT; NEWBORN; PRESCHOOL CHILD; REVIEW; TREATMENT OUTCOME;

ADULT; AGAMMAGLOBULINEMIA; CHILD; CHILD, PRESCHOOL; COHORT STUDIES; COMMON VARIABLE IMMUNODEFICIENCY; FEMALE; GRANULOMATOUS DISEASE, CHRONIC; HUMANS; IMMUNOPHENOTYPING; INFANT; INFANT, NEWBORN; MALE; ORGAN SPECIFICITY; PROSPECTIVE STUDIES; RETROSPECTIVE STUDIES; TREATMENT OUTCOME;

MLCS; MLOWN;

EID: 84876453775     PISSN: 02719142     EISSN: 15732592     Source Type: Journal    
DOI: 10.1007/s10875-012-9778-9     Document Type: Article

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