-
1
-
-
41749088672
-
Molecular mechanisms of prion pathogenesis
-
Aguzzi, A., Sigurdson, C., and Heikenwaelder, M. (2008) Molecular mechanisms of prion pathogenesis. Annu. Rev. Pathol. 3, 11-40
-
(2008)
Annu. Rev. Pathol.
, vol.3
, pp. 11-40
-
-
Aguzzi, A.1
Sigurdson, C.2
Heikenwaelder, M.3
-
2
-
-
0032816292
-
Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects
-
Parchi, P., Giese, A., Capellari, S., Brown, P., Schulz-Schaeffer, W., Windl, O., Zerr, I., Budka, H., Kopp, N., Piccardo, P., Poser, S., Rojiani, A., Streichemberger, N., Julien, J., Vital, C., Ghetti, B., Gambetti, P., and Kretzschmar, H. (1999) Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects. Ann. Neurol 46, 224-233
-
(1999)
Ann. Neurol
, vol.46
, pp. 224-233
-
-
Parchi, P.1
Giese, A.2
Capellari, S.3
Brown, P.4
Schulz-Schaeffer, W.5
Windl, O.6
Zerr, I.7
Budka, H.8
Kopp, N.9
Piccardo, P.10
Poser, S.11
Rojiani, A.12
Streichemberger, N.13
Julien, J.14
Vital, C.15
Ghetti, B.16
Gambetti, P.17
Kretzschmar, H.18
-
3
-
-
73549086979
-
Similarities between forms of sheep scrapie and Creutzfeldt-Jakob disease are encoded by distinct prion types
-
Wemheuer, W. M., Benestad, S. L., Wrede, A., Schulze-Sturm, U., Wemheuer, W. E., Hahmann, U., Gawinecka, J., Schütz, E., Zerr, I., Brenig, B., Bratberg, B., Andréoletti, O., and Schulz-Schaeffer, W. J. (2009) Similarities between forms of sheep scrapie and Creutzfeldt-Jakob disease are encoded by distinct prion types. Am. J. Pathol. 175, 2566-2573
-
(2009)
Am. J. Pathol.
, vol.175
, pp. 2566-2573
-
-
Wemheuer, W.M.1
Benestad, S.L.2
Wrede, A.3
Schulze-Sturm, U.4
Wemheuer, W.E.5
Hahmann, U.6
Gawinecka, J.7
Schütz, E.8
Zerr, I.9
Brenig, B.10
Bratberg, B.11
Andréoletti, O.12
Schulz-Schaeffer, W.J.13
-
4
-
-
12944253111
-
Genetic influence on the structural variations of the abnormal prion protein
-
Parchi, P., Zou, W., Wang, W., Brown, P., Capellari, S., Ghetti, B., Kopp, N., Schulz-Schaeffer, W. J., Kretzschmar, H. A., Head, M. W., Ironside, J. W., Gambetti, P., and Chen, S. G. (2000) Genetic influence on the structural variations of the abnormal prion protein. Proc. Natl. Acad. Sci. U. S. A. 97, 10168-10172
-
(2000)
Proc. Natl. Acad. Sci. U. S. A.
