The role of ficolins and MASPs in hereditary angioedema due to C1-inhibitor deficiency

Molecular Immunology

Volumn 54, Issue 3-4, 2013, Pages 271-277

  Csuka, Dorottya ^a   Munthe Fog, Lea ^b   Skjoedt, Mikkel Ole ^b   Kocsis, Andrea ^c   Zotter, Zsuzsanna ^a   Gál, Péter ^c   Varga, Lilian ^a   Farkas, Henriette ^a   Füst, George ^a   Garred, Peter ^b  

^a SEMMELWEIS UNIVERSITY OF MEDICINE   (Hungary)

^b UNIVERSITY OF COPENHAGEN   (Denmark)

^c INSTITUTE OF EXPERIMENTAL MEDICINE   (Hungary)

Author keywords

C1 inhibitor; Ficolin; Hereditary angioedema; Lectin pathway; MASP

Indexed keywords

COMPLEMENT COMPONENT C1S INHIBITOR; FICOLIN; LECTIN; MANNAN BINDING LECTIN; MANNAN BINDING LECTIN ASSOCIATED SERINE PROTEINASE;

ADULT; ANGIONEUROTIC EDEMA; ARTICLE; BLOOD LEVEL; COMPLEMENT CLASSICAL PATHWAY; CONTROLLED STUDY; ENZYME LINKED IMMUNOSORBENT ASSAY; FEMALE; HUMAN; MAJOR CLINICAL STUDY; MALE; PATHOPHYSIOLOGY; PRIORITY JOURNAL;

ADAPTOR PROTEINS, SIGNAL TRANSDUCING; ADULT; AGED; APOPTOSIS REGULATORY PROTEINS; CASE-CONTROL STUDIES; COMPLEMENT C1 INHIBITOR PROTEIN; COMPLEMENT PATHWAY, MANNOSE-BINDING LECTIN; FEMALE; GLYCOPROTEINS; HEREDITARY ANGIOEDEMA TYPES I AND II; HUMANS; LECTINS; MALE; MANNOSE-BINDING PROTEIN-ASSOCIATED SERINE PROTEASES; MIDDLE AGED; YOUNG ADULT;

EID: 84872422346     PISSN: 01615890     EISSN: 18729142     Source Type: Journal    
DOI: 10.1016/j.molimm.2012.12.015     Document Type: Article

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