Satellite cell dysfunction contributes to the progressive muscle atrophy in myotonic dystrophy type 1

Neuropathology and Applied Neurobiology

Volumn 35, Issue 6, 2009, Pages 603-613

  Thornell, L E ^a   Lindstom M ^a   Renault, V ^c,d,e   Klein, A ^c,d,e   Mouly, V ^c,d,e   Ansved, T ^b   Butler Browne, G ^c,d,e   Furling, D ^c,d,e  

^a UMEÅ UNIVERSITY   (Sweden)

^b KAROLINSKA INSTITUTE   (Sweden)

^c SORBONNE UNIVERSITÉ   (France)

^d INSERM   (France)

^e CNRS   (France)

Author keywords

Atrophy; CTG repeats; Muscle; Myotonic dystrophy type 1; Satellite cells

Indexed keywords

TELOMERASE;

ADULT; ARTICLE; CATARACT; CELL COUNT; CELL ISOLATION; CELL PROLIFERATION; CLINICAL ARTICLE; CLINICAL EVALUATION; CONTROLLED STUDY; DISEASE COURSE; DISEASE SEVERITY; FEMALE; HISTOPATHOLOGY; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; MALE; MUSCLE ATROPHY; MUSCLE BIOPSY; MUSCLE CELL; MUSCLE REGENERATION; MUSCULAR DYSTROPHY; MYOTONIC DYSTROPHY; PRIORITY JOURNAL; SATELLITE CELL; STAINING; STEM CELL; TELOMERE; TIBIALIS ANTERIOR MUSCLE; VASTUS LATERALIS MUSCLE;

ADULT; CELL COUNT; CELL PROLIFERATION; CELLS, CULTURED; FEMALE; HUMANS; IMMUNOHISTOCHEMISTRY; MALE; MIDDLE AGED; MUSCLE, SKELETAL; MUSCULAR ATROPHY; MYOTONIC DYSTROPHY; PROTEIN-SERINE-THREONINE KINASES; REGENERATION; SATELLITE CELLS, SKELETAL MUSCLE; SEVERITY OF ILLNESS INDEX; TELOMERE; TRINUCLEOTIDE REPEAT EXPANSION; YOUNG ADULT;

EID: 70449724660     PISSN: 03051846     EISSN: 13652990     Source Type: Journal    
DOI: 10.1111/j.1365-2990.2009.01014.x     Document Type: Article

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