, vol.97
, pp. 10168-10172
-
-
Parchi, P.1
Zou, W.2
Wang, W.3
Brown, P.4
Capellari, S.5
Ghetti, B.6
Kopp, N.7
Schulz-Schaeffer, W.J.8
Kretzschmar, H.A.9
Head, M.W.10
Ironside, J.W.11
Gambetti, P.12
Chen, S.G.13
-
5
-
-
0029824332
-
Polymorphism at codon 129 of the prion protein gene determines cerebellar pathology in Creutzfeldt-Jakob disease
-
Schulz-Schaeffer, W. J., Giese, A., Windl, O., and Kretzschmar, H. A. (1996) Polymorphism at codon 129 of the prion protein gene determines cerebellar pathology in Creutzfeldt-Jakob disease. Clin. Neuropathol 15, 353-357
-
(1996)
Clin. Neuropathol
, vol.15
, pp. 353-357
-
-
Schulz-Schaeffer, W.J.1
Giese, A.2
Windl, O.3
Kretzschmar, H.A.4
-
6
-
-
34249680730
-
Creutzfeldt-Jakob disease in Germany: A prospective 12-year surveillance
-
Heinemann, U., Krasnianski, A., Meissner, B., Varges, D., Kallenberg, K., Schulz-Schaeffer, W. J., Steinhoff, B. J., Grasbon-Frodl, E. M., Kretzschmar, H. A., and Zerr, I. (2007) Creutzfeldt-Jakob disease in Germany: a prospective 12-year surveillance. Brain 130, 1350-1359
-
(2007)
Brain
, vol.130
, pp. 1350-1359
-
-
Heinemann, U.1
Krasnianski, A.2
Meissner, B.3
Varges, D.4
Kallenberg, K.5
Schulz-Schaeffer, W.J.6
Steinhoff, B.J.7
Grasbon-Frodl, E.M.8
Kretzschmar, H.A.9
Zerr, I.10
-
7
-
-
80054725724
-
Transgenic mouse models and prion strains
-
Telling, G. C. (2011) Transgenic mouse models and prion strains. Top Curr. Chem. 305, 79-99
-
(2011)
Top Curr. Chem.
, vol.305
, pp. 79-99
-
-
Telling, G.C.1
-
8
-
-
0034931126
-
Three-dimensional structures of prion proteins
-
Wüthrich, K., and Riek, R. (2001) Three-dimensional structures of prion proteins. Adv. Protein Chem. 57, 55-82
-
(2001)
Adv. Protein Chem.
, vol.57
, pp. 55-82
-
-
Wüthrich, K.1
Riek, R.2
-
9
-
-
70350134002
-
Natural and synthetic prion structure from x-ray fiber diffraction
-
Wille, H., Bian, W., McDonald, M., Kendall, A., Colby, D. W., Bloch, L., Ollesch, J., Borovinskiy, A. L., Cohen, F. E., Prusiner, S. B., and Stubbs, G. (2009) Natural and synthetic prion structure from x-ray fiber diffraction. Proc. Natl. Acad. Sci. U. S. A. 106, 16990-16995
-
(2009)
Proc. Natl. Acad. Sci. U. S. A.
, vol.106
, pp. 16990-16995
-
-
Wille, H.1
Bian, W.2
McDonald, M.3
Kendall, A.4
Colby, D.W.5
Bloch, L.6
Ollesch, J.7
Borovinskiy, A.L.8
Cohen, F.E.9
Prusiner, S.B.10
Stubbs, G.11
-
10
-
-
0038717543
-
Aprion protein epitope selective for the pathologically misfolded conformation
-
Paramithiotis, E., Pinard, M., Lawton, T., La Boissiere, S., Leathers, V. L., Zou, W. Q., Estey, L. A., Lamontagne, J., Lehto, M. T., Kondejewski, L. H., Francoeur, G. P., Papadopoulos, M., Haghighat, A., Spatz, S. J., Head, M., Will, R., Ironside, J., O'Rourke, K., Tonelli, Q., Ledebur, H. C., Chakrabartty, A., and Cashman, N. R. (2003) Aprion protein epitope selective for the pathologically misfolded conformation. Nat. Med. 9, 893-899
-
(2003)
Nat. Med.
, vol.9
, pp. 893-899
-
-
Paramithiotis, E.1
Pinard, M.2
Lawton, T.3
La Boissiere, S.4
Leathers, V.L.5
Zou, W.Q.6
Estey, L.A.7
Lamontagne, J.8
Lehto, M.T.9
Kondejewski, L.H.10
Francoeur, G.P.11
Papadopoulos, M.12
Haghighat, A.13
Spatz, S.J.14
Head, M.15
Will, R.16
Ironside, J.17
O'Rourke, K.18
Tonelli, Q.19
Ledebur, H.C.20
Chakrabartty, A.21
Cashman, N.R.22
more..
