P62/SQSTM1 prominently accumulates in renal proximal tubules in nephropathic cystinosis

Pediatric Nephrology

Volumn 27, Issue 11, 2012, Pages 2137-2144

  Sansanwal, Poonam ^a   Sarwal, Minnie M ^a  

^a CALIFORNIA PACIFIC MEDICAL CENTER   (United States)

Author keywords

Autophagy; Cystinosis; LC3; p62; Renal Fanconi Syndrome; Renal proximal tubules; SQSTM1

Indexed keywords

PROTEIN P62;

ARTICLE; AUTOPHAGY; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; CYSTINOSIS; FEMALE; FLUORESCENCE IMAGING; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; KIDNEY BIOPSY; KIDNEY INJURY; KIDNEY PROXIMAL TUBULE; KIDNEY TUBULE CELL; MALE; NEPHROPATHIC CYSTINOSIS; PATHOGENESIS; PRIORITY JOURNAL; SCHOOL CHILD;

ADAPTOR PROTEINS, SIGNAL TRANSDUCING; ADOLESCENT; AUTOPHAGY; BIOPSY; BLOTTING, WESTERN; CASE-CONTROL STUDIES; CELLS, CULTURED; CHILD; CYSTINOSIS; EPITHELIAL CELLS; FANCONI SYNDROME; HUMANS; IMMUNOHISTOCHEMISTRY; KIDNEY TUBULES, PROXIMAL; MICROSCOPY, CONFOCAL; MICROTUBULE-ASSOCIATED PROTEINS; NEPHROTIC SYNDROME; UP-REGULATION;

EID: 84868128390     PISSN: 0931041X     EISSN: 1432198X     Source Type: Journal    
DOI: 10.1007/s00467-012-2227-4     Document Type: Article

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