Muscle fiber atrophy and regeneration coexist in collagen VI-deficient human muscle: Role of calpain-3 and nuclear factor-κB signaling

Journal of Neuropathology and Experimental Neurology

Volumn 71, Issue 10, 2012, Pages 894-906

  Paco, Sonia ^a   Ferrer, Isidre ^b   Jou, Cristina ^c   Cusí, Victoria ^c   Corbera, Joan ^c   Torner, Ferran ^c   Gualandi, Francesca ^d   Sabatelli, Patrizia ^e   Orozco, Anna ^f   Gómez Foix, Anna Maria ^f   Colomer, Jaume ^a,g   Nascimento, Andres ^a,g   Jimenez Mallebrera, Cecilia ^a,g  

^a HOSPITAL SANT JOAN DE DÉU   (Spain)

^b HOSPITAL UNIVERSITARI DE BELLVITGE   (Spain)

^c HOSPITAL MATERNO INFANTIL VALL D HEBRON   (Spain)

^d Dipartimento di Medicina Sperimentale e Diagnostica Sezione di Genetica Medica   (Italy)

^e CNR   (Italy)

^f UNIVERSITY OF BARCELONA   (Spain)

^g CENTRO DE INVESTIGACIÓN BIOMÉDICA EN RED DE ENFERMEDADES RARAS CIBERER   (Spain)

Author keywords

Calpain 3; Collagen type VI; Extracellular matrix; Muscle atrophy; Muscle regeneration; NF B; Ullrich congenital muscular dystrophy

Indexed keywords

ATROGIN 1; CALPAIN 3; COLLAGEN TYPE 6; I KAPPA B; MESSENGER RNA; MUSCLE RING FINGER 1 PROTEIN; PROTEASOME; RNA; UBIQUITIN;

ARTICLE; CELL SIZE; CELL SURVIVAL; CONTROLLED STUDY; DOWN REGULATION; HUMAN; HUMAN TISSUE; IMMUNOLOCALIZATION; MUSCLE ATROPHY; MUSCLE BIOPSY; MUSCLE CELL; MUSCLE REGENERATION; MYOPATHY; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROTEIN EXPRESSION; SATELLITE CELL; SIGNAL TRANSDUCTION;

CALPAIN; CHILD; CHILD, PRESCHOOL; COLLAGEN TYPE VI; FEMALE; HUMANS; MALE; MUSCLE FIBERS, SKELETAL; MUSCLE PROTEINS; MUSCLE, SKELETAL; MUSCULAR ATROPHY; MUSCULAR DYSTROPHIES; NF-KAPPA B; REGENERATION; SIGNAL TRANSDUCTION; YOUNG ADULT;

EID: 84866728930     PISSN: 00223069     EISSN: 15546578     Source Type: Journal    
DOI: 10.1097/NEN.0b013e31826c6f7b     Document Type: Article

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