-
11
-
-
79953785159
-
Structural organization of brain-derived mammalian prions examined by hydrogen-deuterium exchange
-
Smirnovas, V., Baron, G. S., Offerdahl, D. K., Raymond, G. J., Caughey, B., and Surewicz, W. K. (2011) Structural organization of brain-derived mammalian prions examined by hydrogen-deuterium exchange. Nat. Struct. Mol. Biol. 18, 504-506
-
(2011)
Nat. Struct. Mol. Biol.
, vol.18
, pp. 504-506
-
-
Smirnovas, V.1
Baron, G.S.2
Offerdahl, D.K.3
Raymond, G.J.4
Caughey, B.5
Surewicz, W.K.6
-
12
-
-
2942616602
-
Evidence for assembly of prions with left-handed β-helices into trimers
-
Govaerts, C., Wille, H., Prusiner, S. B., and Cohen, F. E. (2004) Evidence for assembly of prions with left-handed β-helices into trimers. Proc. Natl. Acad. Sci. U. S. A. 101, 8342-8347
-
(2004)
Proc. Natl. Acad. Sci. U. S. A.
, vol.101
, pp. 8342-8347
-
-
Govaerts, C.1
Wille, H.2
Prusiner, S.B.3
Cohen, F.E.4
-
13
-
-
35748972976
-
Electron crystallography of the scrapie prion protein complexed with heavy metals
-
Wille, H., Govaerts, C., Borovinskiy, A., Latawiec, D., Downing, K. H., Cohen, F. E., and Prusiner, S. B. (2007) Electron crystallography of the scrapie prion protein complexed with heavy metals. Arch Biochem. Biophys. 467, 239-248
-
(2007)
Arch Biochem. Biophys.
, vol.467
, pp. 239-248
-
-
Wille, H.1
Govaerts, C.2
Borovinskiy, A.3
Latawiec, D.4
Downing, K.H.5
Cohen, F.E.6
Prusiner, S.B.7
-
14
-
-
62449276454
-
Left handed β helix models for mammalian prion fibrils
-
Kunes, K. C., Clark, S. C., Cox, D. L., and Singh, R. R. (2008) Left handed β helix models for mammalian prion fibrils. Prion 2, 81-90
-
(2008)
Prion
, vol.2
, pp. 81-90
-
-
Kunes, K.C.1
Clark, S.C.2
Cox, D.L.3
Singh, R.R.4
-
15
-
-
33846811599
-
β-Sheet core of human prion protein amyloid fibrils as determined by hydrogen/deuterium exchange
-
Lu, X., Wintrode, P. L., and Surewicz, W. K. (2007) β-Sheet core of human prion protein amyloid fibrils as determined by hydrogen/deuterium exchange. Proc. Natl. Acad. Sci. U. S. A. 104, 1510-1515
-
(2007)
Proc. Natl. Acad. Sci. U. S. A.
, vol.104
, pp. 1510-1515
-
-
Lu, X.1
Wintrode, P.L.2
Surewicz, W.K.3
-
16
-
-
67649204153
-
Hydrogen/deuterium exchange mass spectrometry identifies two highly protected regions in recombinant full-length prion protein amyloid fibrils
-
Nazabal, A., Hornemann, S., Aguzzi, A., and Zenobi, R. (2009) Hydrogen/deuterium exchange mass spectrometry identifies two highly protected regions in recombinant full-length prion protein amyloid fibrils. J. Mass Spectrom 44, 965-977
-
(2009)
J. Mass Spectrom
, vol.44
, pp. 965-977
-
-
Nazabal, A.1
Hornemann, S.2
Aguzzi, A.3
Zenobi, R.4
-
17
-
-
77957756752
-
Probing the conformation of a prion protein fibril with hydrogen exchange
-
Damo, S. M., Phillips, A. H., Young, A. L., Li, S., Woods, V. L., Jr., and Wemmer, D. E. (2010) Probing the conformation of a prion protein fibril with hydrogen exchange. J. Biol. Chem. 285, 32303-32311
-
(2010)
J. Biol. Chem.
, vol.285
, pp. 32303-32311
-
-
Damo, S.M.1
Phillips, A.H.2
Young, A.L.3
Li, S.4
Woods Jr., V.L.5
Wemmer, D.E.6
-
18
-
-
1442330474
-
From conversion to aggregation: Protofibril formation of the prion protein
-
De Marco, M. L., and Daggett, V. (2004) From conversion to aggregation: protofibril formation of the prion protein. Proc. Natl. Acad. Sci. U. S. A. 101, 2293-2298
-
(2004)
Proc. Natl. Acad. Sci. U. S. A.
