Aberrant lung structure, composition, and function in a murine model of Hermansky-Pudlak syndrome

American Journal of Physiology - Lung Cellular and Molecular Physiology

Volumn 285, Issue 3 29-3, 2003, Pages

  Lyerla, Timothy A ^a   Rusiniak, Michael E ^b   Borchers, Michael ^d   Jahreis, Gerald ^b   Tan, Jian ^b   Ohtake, Patricia ^c   Novak, Edward K ^b   Swank, Richard T ^b  

^a CLARK UNIVERSITY   (United States)

^b ROSWELL PARK CANCER INSTITUTE   (United States)

^c UNIVERSITY AT BUFFALO   (United States)

^d UNIVERSITY OF CINCINNATI MEDICAL CENTER   (United States)

Author keywords

Inflammation; Inherited lung dysfunction; Lamellar body; Secretion; Surfactant protein

Indexed keywords

AIR SAC; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUTOFLUORESCENCE; BLEEDING TIME; CONTROLLED STUDY; DISEASE ASSOCIATION; DISEASE SEVERITY; EMPHYSEMA; FEMALE; GENETIC DISORDER; HYPOPIGMENTATION; INFLAMMATORY CELL; LAMELLAR BODY; LUNG ALVEOLUS CELL TYPE 2; LUNG DISEASE; LUNG FUNCTION; MACROPHAGE; MALE; MEASUREMENT; MORPHOMETRICS; MORTALITY; NONHUMAN; OCULAR ALBINISM; PRIORITY JOURNAL; RECESSIVE INHERITANCE;

EID: 0041508928     PISSN: 10400605     EISSN: None     Source Type: Journal    
DOI: 10.1152/ajplung.00024.2003     Document Type: Article

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