Renal phenotype of the cystinosis mouse model is dependent upon genetic background

Nephrology Dialysis Transplantation

Volumn 25, Issue 4, 2010, Pages 1059-1066

  Nevo, Nathalie ^a,b   Chol, Marie ^a,b   Bailleux, Anne ^a,b   Kalatzis, Vasiliki ^c,d   Morisset, Ludivine ^a,b   Devuyst, Olivier ^e   Gubler, Marie Claire ^a,b   Antignac, Corinne ^a,b  

^a HÔPITAL NECKER ENFANTS MALADES   (France)

^b UNIVERSITÉ PARIS DESCARTES   (France)

^c CNRS   (France)

^d UNIV MONTPELLIER   (France)

^e UNIVERSITÉ CATHOLIQUE DE LOUVAIN   (Belgium)

Author keywords

Chronic renal failure; Cystinosis; Genetic background; Mouse model; Proximal tubule dysfunction

Indexed keywords

CYSTINE; CYSTINOSIN; PROTEIN; UNCLASSIFIED DRUG;

AMINO ACID URINE LEVEL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BIOCHEMISTRY; CHRONIC KIDNEY FAILURE; CONGENIC STRAIN; CONTROLLED STUDY; CYSTINOSIS; FAILURE TO THRIVE; GENETICS; HISTOLOGY; KIDNEY DYSFUNCTION; KIDNEY FIBROSIS; KIDNEY FUNCTION; KIDNEY INJURY; KIDNEY PROXIMAL TUBULE; KIDNEY TUBULE DISORDER; MOUSE; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; URINALYSIS;

AMINO ACID TRANSPORT SYSTEMS, NEUTRAL; ANIMALS; CYSTINE; CYSTINOSIS; DISEASE MODELS, ANIMAL; FEMALE; KIDNEY FAILURE, CHRONIC; MALE; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MUTATION; PHENOTYPE; SPECIES SPECIFICITY;

EID: 77950244078     PISSN: 09310509     EISSN: 14602385     Source Type: Journal    
DOI: 10.1093/ndt/gfp553     Document Type: Article

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