, vol.101
, pp. 2293-2298
-
-
De Marco, M.L.1
Daggett, V.2
-
19
-
-
0029658434
-
Immunohistological evaluation of Creutzfeldt-Jakob disease with reference to the type PrPres deposition
-
Tateishi, J., Kitamoto, T., Kretzschmar, H., and Mehraein, P. (1996) Immunohistological evaluation of Creutzfeldt-Jakob disease with reference to the type PrPres deposition. Clin. Neuropathol 15, 358-360
-
(1996)
Clin. Neuropathol
, vol.15
, pp. 358-360
-
-
Tateishi, J.1
Kitamoto, T.2
Kretzschmar, H.3
Mehraein, P.4
-
20
-
-
0142091396
-
Nucleation-dependent conformational conversion of the Y145Stop variant of human prion protein: Structural clues for prion propagation
-
Kundu, B., Maiti, N. R., Jones, E. M., Surewicz, K. A., Vanik, D. L., and Surewicz, W. K. (2003) Nucleation-dependent conformational conversion of the Y145Stop variant of human prion protein: structural clues for prion propagation. Proc. Natl. Acad. Sci. U. S. A. 100, 12069-12074
-
(2003)
Proc. Natl. Acad. Sci. U. S. A.
, vol.100
, pp. 12069-12074
-
-
Kundu, B.1
Maiti, N.R.2
Jones, E.M.3
Surewicz, K.A.4
Vanik, D.L.5
Surewicz, W.K.6
-
21
-
-
1842766124
-
Molecular basis of barriers for interspecies transmissibility of mammalian prions
-
Vanik, D. L., Surewicz, K. A., and Surewicz, W. K. (2004) Molecular basis of barriers for interspecies transmissibility of mammalian prions. Mol. Cell 14, 139-145
-
(2004)
Mol. Cell
, vol.14
, pp. 139-145
-
-
Vanik, D.L.1
Surewicz, K.A.2
Surewicz, W.K.3
-
22
-
-
33749574062
-
Prion protein helix1 promotes aggregation but is not converted into β-sheet
-
Watzlawik, J., Skora, L., Frense, D., Griesinger, C., Zweckstetter, M., Schulz-Schaeffer, W. J., and Kramer, M. L. (2006) Prion protein helix1 promotes aggregation but is not converted into β-sheet. J. Biol. Chem. 281, 30242-30250
-
(2006)
J. Biol. Chem.
, vol.281
, pp. 30242-30250
-
-
Watzlawik, J.1
Skora, L.2
Frense, D.3
Griesinger, C.4
Zweckstetter, M.5
Schulz-Schaeffer, W.J.6
Kramer, M.L.7
-
23
-
-
79955397626
-
Familial prion disease with Alzheimer disease-like Tau pathology and clinical phenotype
-
Jayadev, S., Nochlin, D., Poorkaj, P., Steinbart, E. J., Mastrianni, J. A., Montine, T. J., Ghetti, B., Schellenberg, G. D., Bird, T. D., and Leverenz, J. B. (2011) Familial prion disease with Alzheimer disease-like Tau pathology and clinical phenotype. Ann. Neurol 69, 712-720
-
(2011)
Ann. Neurol
, vol.69
, pp. 712-720
-
-
Jayadev, S.1
Nochlin, D.2
Poorkaj, P.3
Steinbart, E.J.4
Mastrianni, J.A.5
Montine, T.J.6
Ghetti, B.7
Schellenberg, G.D.8
Bird, T.D.9
Leverenz, J.B.10
-
24
-
-
44049102092
-
Molecular conformation and dynamics of the Y145Stop variant of human prion protein in amyloid fibrils
-
Helmus, J. J., Surewicz, K., Nadaud, P. S., Surewicz, W. K., and Jaroniec, C. P. (2008) Molecular conformation and dynamics of the Y145Stop variant of human prion protein in amyloid fibrils. Proc. Natl. Acad. Sci. U. S. A. 105, 6284-6289
-
(2008)
Proc. Natl. Acad. Sci. U. S. A.
