Nucleation-dependent conformational conversion of the Y145Stop variant of human prion protein: Structural clues for prion propagation

Proceedings of the National Academy of Sciences of the United States of America

Volumn 100, Issue 21, 2003, Pages 12069-12074

  Kundu, Bishwajit ^a   Maiti, Nilesh R ^a   Jones, Eric M ^a   Surewicz, Krystyna A ^a   Vanik, David L ^b   Surewicz, Witold K ^a,b  

^a CASE WESTERN RESERVE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b CASE WESTERN RESERVE UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

AMYLOID; MONOMER; POLYPEPTIDE; PRION PROTEIN; RECOMBINANT PROTEIN;

AMINO ACID SEQUENCE; ARTICLE; ATOMIC FORCE MICROSCOPY; BETA SHEET; CONCENTRATION RESPONSE; CONFORMATIONAL TRANSITION; GERSTMANN STRAUSSLER SCHEINKER SYNDROME; HUMAN; INFRARED SPECTROSCOPY; PERIODICITY; POLYMERIZATION; PRIORITY JOURNAL; PROTEIN CONFORMATION; SEQUENCE ANALYSIS;

AMINO ACID SUBSTITUTION; CODON, TERMINATOR; ENDOPEPTIDASE K; GERSTMANN-STRAUSSLER-SCHEINKER DISEASE; HUMANS; MICROSCOPY, ATOMIC FORCE; MICROSCOPY, ELECTRON; MUTAGENESIS, SITE-DIRECTED; PEPTIDE FRAGMENTS; PEPTIDE MAPPING; PRIONS; PROTEIN CONFORMATION; PROTEIN STRUCTURE, SECONDARY; RECOMBINANT PROTEINS; SPECTROSCOPY, FOURIER TRANSFORM INFRARED; VARIATION (GENETICS);

EID: 0142091396     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.2033281100     Document Type: Article

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