Human skeletal dysplasia caused by a constitutive activated transient receptor potential vanilloid 4 (TRPV4) cation channel mutation

Experimental and Molecular Medicine

Volumn 44, Issue 12, 2012, Pages 707-722

  Kang, Sang Sun ^a   Shin, Sung Hwa ^a   Auh, Chung Kyoon ^c   Chun, Jaesun ^b  

^a Chungbuk National University   (South Korea)

^b Korea National University of Education   (South Korea)

^c Mokpo National University   (South Korea)

Author keywords

Genetic diseases; Inborn; Osteochondrodysplasias; Osteogenesis; Phosphorylation; TRPV cation channels

Indexed keywords

BRACHYOLMIA TYPE 3 PROTEIN; MUTANT PROTEIN; SODIUM; UNCLASSIFIED DRUG; VANILLOID RECEPTOR 4;

AKINESIA; AMINO ACID SEQUENCE; BONE DISEASE; BONE DYSPLASIA; BONE MINERALIZATION; BRACHYOLMIA TYPE 3 GENE; CARTILAGE CELL; CHRONIC OBSTRUCTIVE LUNG DISEASE; DISEASE ASSOCIATION; ENCHONDRAL OSSIFICATION; FAMILIAL DIGITAL ARTHROPATHY BRACHYDACTYLY; FETUS DISEASE; GENE DELETION; GENE EXPRESSION REGULATION; GENE FUNCTION; GENE INSERTION SEQUENCE; GENETIC LINKAGE; HEREDITARY MOTOR SENSORY NEUROPATHY; HEREDITARY SPINAL MUSCULAR ATROPHY; HUMAN; HYPONATREMIA; METATROPIC DYSPLASIA; MISSENSE MUTATION; MOLECULAR PATHOLOGY; MUTATIONAL ANALYSIS; NONHUMAN; NUCLEOTIDE SEQUENCE; PARASTREMMATIC DWARFISM; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN PHOSPHORYLATION; PROTEIN PROTEIN INTERACTION; QUANTITATIVE TRAIT LOCUS; REGULATORY MECHANISM; REVIEW; SIGNAL TRANSDUCTION; SODIUM BLOOD LEVEL; SPONDYLOEPIPHYSEAL DYSPLASIA MAROTEAUX TYPE; VANILLOID RECEPTOR 4 GENE;

EID: 84871349942     PISSN: 12263613     EISSN: 20926413     Source Type: Journal    
DOI: 10.3858/emm.2012.44.12.080     Document Type: Review

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