, vol.105
, pp. 6284-6289
-
-
Helmus, J.J.1
Surewicz, K.2
Nadaud, P.S.3
Surewicz, W.K.4
Jaroniec, C.P.5
-
25
-
-
77749237271
-
Conformational flexibility of Y145Stop human prion protein amyloid fibrils probed by solid-state nuclear magnetic resonance spectroscopy
-
Helmus, J. J., Surewicz, K., Surewicz, W. K., and Jaroniec, C. P. (2010) Conformational flexibility of Y145Stop human prion protein amyloid fibrils probed by solid-state nuclear magnetic resonance spectroscopy. J. Am. Chem. Soc. 132, 2393-2403
-
(2010)
J. Am. Chem. Soc.
, vol.132
, pp. 2393-2403
-
-
Helmus, J.J.1
Surewicz, K.2
Surewicz, W.K.3
Jaroniec, C.P.4
-
26
-
-
80052320137
-
Intermolecular alignment in Y145Stop human prion protein amyloid fibrils probed by solid-state NMR spectroscopy
-
Helmus, J. J., Surewicz, K., Apostol, M. I., Surewicz, W. K., and Jaroniec, C. P. (2011) Intermolecular alignment in Y145Stop human prion protein amyloid fibrils probed by solid-state NMR spectroscopy. J. Am. Chem. Soc. 133, 13934-13937
-
(2011)
J. Am. Chem. Soc.
, vol.133
, pp. 13934-13937
-
-
Helmus, J.J.1
Surewicz, K.2
Apostol, M.I.3
Surewicz, W.K.4
Jaroniec, C.P.5
-
27
-
-
0033574161
-
Influence of amino acid substitutions related to inherited human prion diseases on the thermodynamic stability of the cellular prion protein
-
Liemann, S., and Glockshuber, R. (1999) Influence of amino acid substitutions related to inherited human prion diseases on the thermodynamic stability of the cellular prion protein. Biochemistry 38, 3258-3267
-
(1999)
Biochemistry
, vol.38
, pp. 3258-3267
-
-
Liemann, S.1
Glockshuber, R.2
-
28
-
-
79251538912
-
Conserved core of amyloid fibrils of wild type and A30P mutant α-synuclein
-
Cho, M. K., Kim, H. Y., Fernandez, C. O., Becker, S., and Zweckstetter, M. (2011) Conserved core of amyloid fibrils of wild type and A30P mutant α-synuclein. Protein Sci. 20, 387-395
-
(2011)
Protein Sci.
, vol.20
, pp. 387-395
-
-
Cho, M.K.1
Kim, H.Y.2
Fernandez, C.O.3
Becker, S.4
Zweckstetter, M.5
-
29
-
-
0029400480
-
NMRPipe: A multidimensional spectral processing system based on UNIX pipes
-
Delaglio, F., Grzesiek, S., Vuister, G. W., Zhu, G., Pfeifer, J., and Bax, A. (1995) NMRPipe: a multidimensional spectral processing system based on UNIX pipes. J. Biomol. NMR 6, 277-293
-
(1995)
J. Biomol. NMR
, vol.6
, pp. 277-293
-
-
Delaglio, F.1
Grzesiek, S.2
Vuister, G.W.3
Zhu, G.4
Pfeifer, J.5
Bax, A.6
-
30
-
-
12044252858
-
Methodological advances in protein
-
Bax, A., and Grzesiek, S. (1993) Methodological advances in protein. Acc. Chem. Res. 26, 131-138
-
(1993)
Acc. Chem. Res.
