Translational attenuation differentially alters the fate of disease-associated fibulin proteins

FASEB Journal

Volumn 26, Issue 11, 2012, Pages 4548-4560

  Hulleman, John D ^a,b   Balch, William E ^b   Kelly, Jeffery W ^a,b  

^a Department of Chemistry ^*  (United States)

^b SCRIPPS RESEARCH INSTITUTE   (United States)

Author keywords

Age related macular degeneration; Cutis laxa; EIF2 ; Malattia leventinese; Proteostasis

Indexed keywords

ARSENIC TRIOXIDE; FIBULIN; FIBULIN 3; FIBULIN 5; INITIATION FACTOR 2ALPHA; UNCLASSIFIED DRUG;

ARTICLE; CUTIS LAXA; HUMAN; HUMAN CELL; PRIORITY JOURNAL; PROTEIN HOMEOSTASIS; PROTEIN PHOSPHORYLATION; PROTEIN SECRETION; RETINA MACULA AGE RELATED DEGENERATION; SIGNAL TRANSDUCTION; UNFOLDED PROTEIN RESPONSE;

ACTIVATING TRANSCRIPTION FACTOR 4; EIF-2 KINASE; EUKARYOTIC INITIATION FACTOR-2; EXTRACELLULAR MATRIX PROTEINS; HEK293 CELLS; HUMANS; LUCIFERASES; MUTATION; PROTEIN PROCESSING, POST-TRANSLATIONAL; SIGNAL TRANSDUCTION; TACROLIMUS; TRANSCRIPTION FACTORS;

EID: 84868296265     PISSN: None     EISSN: 15306860     Source Type: Journal    
DOI: 10.1096/fj.11-202861     Document Type: Article

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