Depressed activation of the lectin pathway of complement in hereditary angioedema

Clinical and Experimental Immunology

Volumn 153, Issue 1, 2008, Pages 68-74

  Varga, L ^a   Szeplaki G ^a   Laki, J ^a   Kocsis, A ^b   Kristof K ^c   Gal P ^b   Bajtay, Z ^c   Wieslander, J ^d   Daha, M R ^e   Garred, P ^f   Madsen, H O ^f   Fust G ^a   Farkas, H ^a  

^a SEMMELWEIS UNIVERSITY OF MEDICINE   (Hungary)

^b INSTITUTE OF EXPERIMENTAL MEDICINE   (Hungary)

^c EÖTVÖS LORÁND UNIVERSITY   (Hungary)

^d Wieslab AB   (Sweden)

^e LEIDEN UNIVERSITY   (Netherlands)

^f UNIVERSITY OF COPENHAGEN   (Denmark)

Author keywords

Complement; ELISA; Immunodeficiency primary

Indexed keywords

COMPLEMENT COMPONENT C1Q; COMPLEMENT COMPONENT C1S INHIBITOR; COMPLEMENT COMPONENT C3; COMPLEMENT COMPONENT C4; MANNAN BINDING LECTIN; MANNAN BINDING LECTIN ASSOCIATED SERINE PROTEINASE; MANNAN BINDING LECTIN ASSOCIATED SERINE PROTEINASE 2;

ADULT; ALLELE; ANGIONEUROTIC EDEMA; ARTICLE; CONTROLLED STUDY; ENZYME LINKED IMMUNOSORBENT ASSAY; FEMALE; GENOTYPE; HETEROZYGOSITY; HOMOZYGOSITY; HUMAN; LABORATORY TEST; MAJOR CLINICAL STUDY; MALE; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL;

ADULT; ANGIOEDEMA, HEREDITARY; BIOLOGICAL MARKERS; CASE-CONTROL STUDIES; COMPLEMENT ACTIVATION; COMPLEMENT C1 INHIBITOR PROTEIN; COMPLEMENT C4; COMPLEMENT PATHWAY, ALTERNATIVE; COMPLEMENT PATHWAY, CLASSICAL; COMPLEMENT PATHWAY, MANNOSE-BINDING LECTIN; ENZYME-LINKED IMMUNOSORBENT ASSAY; FEMALE; GENOTYPE; HOMOZYGOTE; HUMANS; MALE; MANNOSE-BINDING PROTEIN-ASSOCIATED SERINE PROTEASES; MIDDLE AGED; STATISTICS, NONPARAMETRIC;

EID: 44949203710     PISSN: 00099104     EISSN: 13652249     Source Type: Journal    
DOI: 10.1111/j.1365-2249.2008.03671.x     Document Type: Article

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