, vol.26
, pp. 131-138
-
-
Bax, A.1
Grzesiek, S.2
-
32
-
-
33646376290
-
Spin diffusion measurements: Spin echoes in the presence of a time-dependent field gradient
-
Stejskal, E. O., and Tanner, J. E. (1965) Spin diffusion measurements: spin echoes in the presence of a time-dependent field gradient. J. Chem. Phys. 42, 288-292
-
(1965)
J. Chem. Phys.
, vol.42
, pp. 288-292
-
-
Stejskal, E.O.1
Tanner, J.E.2
-
33
-
-
58149362694
-
An improved diffusionordered spectroscopy experiment incorporating bipolar-gradient pulses
-
Wu, D. H., Chen, A. D., and Johnson, C. S. (1995) An improved diffusionordered spectroscopy experiment incorporating bipolar-gradient pulses. J. Magn. Reson. A 115, 260-264
-
(1995)
J. Magn. Reson. A
, vol.115
, pp. 260-264
-
-
Wu, D.H.1
Chen, A.D.2
Johnson, C.S.3
-
34
-
-
0037442729
-
Protein surface mapping by chemical oxidation: Structural analysis by mass spectrometry
-
Sharp, J. S., Becker, J. M., and Hettich, R. L. (2003) Protein surface mapping by chemical oxidation: structural analysis by mass spectrometry. Anal. Biochem. 313, 216-225
-
(2003)
Anal. Biochem.
, vol.313
, pp. 216-225
-
-
Sharp, J.S.1
Becker, J.M.2
Hettich, R.L.3
-
35
-
-
0037317228
-
Stop and go extraction tips for matrix-assisted laser desorption/ionization, nanoelectrospray, and LC/MS sample pretreatment in proteomics
-
Rappsilber, J., Ishihama, Y., and Mann, M. (2003) Stop and go extraction tips for matrix-assisted laser desorption/ionization, nanoelectrospray, and LC/MS sample pretreatment in proteomics. Anal. Chem. 75, 663-670
-
(2003)
Anal. Chem.
, vol.75
, pp. 663-670
-
-
Rappsilber, J.1
Ishihama, Y.2
Mann, M.3
-
36
-
-
57449099865
-
MaxQuant enables high peptide identification rates, individualized p. p. b.-range mass accuracies, and proteomewide protein quantification
-
Cox, J., and Mann, M. (2008) MaxQuant enables high peptide identification rates, individualized p. p. b.-range mass accuracies, and proteomewide protein quantification. Nat. Biotechnol. 26, 1367-1372
-
(2008)
Nat. Biotechnol.
, vol.26
, pp. 1367-1372
-
-
Cox, J.1
Mann, M.2
-
37
-
-
79953701087
-
Andromeda: A peptide search engine integrated into the MaxQuant environment
-
Cox, J., Neuhauser, N., Michalski, A., Scheltema, R. A., Olsen, J. V., and Mann, M. (2011) Andromeda: a peptide search engine integrated into the MaxQuant environment. J. Proteome Res. 10, 1794-1805
-
(2011)
J. Proteome Res.
, vol.10
, pp. 1794-1805
-
-
Cox, J.1
Neuhauser, N.2
Michalski, A.3
Scheltema, R.A.4
Olsen, J.V.5
Mann, M.6
-
38
-
-
55149093649
-
Quantifying protein interface footprinting by hydroxyl radical oxidation and molecular dynamics simulation: Application to galectin-1
-
Charvátová, O., Foley, B. L., Bern, M. W., Sharp, J. S., Orlando, R., and Woods, R. J. (2008) Quantifying protein interface footprinting by hydroxyl radical oxidation and molecular dynamics simulation: application to galectin-1. J. Am. Soc. Mass Spectrom 19, 1692-1705
-
(2008)
J. Am. Soc. Mass Spectrom
, vol.19
, pp. 1692-1705
-
-
Charvátová, O.1
Foley, B.L.2
Bern, M.W.3
Sharp, J.S.4
Orlando, R.5
Woods, R.J.6
-
39
-
-
0000856458
-
Brownian motion of an ellipsoid. I. Dielectric dispersion for ellipsoidal molecules
-
Perrin, F. (1934) Brownian motion of an ellipsoid. I. Dielectric dispersion for ellipsoidal molecules. J. Phys. Radium 5, 497-511
-
(1934)
J. Phys. Radium
, vol.5
, pp. 497-511
-
-
Perrin, F.1
-
41
-
-
34548337296
-
Hydroxyl radical-mediated modification of proteins as probes for structural proteomics
-
Xu, G., and Chance, M. R. (2007) Hydroxyl radical-mediated modification of proteins as probes for structural proteomics. Chem. Rev. 107, 3514-3543
-
(2007)
Chem. Rev.
