Hermansky-Pudlak syndrome interstitial pneumonia: It's the epithelium, stupid!

American Journal of Respiratory and Critical Care Medicine

Volumn 186, Issue 10, 2012, Pages 939-940

  Mahavadi, Poornima ^a   Guenther, Andreas ^a,b,c   Gochuico, Bernadette R ^d  

^a JUSTUS LIEBIG UNIVERSITY GIESSEN   (Germany)

^b Agaplesion Lung Clinic Waldhof Elgershausen   (Germany)

^c German Center for Lung Research   (Germany)

^d NATIONAL HUMAN GENOME RESEARCH INSTITUTE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BLEOMYCIN; CYTOKINE; PIRFENIDONE;

CYTOKINE RELEASE; EDITORIAL; ENDOPLASMIC RETICULUM STRESS; HERMANSKI PUDLAK SYNDROME INTERSTITIAL PNEUMONIA; INTERSTITIAL PNEUMONIA; LUNG ALVEOLUS MACROPHAGE; LUNG FIBROSIS; NONHUMAN; OCULAR ALBINISM; PRIORITY JOURNAL; QUALITY OF LIFE; WILD TYPE;

ANIMALS; GENETIC PREDISPOSITION TO DISEASE; HERMANSKI-PUDLAK SYNDROME; HUMANS; PULMONARY ALVEOLI; PULMONARY FIBROSIS; RESPIRATORY MUCOSA;

EID: 84869208900     PISSN: 1073449X     EISSN: 15354970     Source Type: Journal    
DOI: 10.1164/rccm.201210-1771ED     Document Type: Editorial

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