, vol.107
, pp. 3514-3543
-
-
Xu, G.1
Chance, M.R.2
-
42
-
-
28244486826
-
Methionine oxidation interferes with conversion of the prion protein into the fibrillar proteinase K-resistant conformation
-
Breydo, L., Bocharova, O. V., Makarava, N., Salnikov, V. V., Anderson, M., and Baskakov, I. V. (2005) Methionine oxidation interferes with conversion of the prion protein into the fibrillar proteinase K-resistant conformation. Biochemistry 44, 15534-15543
-
(2005)
Biochemistry
, vol.44
, pp. 15534-15543
-
-
Breydo, L.1
Bocharova, O.V.2
Makarava, N.3
Salnikov, V.V.4
Anderson, M.5
Baskakov, I.V.6
-
43
-
-
13344295093
-
Vascular variant of prion protein cerebral amyloidosis with Tau-positive neurofibrillary tangles: The phenotype of the stop codon 145 mutation in PRNP
-
Ghetti, B., Piccardo, P., Spillantini, M. G., Ichimiya, Y., Porro, M., Perini, F., Kitamoto, T., Tateishi, J., Seiler, C., Frangione, B., Bugiani, O., Giaccone, G., Prelli, F., Goedert, M., Dlouhy, S. R., and Tagliavini, F. (1996) Vascular variant of prion protein cerebral amyloidosis with Tau-positive neurofibrillary tangles: the phenotype of the stop codon 145 mutation in PRNP. Proc. Natl. Acad. Sci. U. S. A. 93, 744-748
-
(1996)
Proc. Natl. Acad. Sci. U. S. A.
, vol.93
, pp. 744-748
-
-
Ghetti, B.1
Piccardo, P.2
Spillantini, M.G.3
Ichimiya, Y.4
Porro, M.5
Perini, F.6
Kitamoto, T.7
Tateishi, J.8
Seiler, C.9
Frangione, B.10
Bugiani, O.11
Giaccone, G.12
Prelli, F.13
Goedert, M.14
Dlouhy, S.R.15
Tagliavini, F.16
-
44
-
-
77449089995
-
Prion protein amyloidosis with divergent phenotype associated with two novel nonsense mutations in PRNP
-
Jansen, C., Parchi, P., Capellari, S., Vermeij, A. J., Corrado, P., Baas, F., Strammiello, R., van Gool, W. A., van Swieten, J. C., and Rozemuller, A. J. (2010) Prion protein amyloidosis with divergent phenotype associated with two novel nonsense mutations in PRNP. Acta Neuropathol 119, 189-197
-
(2010)
Acta Neuropathol
, vol.119
, pp. 189-197
-
-
Jansen, C.1
Parchi, P.2
Capellari, S.3
Vermeij, A.J.4
Corrado, P.5
Baas, F.6
Strammiello, R.7
Van Gool, W.A.8
Van Swieten, J.C.9
Rozemuller, A.J.10
-
45
-
-
0026033998
-
Amyloid protein of Gerstmann-Sträussler-Scheinker disease (Indiana kindred) is an 11 kd fragment of prion protein with an N-terminal glycine at codon 58
-
Tagliavini, F., Prelli, F., Ghiso, J., Bugiani, O., Serban, D., Prusiner, S. B., Farlow, M. R., Ghetti, B., and Frangione, B. (1991) Amyloid protein of Gerstmann-Sträussler-Scheinker disease (Indiana kindred) is an 11 kd fragment of prion protein with an N-terminal glycine at codon 58. EMBO J. 10, 513-519
-
(1991)
EMBO J.
, vol.10
, pp. 513-519
-
-
Tagliavini, F.1
Prelli, F.2
Ghiso, J.3
Bugiani, O.4
Serban, D.5
Prusiner, S.B.6
Farlow, M.R.7
Ghetti, B.8
Frangione, B.9
-
46
-
-
0344326239
-
Analysis of 27 mammalian and 9 avian PrPs reveals high conservation of flexible regions of the prion protein
-
Wopfner, F., Weidenhöfer, G., Schneider, R., von Brunn, A., Gilch, S., Schwarz, T. F., Werner, T., and Schätzl, H. M. (1999) Analysis of 27 mammalian and 9 avian PrPs reveals high conservation of flexible regions of the prion protein. J. Mol. Biol. 289, 1163-1178
-
(1999)
J. Mol. Biol.
, vol.289
, pp. 1163-1178
-
-
Wopfner, F.1
Weidenhöfer, G.2
Schneider, R.3
Von Brunn, A.4
Gilch, S.5
Schwarz, T.F.6
Werner, T.7
Schätzl, H.M.8
-
47
-
-
0031594587
-
Overexpression of nonconvertible PrPc 114-121 in scrapie-infected mouse neuroblastoma cells leads to trans-dominant inhibition of wild-type PrPSc accumulation
-
Hölscher, C., Delius, H., and Bürkle, A. (1998) Overexpression of nonconvertible PrPc 114-121 in scrapie-infected mouse neuroblastoma cells leads to trans-dominant inhibition of wild-type PrPSc accumulation. J. Virol. 72, 1153-1159
-
(1998)
J. Virol.
, vol.72
, pp. 1153-1159
-
-
Hölscher, C.1
Delius, H.2
Bürkle, A.3
-
48
-
-
84870355272
-
Determination of amyloid core structure using chemical shifts
-
Skora, L., and Zweckstetter, M. (2012) Determination of amyloid core structure using chemical shifts. Protein Sci. 21, 1948-1953
-
(2012)
Protein Sci.
, vol.21
, pp. 1948-1953
-
-
Skora, L.1
Zweckstetter, M.2
-
49
-
-
33646342768
-
Role of N-terminal familial mutations in prion protein fibrillization and prion amyloid propagation in vitro
-
Jones, E. M., Surewicz, K., and Surewicz, W. K. (2006) Role of N-terminal familial mutations in prion protein fibrillization and prion amyloid propagation in vitro. J. Biol. Chem. 281, 8190-8196
-
(2006)
J. Biol. Chem.
, vol.281
, pp. 8190-8196
-
-
Jones, E.M.1
Surewicz, K.2
Surewicz, W.K.3
-
50
-
-
0025820942
-
Homozygous prion protein genotype predisposes to sporadic Creutzfeldt-Jakob disease
-
Palmer, M. S., Dryden, A. J., Hughes, J. T., and Collinge, J. (1991) Homozygous prion protein genotype predisposes to sporadic Creutzfeldt-Jakob disease. Nature 352, 340-342
-
(1991)
Nature
, vol.352
, pp. 340-342
-
-
Palmer, M.S.1
Dryden, A.J.2
Hughes, J.T.3
Collinge, J.4
-
51
-
-
3843131903
-
Methionine 129 variant of human prion protein oligomerizes more rapidly than the valine 129 variant: Implications for disease susceptibility to Creutzfeldt-Jakob disease
-
Tahiri-Alaoui, A., Gill, A. C., Disterer, P., and James, W. (2004) Methionine 129 variant of human prion protein oligomerizes more rapidly than the valine 129 variant: implications for disease susceptibility to Creutzfeldt-Jakob disease. J. Biol. Chem. 279, 31390-31397
-
(2004)
J. Biol. Chem.
, vol.279
, pp. 31390-31397
-
-
Tahiri-Alaoui, A.1
Gill, A.C.2
Disterer, P.3
James, W.4
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